tandayolili mankebi, deformaciebi da qromosomuli darrvevebi … · 2015. 1. 23. · q12.2 brolis...
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Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Tavi XVII.
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
(Q00-Q99)
ar igulisxmeba: metabolizmis Tandayolili darRvevebi (E 70-E 90)
es Tavi moicavs Semdeg blokebs:
Q00-Q07 nervuli sistemis Tandayolili mankebiQ10-Q18 Tvalis, yuris, saxisa da kisris Tandayolili mankebiQ20-Q28 sisxlis mimoqcevis sistemis Tandayolili mankebiQ30-Q34 sunTqvis sistemis Tandayolili mankebiQ35-Q37 tuCis naprali da sasis napraliQ38-Q45 saWmlis momnelebeli sistemis sxva Tandayolili mankebiQ50-Q56 sasqeso organoebis Tandayolili mankebiQ60-Q64 saSarde sistemis Tandayolili mankebiQ65-Q79 Zval-kunTovani sistemis Tandayolili mankebi da deformaciebiQ80-Q89 sxva Tandayolili mankebi
Q90-Q99 qromosomuli darRvevebi, romlebic ar aris Setanili sxvaklasifikaciebSi
nervuli sistemis Tandayolili mankebi
(Q00-Q07)anencefalia da msgavsi mankebi
Q00.0 anencefaliaacefalia
akraniaamielencefaliahemianencefalia
hemicefalia
Q00.1 kranioraqiSiziQ00.2 iniencefalia
encefalocele
igulisxmeba: encefalomielocele
hidroencefalocelehidromeningocele, kraniulimeningocele, cerebrulimeningoencnfalocele
ar igulisxmeba: mekel-gruberis sindromi (Q 61.9)Q01.0 Sublis encefaloceleQ01.1 cxvir-Sublis encefaloceleQ01.2 kefis encefaloceleQ01.8 encefalocele sxva lokalizaciiTQ01.9 encefalocele, dauzustebeli
mikrocefalia
hidromikrocefalia
mikrencefaloni
ar igulisxmeba: mekel-gruberis sindromi (Q 61.9)
Tandayolili hidrocefalia
igulisxmeba: hidrocefalusi axalSobilebSi
Q00
Q01
Q02
Q03
530
avadmyofobaTa saerTaSoriso klasifikacia
}Tavis tvinis, romelic sxvagvarad ar aris dazustebuli
ar igulisxmeba: arnold-Ciaris sindromi (Q 07.0)hidrocefalusi:. SeZenili (G 91.-). gamowveuli Tandayolili toqsoplazmoziT (P 37.1). spina bifida-sTan erTad (Q 05.0-Q 05.4)
Q03.0 silviusis wyalsadenis mankebisilviusis wyalsadenis
. anomalia
. obstruqcia, Tandayolili
. stenozi
Q03.1 maJendisa da luSkas xvrelebis atreziadendi-uokeris sindromi
Q03.8 sxva Tandayolili hidrocefalusiQ03.9 Tandayolili hidrocefalusi, dauzustebeli
Tavis tvinis sxva Tandayolili mankebi
ar igulisxmeba: ciklopia (Q 87.0)makrocefalia (Q 75.3)
Q04.0 korZiani sxeulis Tandayolili mankebikorZiani sxeulis agenezia
Q04.1 arinencefaliaQ04.2 holoprozencefaliaQ04.3 Tavis tvinis madeformirebeli sxva reduqciebi
ararseboba
ageneziaaplaziahipoplaziaagiriahidranencefalializencefaliamikrogiriapaqigiria
ar igulisxmeba: korZiani sxeulis Tandayolili mankebi (Q 04.0)Q04.4 septur-optikuri displaziaQ04.5 megalencefaliaQ04.6 Tandayolili cerebruli kistebi
porencefaliaSizencefalia
ar igulisxmeba: SeZenili porencefaluri kista (G 93.0)Q04.8 Tavis tvinis sxva dazustebuli Tandayolili mankebi
makrogiria
Q04.9 Tavis tvinis Tandayolili manki, dauzustebeliTandayolili:. anomalia. deformacia. avadmyofoba an dazianeba
. mravlobiTi anomaliebi
Spina bifidaigulisxmeba: hidromeningocele (spinuri)
meningocele (spinuri)meningomielocele
Q04
Tavis tvinis nawilis}
Q05
531
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
mielocelemielomeningoceleraqiSizispina bifida (naprali)(kisturi)siringomielocele
ar igulisxmeba: arnold-Ciaris sindromi (Q 07.0)faruli spina bifida (Q 76.0)
Q05.0 kisris spina bifida hidrocefalusiTQ05.1 gulmkerdis spina bifida hidrocefalusiT
spina bifida:. zurgis
. gulmkerd-welis
Q05.2 welis spina bifida hidrocefalusiTgava-welis spina bifida hidrocefalusiT
Q05.3 gavis spina bifida hidrocefalusiTQ05.4 dauzustebeli spina bifida hidrocefalusiTQ05.5 kisris spina bifida hidrocefalusis gareSeQ05.6 gulmkerdis spina bifida hidrocefalusis gareSe
spina bifida:. zurgis, romelic sxvagvarad ar aris dazustebuli
. gulmkerd-welis, romelic sxvagvarad ar aris dazustebuli
Q05.7 welis spina bifida hidrocefalusis gareSegava-welis spina bifida, romelic sxvagvarad ar aris dazustebuli
Q05.8 gavis spina bifida hidrocefalusis gareSeQ05.9 Spina bifida, dauzustebeli
zurgis tvinis sxva Tandayolili mankebi
Q06.0 amieliaQ06.1 zurgis tvinis hipoplazia da displazia
atelomielia
mielateliazurgis tvinis mielodisplazia
Q06.2 diastematomieliaQ06.3 raSis kudis sxva Tandayolili mankebiQ06.4 hidromielia
hidroraqisi
Q06.8 zurgis tvinis sxva dazustebuli Tandayolili mankebiQ06.9 zurgis Tvinis Tandayolili manki, dauzustebeli
Tandayolili
. anomalia
. deformacia
. avadmyofoba an dazianeba
nervuli sistemis sxva Tandayolili mankebi
ar igulisxmeba: ojaxuri disavtonomia [raili-deis] (G 90.1)neirofibromatozi (araavTvisebiani)(Q 85.0)
Q07.0 arnold-Ciaris sindromiQ07.8 nervuli sistemis sxva dazustebuli Tandayolili mankebi
nervis agenezia
mxris wnulis gadanacvlebaquTuTo-qvedaybis sinkineziis sindromi
} hidrocefalusiT
Q06
Q07
}zurgis tvinis an garsebis, romelic
sxvagvarad ar aris dazustebuli
532
avadmyofobaTa saerTaSoriso klasifikacia
} Tvalis
markus gunis sindromi
Q07.9 nervuli sistemis Tandayolili manki, dauzustebeliTandayolili:
. anomalia
. deformacia
. avadmyofoba an dazianeba
Tvalis, yuris, saxisa da kisris Tandayolili mankebi
(Q10-Q18)ar igulisxmeba: kurdRlis tuCi da mglis xaxa (Q 35-Q 37)
Tandayolili manki:. xerxemlis kisris nawilis (Q 05.0, Q 05.5, Q 67.5,Q 76.0-Q 76.4). xorxis (Q 31.-). tuCis, romelic ar aris Setanili sxva klasifikaciebSi (Q 38.0). cxviris (Q 30.-). farisebraxlo jirkvlis (Q 89.2). farisebri jirkvlis (Q 89.2)
Q quTuTos, sacremle aparatisa da Tvalbudis Tandayolili mankebi
ar igulisxmeba: kriptofTalmi:
. romelic sxvagvarad ar aris dazustebuli (Q 11.2)
. sindromi (Q 87.0)Q10.0 Tandayolili ftoziQ10.1 Tandayolili eqtropioniQ10.2 Tandayolili entropioniQ10.3 quTuTos sxva Tandayolili mankebi
ablefaroni
ararseboba an agenezia:. wamwamebis. quTuToebisdamatebiTi:. quTuTo
. Tvalis kunTebi
blefarofimozi, Tandayolili
quTuTos kolobomaquTuTos Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
Q10.4 ararseboba da agenezia sacremle aparatissacremle wertilis ararseboba
Q10.5 sacremle sadinris Tandayolili stenozi da striqturaQ10.6 sacremle aparatis sxva Tandayolili mankebi
sacremle aparatis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
Q10.7 Tvalbudis Tandayolili manki
anofTalmi, mikrofTalmi da makrofTalmi
Q11.0 kisturi Tvalis kakaliQ11.1 sxva anofTalmi
agenezia
aplazia
Q11.2 mikrofTalmikriptofTalmi, romelic sxvagvarad ar aris dazustebuli
Tvalis displaziaTvalis hipoplazia
nervuli sistemis, romelic sxvagvarad ar
aris dazustebuli}
Q10
Q11
533
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
rudimentuli Tvaliar igulisxmeba: kriptofTalmuri sindromi (Q 87.0)
Q11.3 makrofTalmiar igulisxmeba: makrofTalmi Tandayolili glaukomis dros (Q 15.0)
brolis Tandayolili mankebi
Q12.0 Tandayolili kataraqtaQ12.1 Tandayolili gadanacvlebuli broliQ12.2 brolis kolobomaQ12.3 Tandayolili afakiaQ12.4 sferofakiaQ12.8 brolis sxva Tandayolili mankebiQ12.9 brolis Tandayolili manki, dauzustebeli
Tvalis wina segmentis Tandayolili mankebi
Q13.0 feradi garsis kolobomakoloboma, romelic sxvagvarad ar aris dazustebuli
Q13.1 feradi garsis ararsebobaaniridia
Q13.2 feradi garsis sxva Tandayolili mankebianizokoria, Tandayolili
gugis atreziaferadi garsis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
koreqtopia
Q13.3 rqovanas Tandayolili SemRvrevaQ13.4 rqovanas sxva Tandayolili mankebi
rqovanas Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
mikrorqovana
piteris anomalia
Q13.5 lurji skleraQ13.8 Tvalis wina segmentis sxva Tandayolili mankebi
raijeris anomalia
Q13.9 Tvalis wina segmentis Tandayolili manki, dauzustebeli
Tvalis ukana segmentis Tandayolili mankebi
Q14.0 minisebri sxeulis siTxis Tandayolili mankiminisebri sxeulis Tandayolili SemRvreva
Q14.1 baduris Tandayolili mankibaduris Tandayolili anevrizma
Q14.2 mxedvelobis nervis diskis Tandayolili mankimxedvelobis nervis diskis koloboma
Q14.3 sisxlZarRvovani garsis Tandayolili mankiQ14.8 Tvalis ukana segmentis sxva Tandayolili mankebi
Tvalis fskeris koloboma
Q14.9 Tvalis ukana segmentis Tandayolili manki, dauzustebeli
Tvalis sxva Tandayolili mankebi
ar igulisxmeba: Tandayolili nistagmi (H 55); Tvalis albinizmi (E 70.3); pigmenturi retiniti (H 35.5)Q15.0 Tandayolili glaukoma
bufTalmi
Q12
Q13
Q14
Q15
534
avadmyofobaTa saerTaSoriso klasifikacia
axalSobilTa glaukomahidrofTalmikeratoglobusi, TandayolilimakrofTalmi Tandayolili glaukomis dros
