tandayolili mankebi, deformaciebi da qromosomuli darrvevebi … · 2015. 1. 23. · q12.2 brolis...

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529 Tavi XVII. Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi (Q00-Q99) ar igulisxmeba: metabolizmis Tandayolili darRvevebi (E 70-E 90) es Tavi moicavs Semdeg blokebs: Q00-Q07 nervuli sistemis Tandayolili mankebi Q10-Q18 Tvalis, yuris, saxisa da kisris Tandayolili mankebi Q20-Q28 sisxlis mimoqcevis sistemis Tandayolili mankebi Q30-Q34 sunTqvis sistemis Tandayolili mankebi Q35-Q37 tuCis naprali da sasis naprali Q38-Q45 saWmlis momnelebeli sistemis sxva Tandayolili mankebi Q50-Q56 sasqeso organoebis Tandayolili mankebi Q60-Q64 saSarde sistemis Tandayolili mankebi Q65-Q79 Zval-kunTovani sistemis Tandayolili mankebi da deformaciebi Q80-Q89 sxva Tandayolili mankebi Q90-Q99 qromosomuli darRvevebi, romlebic ar aris Setanili sxvaklasifikaciebSi nervuli sistemis Tandayolili mankebi (Q00-Q07) anencefalia da msgavsi mankebi Q00.0 anencefalia acefalia akrania amielencefalia hemianencefalia hemicefalia Q00.1 kranioraqiSizi Q00.2 iniencefalia encefalocele igulisxmeba: encefalomielocele hidroencefalocele hidromeningocele, kraniuli meningocele, cerebruli meningoencnfalocele ar igulisxmeba: mekel-gruberis sindromi (Q 61.9) Q01.0 Sublis encefalocele Q01.1 cxvir-Sublis encefalocele Q01.2 kefis encefalocele Q01.8 encefalocele sxva lokalizaciiT Q01.9 encefalocele, dauzustebeli mikrocefalia hidromikrocefalia mikrencefaloni ar igulisxmeba: mekel-gruberis sindromi (Q 61.9) Tandayolili hidrocefalia igulisxmeba: hidrocefalusi axalSobilebSi Q00 Q01 Q02 Q03

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Page 1: Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi … · 2015. 1. 23. · Q12.2 brolis koloboma Q12.3 Tandayolili afakia Q12.4 sferofakia Q12.8 brolis sxva Tandayolili mankebi

529

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Tavi XVII.

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

(Q00-Q99)

ar igulisxmeba: metabolizmis Tandayolili darRvevebi (E 70-E 90)

es Tavi moicavs Semdeg blokebs:

Q00-Q07 nervuli sistemis Tandayolili mankebiQ10-Q18 Tvalis, yuris, saxisa da kisris Tandayolili mankebiQ20-Q28 sisxlis mimoqcevis sistemis Tandayolili mankebiQ30-Q34 sunTqvis sistemis Tandayolili mankebiQ35-Q37 tuCis naprali da sasis napraliQ38-Q45 saWmlis momnelebeli sistemis sxva Tandayolili mankebiQ50-Q56 sasqeso organoebis Tandayolili mankebiQ60-Q64 saSarde sistemis Tandayolili mankebiQ65-Q79 Zval-kunTovani sistemis Tandayolili mankebi da deformaciebiQ80-Q89 sxva Tandayolili mankebi

Q90-Q99 qromosomuli darRvevebi, romlebic ar aris Setanili sxvaklasifikaciebSi

nervuli sistemis Tandayolili mankebi

(Q00-Q07)anencefalia da msgavsi mankebi

Q00.0 anencefaliaacefalia

akraniaamielencefaliahemianencefalia

hemicefalia

Q00.1 kranioraqiSiziQ00.2 iniencefalia

encefalocele

igulisxmeba: encefalomielocele

hidroencefalocelehidromeningocele, kraniulimeningocele, cerebrulimeningoencnfalocele

ar igulisxmeba: mekel-gruberis sindromi (Q 61.9)Q01.0 Sublis encefaloceleQ01.1 cxvir-Sublis encefaloceleQ01.2 kefis encefaloceleQ01.8 encefalocele sxva lokalizaciiTQ01.9 encefalocele, dauzustebeli

mikrocefalia

hidromikrocefalia

mikrencefaloni

ar igulisxmeba: mekel-gruberis sindromi (Q 61.9)

Tandayolili hidrocefalia

igulisxmeba: hidrocefalusi axalSobilebSi

Q00

Q01

Q02

Q03

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530

avadmyofobaTa saerTaSoriso klasifikacia

}Tavis tvinis, romelic sxvagvarad ar aris dazustebuli

ar igulisxmeba: arnold-Ciaris sindromi (Q 07.0)hidrocefalusi:. SeZenili (G 91.-). gamowveuli Tandayolili toqsoplazmoziT (P 37.1). spina bifida-sTan erTad (Q 05.0-Q 05.4)