megalokornea
Q15.8 Tvalis sxva dazustebuli Tandayolili mankebiQ15.9 Tvalis Tandayolili manki, dauzustebeli
Tandayolili:
. anomalia
. deformacia
yuris Tandayolili mankebi, romlebic iwvevs smenis daqveiTebas
ar igulisxmeba: Tandayolili siyrue (H 90.-)Q16.0 (yuris) niJaris Tandayolili ararsebobaQ16.1 sasmeni milis (gareTa) Tandayolili ararseboba, atrezia an striqtura
Zvlovani gasavlis atrezia an striqtura
Q16.2 evstaqis milis ararsebobaQ16.3 sasmeni Zvlebis Tandayolili manki
sasmeni Zvlebis Serwyma
Q16.4 Sua yuris sxva Tandayolili mankebiSua yuris Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
Q16.5 SigniTa yuris Tandayolili mankianomaluri:. apkovani labirinTi
. kortis organo
Q16.9 yuris Tandayolili manki, romelic iwvevs smenis daqveiTebas, dauzustebeliyuris Tandayolili ararseboba, romelic sxvagvarad ar aris dazustebuli
yuris sxva Tandayolili mankebi
ar igulisxmeba: preaurikuluri wiaRi (Q 18.1)
Q17.0 damatebiTi yuris niJaradamatebiTi wina saxuri
poliotia (mravalyurianoba)preaurikuluri danamati anu wanazardizedmeti:. yuri
. wilaki
Q17.1 makrotiaQ17.2 mikrotiaQ17.3 sxva araswori formis yuri
miniSnebuli yuri
Q17.4 araswori mdebareobis yuriyurebis dabla mdebareoba
ar igulisxmeba: kisris yuri (Q 18.2)Q17.5 warziduli yuri
Ramuris yuri
Q17.8 yuris sxva dazustebuli Tandayolili mankebiyuris wilis Tandayolili ararseboba
Q17.9 yuris Tandayolili manki, dauzustebeliyuris Tandayolili anomalia, romelic sxvagvarad ar aris dazustebuli
Q16
Q17
} Tvalis, romelic ar aris dazustebuli
535
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
saxisa da kisris sxva Tandayolili mankebi
ar igulisxmeba: kurdRlis tuCi da mglis xaxa (Q 35-Q 37)mdgomareobebi, romelTa klasifikacia mocemulia Q 67.0-Q 67.4-SiTavis qalasa da saxis Zvlebis Tandayolili mankebi (Q 75.-); ciklopia (Q 87.0)kbil-saxis anomaliebi [Tankbilvis anomaliis CaTvliT] (K 07.-)mankiani sindromebi, romelic iwvevs saxis damaxinjvebas (Q 87.0)persistenciuli far-enis sadinari (Q 89.2)
Q18.0 salayuCe napralis wiaRi, fistula da kistasalayuCe rudimenti (kvali)
Q18.1 preaurikuluri (yuriswina) wiaRi da kistafistula:
. yuris niJaris, Tandayolili
. kiser-yuris
Q18.2 salayuCe napralis sxva mankebisalayuCe napralis manki, romelic sxvagvarad ar aris dazustebuli
kisris (kisris gverdiTi) fistula
otocefalia
Q18.3 kisris nakecebiyelis pterigiumi
Q18.4 makrostomiaQ18.5 mikrostomiaQ18.6 makroxeilia
tuCis hipertrofia, Tandayolili
Q18.7 mikroxeiliaQ18.8 saxisa da kisris sxva dazustebuli Tandayolili mankebi
Sua:
. kista
. fistula saxisa da kisris
. wiaRi
Q18.9 saxisa da kisris Tandayolili manki, dauzustebelisaxisa da kisris Tandayolili anomalia, romelic sxvagvarad ar aris dazustebuli
sisxlis mimoqcevis sistemis Tandayolili mankebi
(Q20-Q28)gulis kamerebisa da damakavSirebeli struqturebis Tandayolili mankebi
ar igulisxmeba: deqstrokardia sawinaaRmdego mdebareobiT (situs inversus)(Q 89.3)winagulebis ganlageba sarkisebri asaxviT (situs inversus) (Q 89.3)
Q20.0 saerTo arteriuli Reroarteriuli Reros persistencia
Q20.1 magistralur sisxlZarRvTa gamosvla marjvena parkuWidantausig-bingis sindromi
Q20.2 magistralur sisxlZarRvTa gamosvla marcxena parkuWidanQ20.3 parkuWovan sisxlZarRvovani kavSiris darRveva
aortis deqstropozicia
magistralur sisxlZarRvTa transpozicia (sruli)
Q20.4 parkuWi ormagi SesavliTsaerTo parkuWi
samsakniani orwinaguliani guli
erTi parkuWi
Q20.5 winagul-parkuWovani kavSiris darRveva
Q18
}
Q20
536
avadmyofobaTa saerTaSoriso klasifikacia
koregirebuli transpozicia
L-transpozicia
parkuWTa inversia
Q20.6 winagulTa danamatebis izomerizmiwinagulTa danamatebis izomerizmi aspleniiT an polispleniiT
Q20.8 gulis kamerebisa da damakavSirebeli struqturebis sxva Tandayolili mankebiQ20.9 gulis kamerebisa da damakavSirebeli struqturebis Tandayolili manki,
dauzustebeli
gulis Zgidis Tandayolili mankebi
ar igulisxmeba: gulis Zgidis SeZenili defeqti (I 51.0)
Q21.0 parkuWTaSua Zgidis defeqtiQ21.1 winagulTaSua Zgidis defeqti
gvirgvinovani sinusis defeqti
Ria anu persistirebuli:. ovaluri xvreli. meoradi Zgidis defeqti (tipi II)
venuri wiaRis defeqti
Q21.2 winagul-parkuWovani Zgidis defeqtisaerTo winagul-parkuWovani arxi
sruli winagul-parkuWovani arxi
winagulTaSua pirveladi Zgidis defeqti (tipi I)
Q21.3 falos tetradaparkuWTaSua Zgidis defeqti filtvis arteriis Reros stenoziT an atreziiT, aortis
deqstropoziciiT da marjvena parkuWis hipertrofiiT
Q21.4 aorta-filtvis arteriis Reros defeqtiaortis Zgidis defeqti
aorta-filtvis arteriis Reros sarkmeli
Q21.8 parkuWSua Zgidis defeqtTan dakavSirebuli mdgomareobanieizenmengeris sindromi
falos pentada
Q21.9 gulis ZgideebTan dakavSirebuli Tandayolili mankebi, dauzustebeliZgidis (gulis) defeqti, romelic sxvagvarad ar aris dazustebuli
filtvis arteriis da samkariani sarqvlebis Tandayolili mankebi
Q22.0 filtvis arteriis sarqvlis atreziaQ22.1 filtvis arteriis sarqvlis Tandayolili stenoziQ22.2 filtvis arteriis sarqvlis Tandayolili naklovaneba
filtvis arteriis sarqvlis Tandayolili regurgitacia
Q22.3 filtvis arteriis sarqvlis sxva Tandayolili mankebifiltvis arteriis sarqvlis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
Q22.4 samkariani sarqvlis stenozisamkariani sarqvlis atrezia
Q22.5 ebSteinis anomaliaQ22.6 hipoplaziuri marjvena gulis sindromiQ22.8 samkariani sarqvlis sxva Tandayolili mankebiQ22.9 samkariani sarqvlis Tandayolili manki, dauzustebeli
aortisa da orkariani sarqvlebis Tandayolili mankebiQ23
Q21
Q22
537
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Q23.0 aortis sarqvlis Tandayolili stenoziaortis Tandayolili:
. atrezia
. stenoziar igulisxmeba: Tandayolili subaortuli stenozi (Q 24.4)
romelic Sedis hipoplaziuri marcxena gulis sindromSi (Q 23.4)Q23.1 aortis sarqvlis Tandayolili naklovaneba
aortis orkariani sarqveli
Tandayolili aortaluri naklovaneba
Q23.2 Tandayolili mitraluri stenoziTandayolili mitraluri atrezia
Q23.3 Tandayolili mitraluri naklovanebaQ23.4 hipoplaziuri marcxena gulis sindromi
aortis Sesavlis an sarqvlis atrezia an gamoxatuli hipoplazia, aswvrivi aortis hipoplaziiT
da marcxena parkuWis defeqturi ganviTarebiT (mitraluri sarqvlis stenoziT an atreziiT)
Q23.8 aortisa da mitraluri sarqvlebis sxva Tandayolili mankebiQ23.9 aortisa da mitraluri sarqvlebis Tandayolili manki, dauzustebeli
gulis sxva Tandayolili mankebi
ar igulisxmeba: endokardiuli fibroelastozi (I 42.4)
Q24.0 deqstrokardiaar igulisxmeba: deqstrokardia situs mversus-iT) (Q 89.3)
winagulebis danamatTa izomerizmi (aspleniiT an polispleniiT) (Q 20.6)winagulebis ganlageba sarkisebri asaxviT situs inversus-iT (Q 89.3)
Q24.1 levokardiaQ24.2 samwinaguliani guliQ24.3 marjvena parkuWis gasavlis stenoziQ24.4 Tandayolili subaortuli stenoziQ24.5 gvirgvinovan arteriaTa mankebi
Tandayolili gvirgvinovani (arteriis) anevrizma
Q24.6 gulis Tandayolili sruli blokadaQ24.8 gulis sxva dazustebuli Tandayolili mankebi
Tandayolili:
. marcxena parkuWis divertikuli
. manki:
. miokardiumis
. perikardiumisgulis araswori mdebareoba (malpozicia)
gulis avadmyofoba
Q24.9 gulis Tandayolili manki, dauzustebeliTandayolili:
. anomalia
. avadmyofoba
msxvili arteriebis Tandayolili mankebi
Q25.0 Ria arteriuli sadinariRia botalis sadinari
persistirebuli arteriuli sadinari
Q25.1 aortis koarqtaciaaortis koarqtacia (arteriuli sadinris wina)(arteriuli sadinris Semdgomi)
Q25.2 aortis atrezia
Q24
Q25
} gulis. romelic sxvagvarad ar aris dazustebuli
538
avadmyofobaTa saerTaSoriso klasifikacia
} filtvis aretriis
Q25.3 aortis stenoziaortis stenozi, sarqvelzeda
ar igulisxmeba: aortis Tandayolili stenozi (Q 23.0)Q25.4 aortis sxva Tandayolili mankebi
ararseboba
aplaziaTandayolili: aortis. anevrizma. dilataciavalsalvis wiaRis anevrizma (gamskdari)aortis ormagi rkali [aortis sisxlZarRvovani rgoli]aortis hipoplaziadarCenili:. aortis rkalis nadrekebi. marjvena aortis rkali
ar igulisxmeba: aortis hipoplazia hipoplaziuri marcxena gulis sindromis dros (Q 23.4)Q25.5 filtvis arteriis atreziaQ25.6 filtvis arteriis stenoziQ25.7 filtvis arteriis sxva Tandayolili mankebi
aberantiuli filtvis arteria
ageneziaanevrizmaanomaliahipoplazia
filtvis arteriul-venuri anevrizma
Q25.8 magistralur sisxlZarRvTa sxva Tandayolili mankebiQ25.9 magistralur sisxlZarRvTa Tandayolili manki, dauzustebeli
msxvili venebis Tandayolili mankebi
Q26.0 Rru venebis Tandayolili stenoziRru venebis (qveda)(zeda) Tandayolili stenozi
Q26.1 marcxena zeda Rru venaQ26.2 filtvis venebis sruli anomaluri drenaJiQ26.3 filtvis venebis nawilobrivi anomaluri drenaJiQ26.4 filtvis venebis anomaluri kavSirebiQ26.5 karis venuri sistemis anomaluri kavSirebiQ26.6 karis vena - RviZlis arteriuli fistulaQ26.8 msxvili venebis sxva Tandayolili mankebi
Rru venis (qveda)(zeda) ararseboba
qveda Rru venis kenti veniT gagrZelebadarCenili marcxena ukana mTavari vena
~Turquli xmlis~ sindromi
Q26.9 msxvili venis Tandayolili manki, dauzustebeliRru venis (qveda)(zeda) anomalia, romelic sxvagvarad ar aris dazustebuli
periferiuli sisxlZarRvovani sistemis sxva Tandayolili mankebi
ar igulisxmeba: anomaliebi:
. Tavis tvinisa da precerebruli sisxlZarRvebis (Q 28.0--Q 28.3)
. gvirgvinovani sisxlZarRvebis (Q 24.5)
. filtvis arteriis (Q 25.5-Q 25.7)Tandayolili baduris anevrizma (Q 14.1); hemangioma da limfangioma (D 18.-)
Q27.0 Wiplaris arteriis Tandayolili ararseboba da hipoplaziaWiplaris erTi arteria
Q26
}
Q27
539
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Q27.1 Tirkmlis arteriis Tandayolili stenoziQ27.2 Tirkmlis arteriis sxva Tandayolili mankebi
Tirkmlis arteriis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
Tirkmlis mravali arteria
Q27.3 periferiuli arteriul-venuri mankiarteriul-venuri anevrizma
ar igulisxmeba: SeZenili arteriul-venuri anevrizma (I 77.0)
Q27.4 Tandayolili flebeqtaziaQ27.8 periferiuli sisxlZarRvovani sistemis sxva dazustebuli Tandayolili mankebi
aberaciuli laviwqveSa arteria
ararsebobaatreziaTandayolili. anevrizma (periferiuli). striqtura, arteriis
. varikozi
Q27.9 periferiuli sisxlZarRvovani sistemis Tandayolili manki, dauzustebeliarteriis an venis anomalia, romelic sxvagvarad ar aris dazustebuli
sisxlis mimoqcevis sistemis sxva Tandayolili mankebi
ar igulisxmeba: Tandayolili anevrizma:
. romelic sxvagvarad ar aris dazustebuli (Q 27.8)
. gvirgvinovani (Q 24.5)
. periferiuli (Q 27.8)
. filtvis (Q 25.7)
. baduris (Q 14.1)gamskdari:. Tavis tvinis arteriul-venuri manki (I 60.8)
. precerebruli sisxlZarRvebis manki (I 72.-)
Q28.0 precerebruli sisxlZarRvebis arteriul-venuri mankiTandayolili arteriul-venuri precerebruli anevrizma (gaumskdari)
Q28.1 precerebruli sisxlZarRvebis sxva mankebiTandayolili:
. precerebruli sisxlZarRvebis manki, romelic sxvagvarad ar aris dazustebuli
. precerebruli anevrizma (gaumskdari)
Q28.2 Tavis tvinis sixlZarRvebis arteriul-venuri mankiTavis tvinis arteriul-venuri manki, romelic sxvagvarad ar aris dazustebuli
Tandayolili arteriul-venuri cerebruli anevrizma (gaumskdari)
Q28.3 Tavis tvinis sisxlZarRvebis sxva mankebiTandayolili:. cerebruli anevrizma (gaumskdari). Tavis tvinis sisxlZarRvebis manki, romelic sxvagvarad ar aris dazustebuli
Q28.8 sisxlis mimoqcevis sistemis sxva dazustebuli Tandayolili mankebiTandayolili anevrizma, dazustebuli lokalizaciiT, romelic ar aris Setanili sxva klasifikaciebSi
Q28.9 sisxlis mimoqcevis sistemis Tandayolili manki, dauzustebeli
sasunTqi sistemis Tandayolili mankebi
(Q30-Q34)cxviris Tandayolili mankebi
ar igulisxmeba: cxviris Zgidis Tandayolili gamrudeba (Q 67.4)Q30.0 qoanis atrezia
Q28
Q30
arteriis an venis, romelic ar aris Setanili sxvaklasifikaciebSi}
540
avadmyofobaTa saerTaSoriso klasifikacia
} beWdisebri xrtilis, xorxsarqvelis, yiis,xorcis an farisebri xrtilis
}
atrezia
Tandayolili stenozi
Q30.1 cxviris agenezia da ganviTarebaSi CamorCenacxviris Tandayolili ararseboba
Q30.2 napralovani, naxeTqisebri da naWdevisebri cxviriQ30.3 Tandayolili dacxriluli cxviris ZgideQ30.8 cxviris sxva Tandayolili mankebi
damatebiTi cxviri
cxviris wiaRTa kedlebis Tandayolili anomalia
Q30.9 cxviris Tandayolili manki, dauzustebeli
xorxis Tandayolili mankebi
Q31.0 xorxis apkixorxis apki:
. romelic sxvagvarad ar aris dazustebuli
. yiis
. yiisqveda
Q31.1 Tandayolili yiisqveda stenoziQ31.2 xorxis hipoplaziaQ31.3 laringoceleQ31.4 xorxis Tandayolili stridori
Tandayolili stridori (xorxis), romelic sxvagvarad ar aris dazustebuli
Q31.8 xorxis sxva Tandayolili mankebiararseboba
ageneziaatreziafarisebri xrtilis napralixorxis Tandayolili stenozi, romelic ar aris Setanili sxva klasifikaciebSixorxsarqvelis naxeTqi
beWdisebri xrtilis ukana naprali
Q31.9 xorxis Tandayolili manki, dauzustebeli
traqeisa da bronqebis Tandayolili mankebi
ar igulisxmeba: Tandayolili bronqoeqtazia (Q 33.4)Q32.0 Tandayolili traqeomalaciaQ32.1 traqeis sxva Tandayolili mankebi
traqeis xrtilis anomalia
traqeis atreziaTandayolili:. gafarToeba. manki traqeis. stenozi
. traqeocele
Q32.2 Tandayolili bronqomalaciaQ32.3 bronqis Tandayolili stenoziQ32.4 bronqis sxva Tandayolili mankebi
ar arseboba
agneziaTandayolili manki,romelic sxvagvarad ar aris dazustebuli
divertikuli
Q31
Q32
cxviris xvrelebis (wina, ukana)}
bronqis}
541
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
filtvis Tandayolili mankebi
Q33.0 Tandayolili kisturi filtviTandayolili:
. fiWuri filtvi
. filtvis avadmyofoba:
. kisturi
. polikisturi
ar igulisxmeba: filtvis kisturi avadmyofoba, SeZenili an dauzustebeli (J 98.4)Q33.1 filtvis damatebiTi wiliQ33.2 filtvis sekvestraciaQ33.3 filtvis agenezia
filtvis ararseboba (wilis)
Q33.4 Tandayolili bronqeqtaziaQ33.5 eqtopiuri qsovili filtvSiQ33.6 filtvis hipoplazia da displazia
ar igulisxmeba: piltvis hipoplazia, dakavSirebuli dRenaklulobasTan (P 28.0)Q33.8 filtvis sxva Tandayolili mankebiQ33.9 filtvis Tandayolili manki, dauzustebeli
sasunTqi sistemis sxva Tandayolili mankebi
Q34.0 plevris anomaliaQ34.1 Suasayris Tandayolili kistaQ34.8 sunTqvis sistemis sxva dazustebuli Tandayolili mankebi
cxvir-xaxis atrezia
Q34.9 sunTqvis sistemis Tandayolili manki, dauzustebeliTandayolili:. ararseboba. anomalia, romelic sxvagvarad ar aris
dazustebuli
tuCis naprali da sasis naprali
(Q35-Q37)ar igulisxmeba: robinis sindromi (Q 87.0)
sasis naprali
igulisxmeba: sasis naWdevi; palatoSiziar igulisxmeba: mglis xaxa kurdRlis tuCiT (Q 37.-)
Q35.0 magari sasis naprali, ormxriviQ35.1 magari sasis naprali, calmxrivi
magari sasis naprali, romelic sxvagvarad ar aris dazustebuli
Q35.2 rbili sasis naprali, ormxriviQ35.3 rbili sasis naprali, calmxrivi
rbili sasis naprali, romelic sxvagvarad ar aris dazustebuli
Q35.4 magari sasis naprali rbili sasis napraliT, ormxriviQ35.5 magari sasis naprali rbili sasis napraliT, calmxrivi
magari sasis naprali rbili sasis napraliT, romelic sxvagvarad ar aris dazustebuli
Q35.6 sasis naprali, SuaQ35.7 naqis napraliQ35.8 sasis naprali, dauzustebeli, ormxriviQ35.9 sasis naprali, dauzustebeli, calmxrivi
sasis naprali, romelic sxvagvarad ar aris dazustebuli
Q33
Q34
Q35
542
avadmyofobaTa saerTaSoriso klasifikacia
tuCis naprali
igulisxmeba: xeiloSizi; Tandayolili tuCis naWdevi; kurdRlis tuCi; labium leporinumar igulisxmeba: tuCisa da magari sasis defeqti (Q 37.-)
Q36.0 tuCis naprali, ormxriviQ36.1 tuCis naprali, SuaQ36.9 tuCis naprali, calmxrivi
tuCis naprali, romelic sxvagvarad ar aris dazustebuli
sasis naprali tuCis napralTan erTad
Q37.0 magari sasis naprali tuCis napraliT, ormxriviQ37.1 magari sasis naprali tuCis napraliT, calmxrivi
magari sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli
Q37.2 rbili sasis naprali tuCis napraliT, ormxriviQ37.3 rbili sasis naprali tuCis napraliT, calmxrivi
rbili sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli
Q37.4 magari da rbili sasis naprali tuCis napraliT, ormxriviQ37.5 magari da rbili sasis naprali tuCis napraliT, calmxrivi
magari da rbili sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli
Q37.8 dauzustebeli sasis naprali tuCis napraliT, ormxriviQ37.9 dauzustebeli sasis naprali tuCis napraliT, calmxrivi
sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli
saWmlis momnelebeli sistemis sxva Tandayolili mankebi
(Q38-Q45)enis, piris da xaxis sxva Tandayolili mankebi
ar igulisxmeba: makrostomia (Q 18.4); mikrostomia (Q 18.5)Q38.0 tuCebis Tandayolili mankebi, romlebic ar aris Setanili sxva
klasifikaciebSiTandayolili:. tuCis fistula. tuCis manki, romelic sxvagvarad ar aris dazustebulivan der vudis sindromiar igulisxmeba: tuCis naprali (Q 36.-). sasis napraliT (Q 37.-)makroxeilia (Q 18.6)mikroxeilia (Q 18.7)
Q38.1 ankiloglosiadabmuli ena
Q38.2 makroglosiaQ38.3 enis sxva Tandayolili mankebi