Q03.0 silviusis wyalsadenis mankebisilviusis wyalsadenis

. anomalia

. obstruqcia, Tandayolili

. stenozi

Q03.1 maJendisa da luSkas xvrelebis atreziadendi-uokeris sindromi

Q03.8 sxva Tandayolili hidrocefalusiQ03.9 Tandayolili hidrocefalusi, dauzustebeli

Tavis tvinis sxva Tandayolili mankebi

ar igulisxmeba: ciklopia (Q 87.0)makrocefalia (Q 75.3)

Q04.0 korZiani sxeulis Tandayolili mankebikorZiani sxeulis agenezia

Q04.1 arinencefaliaQ04.2 holoprozencefaliaQ04.3 Tavis tvinis madeformirebeli sxva reduqciebi

ararseboba

ageneziaaplaziahipoplaziaagiriahidranencefalializencefaliamikrogiriapaqigiria

ar igulisxmeba: korZiani sxeulis Tandayolili mankebi (Q 04.0)Q04.4 septur-optikuri displaziaQ04.5 megalencefaliaQ04.6 Tandayolili cerebruli kistebi

porencefaliaSizencefalia

ar igulisxmeba: SeZenili porencefaluri kista (G 93.0)Q04.8 Tavis tvinis sxva dazustebuli Tandayolili mankebi

makrogiria

Q04.9 Tavis tvinis Tandayolili manki, dauzustebeliTandayolili:. anomalia. deformacia. avadmyofoba an dazianeba

. mravlobiTi anomaliebi

Spina bifidaigulisxmeba: hidromeningocele (spinuri)

meningocele (spinuri)meningomielocele

Q04

Tavis tvinis nawilis}

Q05

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531

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

mielocelemielomeningoceleraqiSizispina bifida (naprali)(kisturi)siringomielocele

ar igulisxmeba: arnold-Ciaris sindromi (Q 07.0)faruli spina bifida (Q 76.0)

Q05.0 kisris spina bifida hidrocefalusiTQ05.1 gulmkerdis spina bifida hidrocefalusiT

spina bifida:. zurgis

. gulmkerd-welis

Q05.2 welis spina bifida hidrocefalusiTgava-welis spina bifida hidrocefalusiT

Q05.3 gavis spina bifida hidrocefalusiTQ05.4 dauzustebeli spina bifida hidrocefalusiTQ05.5 kisris spina bifida hidrocefalusis gareSeQ05.6 gulmkerdis spina bifida hidrocefalusis gareSe

spina bifida:. zurgis, romelic sxvagvarad ar aris dazustebuli

. gulmkerd-welis, romelic sxvagvarad ar aris dazustebuli

Q05.7 welis spina bifida hidrocefalusis gareSegava-welis spina bifida, romelic sxvagvarad ar aris dazustebuli

Q05.8 gavis spina bifida hidrocefalusis gareSeQ05.9 Spina bifida, dauzustebeli

zurgis tvinis sxva Tandayolili mankebi

Q06.0 amieliaQ06.1 zurgis tvinis hipoplazia da displazia

atelomielia

mielateliazurgis tvinis mielodisplazia

Q06.2 diastematomieliaQ06.3 raSis kudis sxva Tandayolili mankebiQ06.4 hidromielia

hidroraqisi

Q06.8 zurgis tvinis sxva dazustebuli Tandayolili mankebiQ06.9 zurgis Tvinis Tandayolili manki, dauzustebeli

Tandayolili

. anomalia

. deformacia

. avadmyofoba an dazianeba

nervuli sistemis sxva Tandayolili mankebi

ar igulisxmeba: ojaxuri disavtonomia [raili-deis] (G 90.1)neirofibromatozi (araavTvisebiani)(Q 85.0)

Q07.0 arnold-Ciaris sindromiQ07.8 nervuli sistemis sxva dazustebuli Tandayolili mankebi

nervis agenezia

mxris wnulis gadanacvlebaquTuTo-qvedaybis sinkineziis sindromi

} hidrocefalusiT

Q06

Q07

}zurgis tvinis an garsebis, romelic

sxvagvarad ar aris dazustebuli

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532

avadmyofobaTa saerTaSoriso klasifikacia

} Tvalis

markus gunis sindromi

Q07.9 nervuli sistemis Tandayolili manki, dauzustebeliTandayolili:

. anomalia

. deformacia

. avadmyofoba an dazianeba

Tvalis, yuris, saxisa da kisris Tandayolili mankebi

(Q10-Q18)ar igulisxmeba: kurdRlis tuCi da mglis xaxa (Q 35-Q 37)

Tandayolili manki:. xerxemlis kisris nawilis (Q 05.0, Q 05.5, Q 67.5,Q 76.0-Q 76.4). xorxis (Q 31.-). tuCis, romelic ar aris Setanili sxva klasifikaciebSi (Q 38.0). cxviris (Q 30.-). farisebraxlo jirkvlis (Q 89.2). farisebri jirkvlis (Q 89.2)

Q quTuTos, sacremle aparatisa da Tvalbudis Tandayolili mankebi

ar igulisxmeba: kriptofTalmi:

. romelic sxvagvarad ar aris dazustebuli (Q 11.2)