aglosiaormagi enaTandayolili:. enis Sexorceba. enis naprali. enis manki, romelic sxvagvarad ar aris dazustebulihipoglosiaenis hipoplazia
mikroglosia
Q38.4 sanerwyve jirkvlebisa da sadinarebis Tandayolili mankebi
Q36
Q37
Q38
543
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
ararseboba
damatebiTi sanerwyve jirkvlis an sadinarisatrezia
sanerwyve jirkvlis Tandayolili fistula
Q38.5 sasis Tandayolili mankebi, romlebic ar aris Setanili sxva klasifikaciebSinaqis ararseboba
sasis Tandayolili manki, romelic sxvagvarad ar aris dazustebulimaRalTaRiani sasa
ar igulisxmeba: sasis naprali (Q 35.-); enis napraliT (Q 37.-)Q38.6 piris Rrus sxva Tandayolili mankebi
piris Rrus Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
Q38.7 xaxis jibexaxis divertikuli
ar igulisxmeba: xaxis jibis sindromi (D 28.1)Q38.8 xaxis sxva Tandayolili mankebi
xaxis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
saylapavis Tandayolili mankebi
Q39.0 saylapavis atrezia fistulis gareSesaylapavis atrezia, romelic sxvagvarad ar aris dazustebuli
Q39.1 saylapavis atrezia traqeo-saylapavis fistuliTsaylapavi milis atrezia saylapav-bronquli fistuliT
Q39.2 traqeo-saylapavis Tandayolili fistula atreziis gareSeTandayolili sasule-saylapavis fistula, romelic sxvagvarad ar aris dazustebuli
Q39.3 saylapavis Tandayolili stenozi da striqturaQ39.4 saylapavis apkiQ39.5 saylapavis Tandayolili dilataciaQ39.6 saylapavis divertikuli
saylapavi milis jibe
Q39.8 saylapavi milis sxva Tandayolili mankebiararseboba
Tandayolili gadanacvleba saylapavi mili (-is)
gaoreba
Q39.9 saylapavi milis Tandayolili manki, dauzustebeli
alimenturi traqtis zeda nawilis sxva Tandayolili mankebi
Q40.0 Tandayolili hipertrofiuli pilorusis stenoziTandayolili an infantiluri:
. Seviwoeba
. hipertrofia
. spazmi pilorusis
. stenozi
. striqtura
Q40.1 saylapavis milis xvrelis Tandayolili TiaqarikuWis kardiuli nawilis gadanacvleba saylapavi milis xvrelis gavliT
ar igulisxmeba: Tandayolili diafragmuli Tiaqari (Q 79.0)Q40.2 kuWis sxva dazustebuli mankebi
Tandayolili:
. kardiaspazmi
. kuWis gadaadgileba
Q39
Q40
}
}
}
544
avadmyofobaTa saerTaSoriso klasifikacia
. kuWis divertikuli
. qviSis saaTisebri kuWikuWis gaorebamegalogastria
mikrogastria
Q40.3 kuWis Tandayolili manki, dauzustebeliQ40.8 alimenturi traqtis zeeda nawilis sxva dazustebuli Tandayolili mankebiQ40.9 alimenturi traqtis zeda nawilis Tandayolili manki, dauzustebeli
Tandayolili:
. anomalia alimenturi traqtis zeda nawilis,
. deformacia romelic sxvagvarad ar aris dazustebuli
wvrili nawlavis Tandayolili ararseboba, atrezia da stenozi
igulisxmeba: wvrili nawlavis anu nawlavis Tandayolili obstruqcia, okluzia dastriqtura, romelic sxvagvarad ar aris dazustebuli
ar igulisxmeba: mekoniumiT gamowveuli gauvaloba (E 84.1)Q41.0 Tormetgoja nawlavis Tandayolili ararseboba, atrezia da stenoziQ41.1 mlivi nawlavis Tandayolili ararseboba, atrezia da stenozi
“vaSlis qerqis” sindromi
gauxvretavi (xvrelis gareSe) mlivi nawlavi
Q41.2 TeZos nawlavis Tandayolili ararseboba, atrezia da stenoziQ41.8 wvrili nawlavebis sxva dazustebuli nawilebis Tandayolili ararseboba,
atrezia da stenoziQ41.9 wvrili nawlavebis, dauzustebeli nawilis, Tandayolili ararseboba,
atrezia da stenozi, romelic sxvagvarad ar aris dazustebuli
msxvili nawlavis Tandayolili ararseboba, atrezia da stenozi
igulisxmeba: msxvili nawlavis Tandayolili obstruqcia, okluzia an striqtura
Q42.0 swori nawlavis Tandayolili ararseboba, atrezia da stenozifistulasTan erTad
Q42.1 swori nawlavis Tandayolili ararseboba, atrezia da stenozi fistulis gareSegauxvretavi (xvrelis gareSe) swori nawlavi
Q42.2 yiTas Tandayolili ararseboba, atrezia da stenozi fistulasTan erTadQ42.3 yiTas Tandayolili ararseboba, atrezia da stenozi fistulis gareSe
gauxvretavi (xvrelis gareSe) yiTa
Q42.8 msxvili nawlavis sxva nawilebis Tandayolili ararseboba, atrezia da stenoziQ42.9 msxvili nawlavis, dauzustebeli nawilis, Tandayolili ararseboba, atrezia
da stenozi
nawlavTa sxva Tandayolili mankebi
Q43.0 mekelis divertikulidarCenili:
. omfalur-mezenteriuli sadinari
. yviTris sadinari
Q43.1 hirSprungis avadmyofobaaganglionozi
Tandayolili (aganglionuri) megakoloni
Q43.2 kolinjis sxva Tandayolili funqciuri dazianebebikolinjis Tandayolili dilatacia
Q43.3 nawlavTa fiqsaciis Tandayolili mankebiTandayolili Sexorcebani [Wimebi]:
}
Q42
Q41
Q43
545
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
. badeqonis, anomaluri
. peritoneumisjeksonis apkikolinjis malrotaciarotacia:. ukmarisoba. dausrulebeli brma nawlavisa da kolinjis. naklovaneba
saerTo (universaluri) jorjali
Q43.4 nawlavis gaormagebaQ43.5 eqtopiuri yiTaQ43.6 swori nawlavisa da yiTas Tandayolili fistula
ar igulisxmeba: Tandayolili fistula:
. swornawlav-saSos (Q 52.2)
. Sardsaden-swori nawlavis (Q 64.7)piloniduri (kudusunis) fistula anu wiaRi swori nawlavis (L 05.-)ararsebobiT, atreziiT da stenoziT (Q 42.0, Q 42.2)
Q43.7 darCenili kloakakloaka, romelic sxvagvarad ar aris dazustebuli
Q43.8 nawlavTa sxva dazustebuli Tandayolili mankebiTandayolili:. brma maryuJis sindromi. divertikuliti, kolinjis. divertikuli, nawlavisdoliqokolinjimegaloapendiqsimegaloduodenumimikrokolinjitranspozicia:. apendiqsis (danamatis). kolinjis
. nawlavis
Q43.9 nawlavTa Tandayolili manki, dauzustebeli
naRvlis buStis, naRvlis sadinarebisa da RviZlis Tandayolili mankebi
Q44.0 naRvlis buStis agenezia, aplazia da hipoplazianaRvlis buStis Tandayolili ararseboba
Q44.1 naRvlis buStis sxva Tandayolili mankebinaRvlis buStis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
RviZliSida naRvlis buSti
Q44.2 naRvlis sadinarebis atreziaQ44.3 naRvlis sadinarebis Tandayolili stenozi da striqturaQ44.4 qoledoqusis (naRvlis saerTo sadinris) kistaQ44.5 naRvlis sadinarebis sxva Tandayolili mankebi
RviZlis damatebiTi sadinari
naRvlis sadinris Tandayolili manki, romelic sxvagvarad ar aris dazustebuligaormageba:. naRvlis sadinaris
. naRvlis buStis sadinaris
Q44.6 RviZlis kisturi avadmyofobaRviZlis kistofibrozuli avadmyofoba
Q44.7 RviZlis sxva Tandayolili mankebidamatebiTi RviZli
}
Q44
546
avadmyofobaTa saerTaSoriso klasifikacia
alajilis sindromiTandayolili:. RviZlis ararseboba. hepatomegalia
. RviZlis manki, romelic sxvagvarad ar aris dazustebuli
saWmlis momnelebeli sistemis sxva Tandayolili mankebi
ar igulisxmeba: Tandayolili:
. diafragmuli Tiaqari (Q 79.0);
. saylapavi milis xvrelis Tiaqari (Q 40.1)Q45.0 pankreasis agenezia, aplazia da hipoplazia
pankreasis Tandayolili ararseboba
Q45.1 rgolisebri pankreasi (nalisebri)Q45.2 Tandayolili pankreasuli kistaQ45.3 pankreasisa da pankreasis sadinaris sxva Tandayolili mankebi
damatebiTi pankreasi
pankreasisa an pankreasis sadinaris Tandayolili manki, romelic sxvagvarad ar aris dazustebuliar igulisxmeba: Saqriani diabeti:
. Tandayolili (E 10.-)
. neonataluri (P 70.2)pankreasis kistofibrozi (E 84.-)
Q45.8 saWmlis momnelebeli sistemis sxva dazustebuli Tandayolili mankebialimenturi traqtis ararseboba (sruli)(nawilobrivi), romelic sxvagvarad ar aris dazustebuli
gaormageba saWmlis momnelebeli organoebis, romelicmalpozicia, Tandayolili sxvagvarad ar aris dazustebuli
Q45.9 saWmlis momnelebeli sistemis Tandayolili manki, dauzustebeliTandayolili:. anomalia saWmlis momnelebeli sistemis, romelic
. deformacia sxvagvarad ar aris dazustebuli
sasqeso organoebis Tandayolili mankebi
(Q50-Q56)ar igulisxmeba: androgen-rezistentuli sindromi (E 34.5)
qromosomebis ricxvisa da formis anomaliebTan dakavSirebuli sindromebi (Q 90-Q 99)testikuluri feminizaciis sindromi (E 34.5)
sakvercxeebis, falopiusis milebisa da ganieri iogis Tandayolili mankebi
Q50.0 sakvercxis Tandayolili ararsebobaar igulisxmeba: terneris sindromi (Q 96.-)
Q50.1 sakvercxis Canasaxovani kistaQ50.2 sakvercxis Tandayolili SemogrexaQ50.3 sakvercxis sxva Tandayolili mankebi
damatebiTi sakvercxe
sakvercxis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
zonriseburi sakvercxe
Q50.4 falopiusis milis embrionuli kistafibriuli (foCebis) kista
Q50.5 ganieris iogis embrionuli kistakista:
. epooforonis
. gartneris sadinris
. paraovariuli
Q45
}
}
Q50
547
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Q50.6 falopiusis milisa da ganieri iogis sxva Tandayolili mankebiararseboba
damatebiTi falopiusis mili(s) an ganieri iogi(s)atrezia
falopiusis milis an ganieri iogis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
saSvilosnosa da saSvilosnos yelis Tandayolili mankebi
Q51.0 saSvilosnos agenezia da aplaziasaSvilosnos Tandayolili ararseboba
Q51.1 ormagi saSvilosno ormagi yeliTa da saSoTiQ51.2 saSvilosnos sxva gaormageba
saSvilosnos gaormageba, romelic sxvaggvarad ar aris dazustebuli
Q51.3 orrqiani saSvilosnoQ51.4 calrqiani saSvilosnoQ51.5 saSvilosnos yelis agenezia da aplazia
saSvilosnos yelis Tandayolili ararseboba
Q51.6 saSvilosnos yelis embrionuli kistaQ51.7 Tandayolili fistula saSvilosnosa da saWmlis momnelebel da saSarde
traqtebs SorisQ51.8 saSvilosnosa da saSvilosnos yelis sxva Tandayolili mankebisaSvilosnosa
da saSvilosnos yelis hipoplaziaQ51.9 saSvilosnosa da saSvilosnos yelis Tandayolili manki, dauzustebeli
qalis sasqeso organoebis sxva Tandayolili mankebi
Q52.0 saSos Tandayolili ararsebobaQ52.1 ormagi saSo
Zgidiani saSo
ar igulisxmeba: ormagi saSo ormagi saSvilosnoTi da yeliT (Q 51.1)Q52.2 Tandayolili swor-nawlav - saSos fistula
ar igulisxmeba: kloaka (Q 43.7)Q52.3 mTliani (xvrelis gareSe) saqalwule apkiQ52.4 saSos sxva Tandayolili mankebi
saSos Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
kista:. nakis arxis, Tandayolili
. saSos embrionuli
Q52.5 bageebis SexorcebaQ52.6 savnebos (klitoris) Tandayolili mankiQ52.7 vulvis sxva Tandayolili mankebi
Tandayolili:
. ararseboba
. kista vulvis
. manki, romelic sxvagvarad ar aris dazustebuli
Q52.8 qalis sasqeso organoebis sxva dazustebuli Tandayolili mankebiQ52.9 qalis sasqeso organoebis Tandayolili manki, dauzustebeli
Camousvleli saTesle jirkvali
Q53.0 eqtopiuri saTesle jirkvalicalmxrivi an ormxrivi eqtopiuri saTesle jirkvali
Q53.1 Camousvleli saTesle jirkvali, calmxrivi
Q51
Q52
}
}
Q53
548
avadmyofobaTa saerTaSoriso klasifikacia
Q53.2 Camousvleli saTesle jirkvali, ormxriviQ53.9 Camousvleli saTesle jirkvali, dauzustebeli
kriptorqizmi, romelic sxvagvarad ar aris dazustebuli
hipospadia
ar igulisxmeba: epispadia (Q 64.0)Q54.0 hipospadia, asos Tavis
hipospadia:
. gvirgvinovani
. jirkvlovani
Q54.1 hipospadia, asos sxeulisQ54.2 hipospadia, aso - saTesle parkisQ54.3 hipospadia, SorisisQ54.4 asos Tandayolili gamrudebaQ54.8 sxva hipospadiaQ54.9 hipospadia, dauzustebeli
mamakacis sasqeso orgaoebis sxva Tandayolili mankebi
ar igulisxmeba: Tandayolili hidrocele (P 83.5); hipospadia (Q 54.-)Q55.0 saTesle jirkvlis ararseboba da aplazia
monorqizmi
Q55.1 saTesle jirkvlisa da saTesle parkis hipoplaziasaTesle jirkvlebis Sexorceba
Q55.2 saTesle jirkvlisa da saTesle parkis sxva Tandayolili mankebisaTesle jirkvlisa da saTesle parkis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
poliorqizmiretraqciuli saTesle jirkvali
moZravi saTesle jirkvali
Q55.3 Teslis gamomtani sadinaris atreziaQ55.4 Teslis gamomtani sadinaris, saTeslis danamatis (epididimisis),
saTesle buStukebisa da winamdebare jirkvlis (prostatis) sxva Tandayolili mankebi
ararseboba an aplazia:. prostatis. saTesle bagirakisTeslis gamomtani sadinaris, epididimisis, saTesle buStukebisa da prostatis Tandayolili
manki, romelic sxvagvarad ar aris dazustebuli
Q55.5 asos Tandayolili ararseboba da aplaziaQ55.6 asos sxva Tandayolili mankebi
asos Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
asos gamrudeba (gverdiTi)
asos hipoplazia
Q55.8 mamakacis sasqeso organoebis sxva dazustebuli Tandayolili mankebiQ55.9 mamakacis sasqeso organos Tandayolili manki, dauzustebeli
Tandayolili:
. anomalia mamakacis sasqeso organosi, romelic sxvagvarad
. deformacia ar aris dazustebuli
ganusazRvreli sqesi da fsevdohermafroditizmi
ar igulisxmeba: fsevdohermafroditizmi:
. qalis, adrenokortikuli dazianebiT (E 25.-)
. mamakacis, androgen-rezistentobiT (E 34.5)
. dazustebuli qromosomuli aberaciiT (Q 96-Q 99)
Q55
}
Q54
Q56
549
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Q56.0 hermafroditizmi, romelic ar aris Setanili sxva klasifikaciebSiO ovotestis (sasqeso jirkvali sakvercxisa da saTeslis komponentebiT)
Q56.1 mamakacis fsevdohermafroditizmi, romelic ar aris Setanili sxvaklasifikaciebSimamakacis fsevdohermafroditizmi, romelic sxvagvarad ar aris dazustebuli
Q56.2 qalis fsevdohermafroditizmi, romelic ar aris Setanili sxva klasifikaciebSiqalis fsevdohermafroditizmi, romelic sxvagvarad ar aris dazustebuli
Q56.3 fsevdohermafroditizmi, dauzustebeliQ56.4 ganusazRvreli sqesi, dauzustebeli
ormagi sasqeso organoebi
saSarde sistemis Tandayolili mankebi
(Q60-Q64)Tirkmlis agenezia da Tirkmlis sxva reduqciuli defeqtebi
igulisxmeba: Tirkmlis atrofia: Tandayolili, infantiluri
Tirkmlis Tandayolili ararseboba
Q60.0 Tirkmlis agenezia, calmxriviQ60.1 Tirkmlis agenezia, ormxriviQ60.2 Tirkmlis agenezia, dauzustebeliQ60.3 Tirkmlis hipoplazia, calmxriviQ60.4 Tirkmlis hipoplazia, ormxriviQ60.5 Tirkmlis hipoplazia, dauzustebeliQ60.6 poteris sindromi
Tirkmlis kisturi avadmyofoba
ar igulisxmeba: Tirkmlis SeZenili kista (N 28.1); poteris sindromi (Q 60.6)Q61.0 Tirkmlis erTi Tandayolili kista
Tirkmlis kista (Tandayolili)(erTi)
Q61.1 polikisturi Tirkmeli, bavSvTa tipisQ61.2 polikisturi Tirkmeli, mozrdilTa tipisQ61.3 polikisturi Tirkmeli, dauzustebeliQ61.4 Tirkmlis displaziaQ61.5 kista Tirkmlis tvinovan nivTierebaSi
Rrublisebri Tirkmeli, romelic sxvagvarad ar aris dazustebuli
Q61.8 Tirkmlis sxva kisturi avadmyofobebifibrokisturi: Tirkmeli, Tirkmlis degeneracia an avadmyofoba
Q61.9 Tirkmlis kisturi avdmyofoba, dauzustebelimekel-gruberis sindromi
Tirkmlis menjis Tandayolili obstruqciuli defeqtebi da SardsawveTis
Tandayolili mankebi
Q62.0 Tandayolili hidronefroziQ62.1 SardsawveTis atrezia da stenozi
Tandayolili okluzia:
. SardsawveTis
. menj-SardsawveTis segmentis
. SardsawveT-Sardis buStis xvrelis
gauvali SardsawveTi
Q61
Q62
Q60
550
avadmyofobaTa saerTaSoriso klasifikacia
Q62.2 Tandayolili megaloureteriSardsawveTis Tandayolili dilatacia
Q62.3 Tirkmlis menjisa da SardsawveTis sxva obstruqciuli defeqtebiTandayolili ureTerocele
Q62.4 SardsawveTis ageneziaSardsawveTis ararseboba
Q62.5 SardsawveTis gaormageba (ormagi SardsawveTi)SardsawveTi damatebiTi
SardsawveTi ormagi
Q62.6 SardsawveTis mdebareobis mankebigadaxra
gadaadgilebaeqtopiuri
implantacia, anomaluri
Q62.7 Tandayolili Sardis buSt-SardsawveT-Tirkmlis refluqsiQ62.8 SardsawveTis sxva Tandayolili mankebi
SardsawveTis anomalia, romelic sxvagvarad ar aris dazustebuli
Tirkmlis sxva Tandayolili mankebi
ar igulisxmeba: Tandayolili nefrozuli sindromi (N 04.-)Q63.0 damatebiTi TirkmeliQ63.1 wilakebiani, SeerTebuli da nalisebri TirkmeliQ63.2 eqtopiuri Tirkmeli
Tandayolili gadaadgilebuli Tirkmeli
Tirkmlis malrotacia
Q63.3 hiperplaziuri da giganturi TirkmeliQ63.8 Tirkmlis sxva dazustebuli Tandayolili mankebi
Tirkmlis Tandayolili kenWi (konkrementi)
Q63.9 Tirkmlis Tandayolili manki, dauzustebeli
saSarde sistemis sxva Tandayolili mankebi
Q64.0 epispadiaar igulisxmeba: hipospadia (Q 54.-)
Q64.1 Sardis buStis eqstrofiaSardis buStis eqtopia
Sardis buStis eqstroversia
Q64.2 Sardsadenis Tandayolili ukana sarqvlebiQ64.3 Sardsadenisa da Sardis buStis yelis sxva atrezia da stenozi
Tandayolili:
. Sardis buStis yelis obstruqcia
. striqtura
. Sardsadenis
. Sardsadenis gareTa xvrelis
. SardisbuSt-Sardsadenis xvrelis
gauvali Sardsadeni
Q64.4 uraxusis mankiuraxusis kista
Ria uraxusi
uraxusis prolapsi
Q64.5 Sardis buStisa da Sardsadenis Tandayolili ararseboba
} SardsawveTi(s) an SardsawveTis xvreli(s)
Q63
Q64
551
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Q64.6 Sardis buStis Tandayolili divertikuliQ64.7 Sardis buStisa da Sardsadenis sxva Tandayolili mankebi
damatebiTi: Sardis buSti, Sardsadeni
Tandayolili:. Sardis buStis Tiaqari. Sardis buStisa da Sardsadenis manki, romelic sxvagvarad ar aris dazustebuli. prolapsi:
. Sardis buStis (lorwovani garsis)
. Sardsadenis
. Sardsadenis gareTa xvrelis
. Sardsaden - swori nawlavis fistula
ormagi: Sardsadeni, Sardsadenis gareTa xvreli
Q64.8 saSarde sistemis sxva dazustebuli Tandayolili mankebiQ64.9 saSarde sistemis Tandayolili manki, dauzustebeli
Tandayolili:
. anomalia saSarde sistemis, romelic sxvagvarad
. deformacia ar aris dazustebuli
Zval-kunTovani sistemis Tandayolili mankebi da deformaciebi
(Q65-Q79)menj-barZayis saxsris Tandayolili deformaciebi
ar igulisxmeba: menj-barZayis tkacuna saxsari (R29.4)Q65.0 menj-barZayis saxsris Tandayolili amovardniloba, calmxriviQ65.1 menj-barZayis saxsris Tandayolili amovardniloba, ormxriviQ65.2 menj-barZayis saxsris Tandayolili amovardniloba, dauzustebeliQ65.3 menj-barZayis saxsris Tandayolili qveamovardniloba, calmxriviQ65.4 menj-barZayis saxsris Tandayolili qveamovardniloba, ormxriviQ65.5 menj-barZayis saxsris Tandayolili qveamovardniloba, dauzustebeliQ65.6 aramdgradi menj-barZayis saxsari
menj-barZayis saxsris Cveuli amovardniloba
menj-barZayis saxsris Cveuli qveamovardniloba
Q65.8 menj-barZayis saxsris sxva Tandayolili deformaciebibarZayis Zvlis yelis anteverzia
tabuxis fosos Tandayolili displaziamenj-barZayis saxsris Tandayolili:. amobruneba (Signidan gareT)(valgusuri)
. Cabruneba (garedan SigniT)(varusuli)
Q65.9 menj-barZayis saxsris Tandayolili deformacia, dauzustebeli
terfebis Tandayolili deformaciebi
ar igulisxmeba: terfebis reduqciuli defeqtebi (Q72.-)amobrunebuli deformaciebi (SeZenili)(valgusuri) (M21.0)Cabrunebuli deformaciebi (SeZenili)(varusuli) (M21.1)
Q66.0 terfis eqvinovarusuli deformaciaQ66.1 terfis kalkaneurvarusuli deformaciaQ66.2 Metatarsus varus (varusuli winaterfi)Q66.3 terfebis sxva Tandayolili varusuli deformaciebi
varusuli fexis ceri TiTi, Tandayolili
Q66.4 terfis kalkaneur-valgusuri deformaciaQ66.5 Tandayolili brtyelterfianoba
}
Q65
Q66
552
avadmyofobaTa saerTaSoriso klasifikacia
brtyeli terfi
. Tandayolili
. rigiduli
. spazmuri (gadmobrunebuli)
Q66.6 terfebis sxva Tandayolili valgusuri deformaciebiM Metatarsus valgus (valgusuri winaterfi)
Q66.7 Pes cavus (Rrma-TaRovani terfi)Q66.8 terfebis sxva Tandayolili deformaciebi
mrude terfi, romelic sxvagvarad ar aris dazustebuli
CaquCisebri TiTi (fexis), Tandayoliliterfis deformacia: romelic sxvagvarad ar aris dazustebuli, asimetriuliukana terfis Zvlebis Serwyma
vertikaluri koWis Zvali
Q66.9 terfebis Tandayolili deformacia, dauzustebeli
Tavis, saxis, xerxemlisa da gulmkerdis Tandayolili Zval-kunTovani deformaciebi
ar igulisxmeba: Tandayolili mankebis sindromebi, romelTa klasifikacia mocemulia Q87.-Sipoteris sindromi (Q60.6)
Q67.0 saxis asimetriaQ67.1 kompresiuli saxeQ67.2 doliqocefaliaQ67.3 plagiocefaliaQ67.4 Tavis qalas, saxisa da ybebis sxva Tandayolili deformaciebi
Tavis qalas CaRrmavebani
cxviris Zgidis gamrudeba, Tandayolilisaxis naxevris atrofia an hiperplaziamiWyletili an mogrexili cxviri, Tandayoliliar igulisxmeba: kbil-saxis anomaliebi [Tankbilvis CaTvliT](K07.-)
aTaSanguri unagira cxviri (A50.5)Q67.5 xerxemlis Tandayolili deformacia
Tandayolili sqoliozi:
. romelic sxvagvarad ar aris dazustebuli
. posturuliar igulisxmeba: bavSvTa odiopaTiuri sqoliozi (M41.0)
sqoliozi, gamowveuli Zvlis Tandayolili mankiT (Q76.3)Q67.6 Pectus excavatum
Tandayolili mewaRis gulmkerdi
Q67.7 Pectus carinatumTandayolili qaTmis gulmkerdi
Q67.8 gulmkerdis sxva Tandayolili deformaciebigulmkerdis kedlis Tandayolili deformacia, romelic sxvagvarad ar aris dazustebuli
sxva Tandayolili Zval-kunTovani deformaciebi
ar igulisxmeba: kidur(eb)is reduqciuli defeqtebi (Q71-Q73)Q68.0 mkerd-laviw-dvrilisebri kunTis Tandayolili deformacia
Tandayolili (mkerd-dvrilovani) kisermrudoba
mkerd-laviw-dvrilisebri (kunTis) kontraqtura
mkerd-dvrilovani simsivne (Tandayolili)
Q68.1 mtevnis Tandayolili deformaciaTandayolili TiTmrudoba
niCbisebri xeli (Tandayolili)
Q68.2 muxlis Tandayolili deformacia
Q67
Q68
553
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Tandayolili: molaylaye muxli, rekurvaciuli muxli
Q68.3 barZayis Zvlis Tandayolili deformaciaar igulisxmeba: barZayis Zvlis (yelis) anteversia (Q65.8)
Q68.4 didi wvivis Zvlisa da mcire wvivis Zvlis Tandayolili deformaciaQ68.5 fexis grZeli Zvlebis Tandayolili deformacia, dauzustebeliQ68.8 sxva dazustebuli Tandayolili Zval-kunTovani deformaciebi
Tandayolili:
. deformacia: laviwis, idayvis, winamxris, beWis
. gadaadgileba: idayvis, mxris sartylis
polidaqtilia
Q69.0 damatebiTi TiT(eb)i (xelis)Q69.1 damatebiTi cer(eb)i (xelis)Q69.2 damatebiTi TiT(eb)i (fexis)
damatebiTi ceri (fexis)
Q69.9 polidaqtilia, dauzustebelimravali TiT(eb)i, romelic sxvagvarad ar aris dazustebuli
sindaqtilia
Q70.0 Sexorcebuli TiTebi (xelis)TiTebis kompleqsuri sindaqtilia sinostozTan erTad
Q70.1 apkiani TiTebi (xelis)TiTebis martivi sindaqtilia sinostozis gareSe
Q70.2 Sexorcebuli TiTebi (fexis)fexis TiTebis kompleqsuri sindaqtilia sinostozTan erTad
Q70.3 apkiani TiTebi (fexis)fexis TiTebis martivi sindaqtilia sinostozis gareSe
Q70.4 polisindaqtiliaQ70.9 sindaqtilia, dauzustebeli
simfalangia, romelic sxvagvarad ar aris dazustebuli
zeda kiduris reduqciuli defeqtebi
Q71.0 zeda kidur(eb)is Tandayolili sruli ararsebobaQ71.1 mxrisa da winamxris Tandayolili ararseboba mtevnis arsebobasTan erTadQ71.2 orive, winamxrisa da mtevnis Tandayolili ararsebobaQ71.3 xelis mtevnisa da TiT(eb)is Tandayolili ararsebobaQ71.4 sxivis Zvlis sigrZivi reduqciuli defeqti
mrude xeli (Tandayolili)
sxivisZvlismieri mrude xeli
Q71.5 idayvis Zvlis sigrZivi reduqciuli defeqtiQ71.6 kiborCxalis-marwuxisebri xeliQ71.8 zeda kidur(eb)is sxva reduqciuli defeqtebi
Tandayolili mokle zeda kidur(eb)i
Q71.9 zeda kiduris reduqciuli defeqti, dauzustebeli
qveda kiduris reduqciuli defeqtebi
Q72.0 qveda kidur(eb)is Tandayolili sruli ararsebobaQ72.1 barZayisa da kanWis Tandayolili ararseboba terfis arsebobasTan erTadQ72.2 orive kanWisa da terfis Tandayolili ararseboba
Q72
Q69
Q70
Q71
554
avadmyofobaTa saerTaSoriso klasifikacia
Q72.3 terfisa da fexis TiT(eb)is Tandayolili ararsebobaQ72.4 barZayis Zvlis sigrZivi reduqciuli defeqti
barZayis Zvlis proqsimaluri adgilobrivi defeqti
Q72.5 didi wvivis Zvlis sigrZivi reduqciuli defeqtiQ72.6 mcire wvivis Zvlis sigrZivi ruduqciuli defeqtiQ72.7 gaxleCili terfiQ72.8 qveda kidur(eb)is sxva reduqciuli defeqtebi
Tandayolili mokle qveda kidur(eb)i
Q72.9 qveda kiduris reduqciuli defeqti, dauzustebeli
dauzustebeli kiduris reduqciuli defeqtebi
Q73.0 dauzustebeli kidur(eb)is Tandayolili ararsebobaamelia, romelic sxvagvarad ar aris dazustebuli
Q73.1 fokomelia, dauzustebeli, kidur(eb)isfokomelia, romelic sxvagvarad ar aris dazustebuli
Q73.8 dauzustebeli kidur(eb)is sxva reduqciuli defeqtebidauzustebeli kidur(eb)is sigrZivi reduqciuli deformacia
eqtromelia, romelic sxvagvaradar aris dazustebuli kidurebis, romelichemimelia, romelic sxvagvarad sxvagvarad ar arisar aris dazustebuli dazustebuli
reduqciuli defeqti
kidur(eb)is sxva Tandayolili mankebi
ar igulisxmeba: polidaqtilia (Q69.-); kiduris reduqciuli defeqti (Q71-Q73)sindaqtilia (Q70.-)
Q74.0 zeda kidur(eb)is sxva Tandayolili mankebi, mxris sartylis CaTvliTmajis damatebiTi Zvlebi
laviw-qalas dizostozilaviwis Tandayolili fsevdoarTrozimakrodaqtilia (xelis TiTebis)madelungis deformaciasxiv-idayvis sinostoziSprengelis deformacia
samfalangiani ceri (xelis)
Q74.1 muxlis Tandayolili mankiTandayolili: kviristavis ararseboba; kviristavis amovardniloba
muxli: amobrunebuli, Cabrunebulirudimentuli kviristaviar igulisxmeba: Tandayolili: muxlis amovardniloba (Q68.2); rekurvaciuli muxli (Q68.2);
arTrosteonoqo displazia
frCxilis kviristavis sindromi (Q87.2)Q74.2 qveda kidur(eb)is sxva Tandayolili mankebi, menjis CaTvliT
Tandayolili: gava-TeZos saxsris Sexorceba, manki, koW-wvivis (saxsris), gava-TeZos (saxsris)
ar igulisxmeba: barZayis Zvlis (yelis) anteversia (Q65.8)Q74.3 Tandayolili mravlobiTi arTrogripoziQ74.8 kidur(eb)is sxva dazustebuli Tandayolili mankebiQ74.9 kidur(eb)is dauzustebeli Tandayolili manki
kidur(eb)is Tandayolili anomalia, romelic sxvagvarad ar aris dazustebuli
Tavis qalasa da saxis Zvlebis sxva Tandayolili mankebi
ar igulisxmeba: saxis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli (Q18.-)
Q74
Q73
}
Q75
555
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
Tandayolili mankebis sindromebi, romelTa klasifikacia mocemulia Q87-Sikbil-saxis anomaliebi [Tankbilvis CaTvliT] (K07.-)Tavisa da saxis Zval-kunTovani deformaciebi (Q67.0--Q67.4)Tavis qalas defeqtebi, dakavSirebuli Tavis tvinis iseT Tandayolili
anomaliebTan, rogoricaa: anencefalia (Q00.0); encefalocele (Q01.-);hidrocefalia (Q03.-); mikrocefalia (Q02)
Q75.0 kraniosinostoziakrocefalia
Tavis qalas gauvali Sexorcebaoqsicefalia
trigonocefalia
Q75.1 qala-saxis dizostozikruzonis avadmyofoba
Q75.2 hipertelorizmiQ75.3 makrocefaliaQ75.4 qveda-yba-saxis dizostoziQ75.5 Tval-qveda-ybis dizostoziQ75.8 Tavis qalasa da saxis Zvlebis sxva dazustebuli Tandayolili
mankebi
Tavis qalas Zvlis ararseboba, TandayoliliSublis Tandayolili deformacia
platibazia
Q75.9 Tavis qalasa da saxis Zvlebis Tandayolili manki, dauzustebeliTandayolili anomalia:
. saxis Zvlebis, romelic sxvagvarad ar aris dazustebuli
. Tavis qalas, romelic sxvagvarad ar aris dazustebuli
xerxemlisa da gulmkerdis Tandayolili mankebi
ar igulisxmeba: xerxemlisa da gulmkerdis Tandayolili Zval-kunTovani deformaciebi
(Q67.5-Q67.8)Q76.0 faruli Spina bifida
ar igulisxmeba: meningocele (spinuri)(Q05.-)spina bifida (Ria)(kisturi)(Q05.-)
Q76.1 klipel-feilis sindromikisris Sexorcebis sindromi
Q76.2 Tandayolili spondilolisToziTandayolili spondilolizi
ar igulisxmeba: spondilolisTozi (SeZenili)(M43.1); spondilolizi (SeZenili) (M43.0)Q76.3 Tandayolili sqoliozi, gamowveuli Zvlis Tandayolili mankiT
hemivertebruli Sexorceba anu segmentaciis darRveva sqolioziT
Q76.4 xerxemlis sxva Tandayolili mankebi, romlebic ar aris dakavSirebuli sqoliozTanTandayolili:
. malis ararseboba
. malebis Serwyma
. kifozi
. lordozi
. gava-welis (saxsris)(midamos) manki dauzustebeli an sqoliozTan kavSiris gareSenaxevarmalaxerxemlis mankiplatispondilozi
malebis simravle
Q76
}
556
avadmyofobaTa saerTaSoriso klasifikacia
Q76.5 kisris neknineknebis simravle kisris midamoSi
Q76.6 neknebis sxva Tandayolili mankebidamatebiTi nekni
Tandayolili:. neknis ararseboba. neknebis Sexorceba. neknebis mankebi, romlebic sxvagvarad ar aris dazustebuli
ar igulisxmeba: mokle neknis sindromi (Q77.2)Q76.7 mkerdis Zvlis Tandayolili manki
mkerdis Zvlis Tandayolili ararseboba
mkerdis Zvlis naprali (sternum bifidum)Q76.8 gulmkerdis yafazis sxva Tandayolili mankebiQ76.9 gulmkerdis yafazis Tandayolili manki, dauzustebeli
osteoqondrodisplazia lulovani Zvlebisa da xerxemlis zrdis defeqtebiT
ar igulisxmeba: mukopolisaqaridozi (E76.0-E76.3)Q77.0 aqondrogenezi
hipoqondrogenezi
Q77.1 Tanatotropuli dabali aRnagobaQ77.2 mokle neknis sindromi
asfiqsiis gamomwvevi gulmkerdis displazia [junis]
Q77.3 wertilovani qondrodisplaziaQ77.4 aqondroplazia
hipoqondroplazia
Q77.5 distrofiuli displaziaQ77.6 qondroeqtodermuli displazia
elis-van kreveldis sindromi
Q77.7 spondiloepifizuri displaziaQ77.8 sxva osteoqondrodisplazia lulovani Zvlebisa da xerxemlis zrdis defeqtebiTQ77.9 osteoqondrodisplazia lulovani Zvlebisa da xerxemlis zrdis
defeqtebiT, dauzustebeli
sxva osteoqondrodisplazia
Q78.0 arasruli osteogenezimsxvrevadi Zvlebi (Fragilitas ossium)osteopsaTirozi
Q78.1 Zvlebis mravlobiTi dazianebiT mimdinare fibrozuli displaziaolbrait (-mak-kiun)(Sternberg)is sindromi
Q78.2 osteopetrozialbers-Sonabergis sindromi
Q78.3 progresuli diafizuri displaziakamurati-engelmanis sindromi
Q78.4 enqodromatozimafuCis sindromi
olies avadmyofoba
Q78.5 metafizuri displaziapailis sindromi
Q78.6 mravlobiTi Tandayolili egzostozebi
Q77
Q78
557
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
diafizuri aklazia
Q78.8 sxva dazustebuli osteoqondrodisplaziaosteopoikilozi
Q78.9 osteoqondrodisplazia, dauzustebeliqondrodistrofia, romelic sxvagvarad ar aris dazustebuli
osteodistrofia, romelic sxvagvarad ar aris dazustebuli
Zval-kunTovani sistemis Tandayolili mankebi, romlebic ar aris Setanili
sxva klasifikaciebSi
ar igulisxmeba: Tandayolili (mkerd-dvrilovani) kisermrudoba (Q68.0)Q79.0 Tandayolili diafragmuli Tiaqari
ar igulisxmeba: Tandayolili Tiaqris xvreli (Q40.1)Q79.1 diafragmis sxva Tandayolili mankebi
diafragmis ararseboba
diafragmis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli
diafragmis eventracia (relaqsacia)
Q79.2 egzomfalosiomfalocele
ar igulisxmeba: Wipis Tiaqari (K 42.-)Q79.3 gastroSiziQ79.4 “Camovardnili muclis” sindromiQ79.5 muclis kedlis sxva Tandayolili mankebi
ar igulisxmeba: Wipis Tiaqari (K 42.-)Q79.6 elers-danlosis sindromiQ79.8 Zval-kunTovani sistemis sxva Tandayolili mankebi
ararseboba: kunTis, myesis
damatebiTi kunTiTandayolili amiotrofiaTandayolili: momWeri Wimebi, myesis damokleba
polandis sindromi
Q79.9 Zval-kunTovani sistemis Tandayolili manki, dauzustebeliTandayolili:
. anomalia, romelic sxvagvarad ar aris dazustebuli
. deformacia, romelic sxvagvarad ar aris dazustebuli
. Zval-kunTovani sistemis, romelic sxvagvarad ar aris dazustebuli
sxva Tandayolili mankebi
(Q80-Q89)Tandayolili iqTiozi
ar igulisxmeba: refsumis avadmyofoba (G60.1)Q80.0 vulgaruli iqTioziQ80.1 X-SeWiduli iqTioziQ80.2 qerclisebri iqTiozi
koloiduri bavSvi
Q80.3 Tandayolili buStukovani iqTioziformuli eriTrodermaQ80.4 “masxarasebri nayofi”Q80.8 sxva Tandayolili iqTioziQ80.9 Tandayolili iqTiozi, dauzustebeli
Q79
Q80
558
avadmyofobaTa saerTaSoriso klasifikacia
buStukovani epidermolizi
Q81.0 martivi buStukovani epidermoliziar igulisxmeba: kokeinis sindromi (Q87.1)
Q81.1 letaluri buStukovani epidermoliziherlicis sindromi
Q81.2 distrofiuli buStukovani epidermoliziQ81.8 sxva buStukovani epidermoliziQ81.9 buStukovani epidermolizi, dauzustebeli
kanis sxva Tandayolili mankebi
ar igulisxmeba: enteropaTiuli akrodermatiti (E83.2)Tandayolili eriTropoezuri porfiria (E80.0)poloniduri kista anu wiaRi (L05.-)sterj-veber-dimitris sindromi (Q85.8)
Q82.0 memkvidruli limfedemaQ82.1 pigmenturi qserodermaQ82.2 mastocitozi
pigmenturi urtikaria
ar igulisxmeba: avTvisebiani mastocitozi (C96.2)Q82.3 pigmentis SeukaveblobaQ82.4 eqtodermuli displazia (anpidrozuli)
ar igulisxmeba: elis-van kreveldis sindromi (Q77.6)Q82.5 Tandayolili ara-simsivnuri xali
xali, romelic sxvagvarad ar aris dazustebuli
xali:. alisferi. portveinisferi. sisxlsavse. marwyvisebri. sisxlZarRvovani, romelic sxvagvarad ar aris dazustebuli. meWeWovaniar igulisxmeba: rZiani yavisebri laqebi (L81.3)
. lentigo (L81.4)xali:. romelic sxvagvarad ar aris dazustebuli (D22.-). araneus (I78.1). melanocituri (D22.-). pigmenturi (D22.-). obobasebri (I78.1). varskvlavisebri (I78.1)
Q82.8 kanis sxva dazustebuli Tandayolili mankebixelisgulis paTologiuri nakecebi
kanis damatebiTi wanazardebikeTilTvisebiani ojaxuri pemfigusi [heili-heilis]dune kani (hiperelastikuri)dermatoglifiuri anomaliebixelisgulisa da fexisgulis memkvidruli keratozi
folikuluri keratozi [darie-vaitis]
ar igulisxmeba: elers-danlosis sindromi (Q79.6)Q82.9 kanis Tandayolili manki, dauzustebeli
Q81
Q82
559
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
sarZeve jirkvlis Tandayolili mankebi
ar igulisxmeba: mkerdis kunTis ararseboba (Q79.8)Q83.0 sarZeve jirkvlis Tandayolili ararseboba dvrilis ararsebobasTan erTadQ83.1 damatebiTi sarZeve jirkvlebi
mravlobiTi sarZeve jirkvlebi
Q83.2 dvrilis ararsebobaQ83.3 damatebiTi dvrili
mravlobiTi dvrilebi
Q83.8 sarZeve jirkvlis sxva Tandayolili mankebisarZeve jirkvlis hipoplazia
Q83.9 sarZeve jirkvlis Tandayolili manki, dauzustebeli
sxeulis safarvelis sxva Tandayolili mankebi
Q84.0 Tandayolili gamelotebaTandayolili etriqozi (uTmoba)
Q84.1 Tmis Tandayolili morfologiuri dazianebebi, romelic ar aris Setanilisxva klasifikaciebSimZivisebri Tma
monileTriqsi (funjisebri Tma)rgolisebri Tma
ar igulisxmeba: menkesis xveuli Tmis sindromi (E83.0)Q84.2 Tmis sxva Tandayolili mankebi
Tandayolili: hipertriqozi, Tmis manki, romelic sxvagvarad ar aris dazustebuli
darCenili lanugo (RinRli, pirveladi)
Q84.3 anoniqiaar igulisxmeba: frCxil-kviristavis sindromi (Q87.2)
Q84.4 Tandayolili leikoniqiaQ84.5 gafarToebuli da hipertrofiuli frCxilebi
Tandayolili onixauqsisi
paqionixia
Q84.6 frCxilebis sxva Tandayolili mankebiTandayolili: mrude frCxili, koilonixia, frCxilis manki, romelic sxvagvarad ar aris dazustebuli
Q84.8 sxeulis safarvelis sxva dazustebuli Tandayolili mankebikanis Tandayolili aplazia
Q84.9 sxeulis safarvelis Tandayolili manki, dauzustebeliTandayolili:
. anomalia, romelic sxvagvarad ar aris dazustebuli sxeulis safarvelis, romelic
. deformacia, romelic sxvagvarad ar aris dazustebuli sxvagvarad ar aris dazustebuli
fakomatozebi, romlebic ar aris Setanili sxva klasifikaciebSi
ar igulisxmeba: ataqsia telangieqtazia [luis-baris] (G11.3)ojaxuri disavtonomia [rilei-deis] (G90.1)
Q85.0 neirofibromatozi (araavTvisebiani)von reklinghauzenis avadmyofoba
Q85.1 tuberozuli skleroziburnevilis avadmyofoba
epiloia
Q85.8 sxva fakomatozebi, romlebic ar aris Satanili sxva klasifikaciebSisindromi: paic-egersis, sterj-veber (-dimitri)-is, von hipel-lindaus
ar igulisxmeba: mekel-gruberis sindromi (Q61.9)
Q83
Q84
}
Q85
560
avadmyofobaTa saerTaSoriso klasifikacia
Q85.9 fakomatozi, araspecifikurifakomatozi, romelic sxvagvarad ar aris dazustebuli
Tandayolili mankebis sindromebi, gamowveuli cnobili egzogenuri
mizezebiT, romlebic ar aris Setanili sxva klasifikaciebSi
ar igulisxmeba: iodis-deficitTan-dakavSirebuli hipoTiroidizmi (E00-E02)placentiTa da dedis rZiT gadasuli nivTierebebis arateratogenuli efeqtebi (P04.-)
Q86.0 nayofis alkoholuri sindromi (dismorfuli)Q86.1 nayofis hidantoinuri sindromi
midous sindromi
Q86.2 dismorfizmi, gamowveuli varfariniTQ86.8 sxva Tandayolili mankebis sindromebi, gamowveuli cnobili egzogenuri mizezebiT
sxva dazustebuli Tandayolili mankebis sindromebi mravlobiTi sistemebis
dazianebiT
Q87.0 Tandayolili mankebis sindromebi upiratesad saxis ieris dazianebiTakrocefalopolisindaqtiliaakrocefalosindaqtilia [apertis]kriptofTalmuri sindromiciklopiasindromi: goldenharis, mebius, pir-saxe-TiTebis, robinis, triCer kolinzis
mstvenavi saxe
Q87.1 Tandayolili mankebis sindromebi upiratesad dakavSirebuli dabal aRnagobasTansindromi:
. aarskogis
. kokeinis
. de lanJes
. dubovicis
. nunanis
. prader-vilis
. robinov-silvermen-smitis
. rasel-silveris
. sekelis
. smit-lemli-opicis
ar igulisxmeba: elis-van kreveldis sindromi (Q77.6)Q87.2 Tandayolili mankebis sindromebi upiratesad kidurebis dazianebiT
sindromi:
. holt-oramis
. klipel-trenone-veberis
. frCxilisebri kviristavis
. rubinStain-teibis
. sirenomeliuri
. Trombocitopeniuri sxivis Zvlis ararsebobiT [TAR]
. VATERQ87.3 ganviTarebis Tandayolili mankebis sindromebi, romlebic Seexeba adreul
Warb zrdassindromi: bekviT-videmanis, zotos, viaveris
Q87.4 marfanis sindromiQ87.5 ganviTarebis Tandayolili mankebis sxva sindromebi ConCxis sxva cvlilebebiTQ87.8 sxva dazustebuli ganviTarebis Tandayolili mankebis sindromebi,
romlebic ar aris Setanili sxva klasifikaciebSisindromi: alportis, laurens - mune (-barde)-bidlis, zelvegeris
Q86
Q87
561
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
sxva Tandayolili mankebi, romlebic ar aris Setanili sxva klasifikaciebSi
Q89.0 elenTis ganviTarebis Tandayolili mankebiasplenia (Tandayolili)
Tandayolili splenomegalia
ar igulisxmeba: winagulis yurebis izomurizmi (aspleniiT an polispleniiT) (Q 20.6)Q89.1 Tirkmelzeda jirkvlis ganviTarebis Tandayolili mankebi
ar igulisxmeba: Tirkmelzeda jirkvlis Tandayolili hiperplazia (E25.0)Q89.2 sxva endokrinuli jirkvlebis ganviTarebis Tandayolili mankebi
farisebraxlo an farisebri jirkvlis ganviTarebis Tandayolili mankebi
persistuli farisebr-enis sadinari
farisebr-enis kista
Q89.3 Situs inversus (gaukuRmarTebuli ganlageba)deqstrokardia Situs inversus-Tan erTad
winagulis sarkisebri (anareklisebri) ganlageba Situs inversus-Tan erTadgaukuRmarTebuli an ganivi ganlageba: muclis Rrusa da gulmkerdis Rrus organoebisSinagan organoTa transpozicia: gulis Rrus, gulmkerdis
ar igulisxmeba: deqstrokardia, romelic sxvagvarad ar aris dazustebuli (Q 24.0)Q89.4 Sezrdili tyupebi
kraniopagusidicefaliaormagi monstrifigofagusi
Torakopagusi
Q89.7 ganviTarebis mravlobiTi Tandayolili mankebi, romlebic ar arisSetanili sxva klasifikaciebSimonstri, romelic sxvagvarad ar aris dazustebuli
mravlobiTi Tandayolili:. anomaliebi, romelic sxvagvarad ar aris dazustebuli. deformaciebi, romelic sxvagvarad ar aris dazustebuliar igulisxmeba: ganviTarebis Tandayolili mankebis sindromebi, mravlobiTi sistemebis
dazianebiT (Q 87.-)Q89.8 sxva dazustebuli ganviTarebis Tandayolili mankebiQ89.9 ganviTarebis Tandayolili mankebi, dauzustebeli
Tandayolili
. anomalia, romelic sxvagvarad ar aris dazustebuli
. deformacia, romelic sxvagvarad ar aris dazustebuli
qromosomuli darRvevebi, romlebic ar aris Setanili sxva klasifikaciebSi
(Q90 - Q99)daunis sindromi
Q90.0 trosomia 21, meiozuri gauTiSvelobaQ90.1 trisomia 21, mozaicizmi (mitozuri gauTiSveloba)Q90.2 trisomia 21, translokaciaQ90.9 daunis sindromi, dauzustebeli
trisomia 21, romelic sxvagvarad ar aris dazustebuli
edvardsis sindromi da pataus sindromi
Q91.0 trisomia 18, meiozuri gauTiSvelobaQ91.1 trisomia 18, mozaicizmi (mitozuri gauTiSveloba)
Q89
Q90
Q91
562
avadmyofobaTa saerTaSoriso klasifikacia
Q91.2 trisomia 18, translokaciaQ91.3 edvardsis sindromi, dauzustebeliQ91.4 trisomia 13, meiozuri gauTiSvelobaQ91.5 trisomia 13, mozaicizmi (mitozuri gauTiSveloba)Q91.6 trisomia 13, translokaciaQ91.7 pataus sindromi, dauzustebeli
autosomebis nawilobrivi trisomiebi da sxva trisomiebi, romlebic ar
aris Setanili sxva klasifikaciebSi
igulisxmeba: arabalansirebuli translokaciebi da inserciebi
ar igulisxmeba: 13, 18, 21 qromosomebis trisomiebi (Q 90 - Q 91)Q92.0 mTliani qromosomis trisomia, meiozuri gauTiSvelobaQ92.1 mTliani qromosomis trisomia, mozaicizmi (mitozuri gauTiSveloba)Q92.2 didi nawilobrivi trisomia
mTliani mxari an metia gaormagebuli
Q92.3 mcire nawilobrivi trisomiamTlian mxarze naklebia gaormagebuli
Q92.4 gaormageba, romelic mxolod prometafazaSi CansQ92.5 gaormageba, danarCeni kompleqsuri cvlilebebiTQ92.6 eqstra markeruli qromosomebiQ92.7 triploidia da poliploidiaQ92.8 sxva dauzustebeli trosomiebi da autosomebis nawilobrivi trisomiebiQ92.9 autosomebis trisomia da nawilobrivi trisomia, dauzustebeli
autosomebis monosomiebi da deleciebi, romlebic ar aris Setanili
sxva klasifikaciebSi
Q93.0 mTliani qromosomis monosomia, meiozuri gauTiSvelobaQ93.1 mTliani qromosomis monosomia, mozaicizmi (mitozuri gauTiSveloba)Q93.2 qromosoma, gardaqmnil rgolad an dicentruladQ93.3 4 qromosomis mokle mxris delecia
volf - hirSxornis sindromi
Q93.4 5 qromosomis mokle mxris deleciakatis knavilis (Cri-du-chat) sindromi
Q93.5 qromosomis Semadgeneli nawilebis sxva deleciebiQ93.6 deleciebi, romelic mxolod prometafazaSi CansQ93.7 deleciebi sxva kompleqsuri gardaqmnebiTQ93.8 autosomebis sxva deleciebiQ93.9 autosomebis delecia, dauzustebeli
balansirebuli gardaqmnebi da struqturuli markerebi, romelic ar aris
Setanili sxva klasifikaciebSi
igulisxmeba: robertsonis da balansirebuli reciprokuli translokaciebi da inserciebi
Q95.0 balansirebuli translokacia da insercia normul individSiQ95.1 qromosomis inversia normul individSiQ95.2 balansirebuli autosomuri gardaqmnebi aranormalur individSiQ95.3 balansirebuli sasqeso/autosomuri gardaqmnebi aranormalur individSiQ95.4 individebi markeruli heteroqromatiniTQ95.5 individebi autosomis msxvrevadi ubnebiTQ95.8 sxva balansirebuli gardaqmnebi da struqturuli markerebiQ95.9 balansirebuli gardaqmna da struqturuli markeri, dauzustebeli
Q92
Q95
Q93
563
Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi
terneris sindromi
ar igulisxmeba: nunenis sindromi (Q 87.1)Q96.0 kariotipi 45,XQ96.1 kariotipi 46,X iso (Xq)Q96.2 kariotipi 46,X aranormuli sasqeso qromosomiT, garda iso (Xq)Q96.3 mozaicizmi, 45,X/46, XX an XYQ96.4 mozaicizmi, 45,X/ sxva ujreduli xazi (ebi) aranormuli sasqeso qromosomiTQ96.8 terneris sindromis sxva variantebiQ96.9 terneris sindromi, dauzustebeli
sasqeso qromosomebis sxva darRvevebi, qalis fenotipi, romelic ar
aris Setanili sxva klasifikaciebSi
ar igulisxmeba: terneris sindromi (Q 96.-)Q97.0 kariotipi 47, XXXQ97.1 qali samze meti X qromosomiTQ97.2 mozaicizmi, xazebi X qromosomebis sxvadasxva raodenobiTQ97.3 qali 46, XY kariotipiTQ97.8 sasqeso qromosomebis sxva dazustebuli anomaliebi, qalis fenotipiQ97.9 sasqeso qromosomis anomalia, qalis fenotipi, dauzustebeli
sasqeso qromosomebis sxva darRvevebi, mamakacis fenotipi, romelic ar
aris Setanili sxva klasifikaciebSi
Q98.0 klainefelteris sindromi, kariotipi 47,XXYQ98.1 klainefelteris sindromi, mamakaci orze meti X qromosomiTQ98.2 klainefelteris sindromi, mamakaci 46,XX kariotipiTQ98.3 sxva tipis mamakaci, 46,XX kariotipiTQ98.4 klainefelteris sindromi, dauzustebeliQ98.5 kariotipi 47,XYYQ98.6 mamakaci struqturulad aranormuli sasqeso qromosomiTQ98.7 mamakaci sasqeso qromosomis mozaicizmiTQ98.8 sasqeso qromosomebis sxva dazustebuli anomaliebi, mamakacis fenotipiQ98.9 sasqeso qromosomis anomalia, mamakacis fenotipi, dauzustebeli
sxva qromosomuli darRvevebi, romlebic ar aris Setanili sxva
klasifikaciebSi
Q99.0 qimera 46,XX/46,XYqimera 46,XX/46,XY WeSmariti hermafroditi
Q99.1 46, XX WeSmariti hermafroditi46, XX zonriseburi gonadebiT46, XY zonriseburi gonadebiTsufTa gonadebis disgenezia
Q99.2 fragiluri X qromosomafragiluri X qromosomis sindromi
Q99.8 sxva dazustebuli qromosomuli darRvevebiQ99.9 qromosomuli darRveva, dauzustebeli
Q97
Q98
Q96
Q99