. sindromi (Q 87.0)Q10.0 Tandayolili ftoziQ10.1 Tandayolili eqtropioniQ10.2 Tandayolili entropioniQ10.3 quTuTos sxva Tandayolili mankebi

ablefaroni

ararseboba an agenezia:. wamwamebis. quTuToebisdamatebiTi:. quTuTo

. Tvalis kunTebi

blefarofimozi, Tandayolili

quTuTos kolobomaquTuTos Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

Q10.4 ararseboba da agenezia sacremle aparatissacremle wertilis ararseboba

Q10.5 sacremle sadinris Tandayolili stenozi da striqturaQ10.6 sacremle aparatis sxva Tandayolili mankebi

sacremle aparatis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

Q10.7 Tvalbudis Tandayolili manki

anofTalmi, mikrofTalmi da makrofTalmi

Q11.0 kisturi Tvalis kakaliQ11.1 sxva anofTalmi

agenezia

aplazia

Q11.2 mikrofTalmikriptofTalmi, romelic sxvagvarad ar aris dazustebuli

Tvalis displaziaTvalis hipoplazia

nervuli sistemis, romelic sxvagvarad ar

aris dazustebuli}

Q10

Q11

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533

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

rudimentuli Tvaliar igulisxmeba: kriptofTalmuri sindromi (Q 87.0)

Q11.3 makrofTalmiar igulisxmeba: makrofTalmi Tandayolili glaukomis dros (Q 15.0)

brolis Tandayolili mankebi

Q12.0 Tandayolili kataraqtaQ12.1 Tandayolili gadanacvlebuli broliQ12.2 brolis kolobomaQ12.3 Tandayolili afakiaQ12.4 sferofakiaQ12.8 brolis sxva Tandayolili mankebiQ12.9 brolis Tandayolili manki, dauzustebeli

Tvalis wina segmentis Tandayolili mankebi

Q13.0 feradi garsis kolobomakoloboma, romelic sxvagvarad ar aris dazustebuli

Q13.1 feradi garsis ararsebobaaniridia

Q13.2 feradi garsis sxva Tandayolili mankebianizokoria, Tandayolili

gugis atreziaferadi garsis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

koreqtopia

Q13.3 rqovanas Tandayolili SemRvrevaQ13.4 rqovanas sxva Tandayolili mankebi

rqovanas Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

mikrorqovana

piteris anomalia

Q13.5 lurji skleraQ13.8 Tvalis wina segmentis sxva Tandayolili mankebi

raijeris anomalia

Q13.9 Tvalis wina segmentis Tandayolili manki, dauzustebeli

Tvalis ukana segmentis Tandayolili mankebi

Q14.0 minisebri sxeulis siTxis Tandayolili mankiminisebri sxeulis Tandayolili SemRvreva

Q14.1 baduris Tandayolili mankibaduris Tandayolili anevrizma

Q14.2 mxedvelobis nervis diskis Tandayolili mankimxedvelobis nervis diskis koloboma

Q14.3 sisxlZarRvovani garsis Tandayolili mankiQ14.8 Tvalis ukana segmentis sxva Tandayolili mankebi

Tvalis fskeris koloboma

Q14.9 Tvalis ukana segmentis Tandayolili manki, dauzustebeli

Tvalis sxva Tandayolili mankebi

ar igulisxmeba: Tandayolili nistagmi (H 55); Tvalis albinizmi (E 70.3); pigmenturi retiniti (H 35.5)Q15.0 Tandayolili glaukoma

bufTalmi

Q12

Q13

Q14

Q15

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534

avadmyofobaTa saerTaSoriso klasifikacia

axalSobilTa glaukomahidrofTalmikeratoglobusi, TandayolilimakrofTalmi Tandayolili glaukomis dros

megalokornea

Q15.8 Tvalis sxva dazustebuli Tandayolili mankebiQ15.9 Tvalis Tandayolili manki, dauzustebeli

Tandayolili:

. anomalia

. deformacia

yuris Tandayolili mankebi, romlebic iwvevs smenis daqveiTebas

ar igulisxmeba: Tandayolili siyrue (H 90.-)Q16.0 (yuris) niJaris Tandayolili ararsebobaQ16.1 sasmeni milis (gareTa) Tandayolili ararseboba, atrezia an striqtura

Zvlovani gasavlis atrezia an striqtura

Q16.2 evstaqis milis ararsebobaQ16.3 sasmeni Zvlebis Tandayolili manki

sasmeni Zvlebis Serwyma

Q16.4 Sua yuris sxva Tandayolili mankebiSua yuris Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

Q16.5 SigniTa yuris Tandayolili mankianomaluri:. apkovani labirinTi

. kortis organo

Q16.9 yuris Tandayolili manki, romelic iwvevs smenis daqveiTebas, dauzustebeliyuris Tandayolili ararseboba, romelic sxvagvarad ar aris dazustebuli

yuris sxva Tandayolili mankebi

ar igulisxmeba: preaurikuluri wiaRi (Q 18.1)

Q17.0 damatebiTi yuris niJaradamatebiTi wina saxuri

poliotia (mravalyurianoba)preaurikuluri danamati anu wanazardizedmeti:. yuri

. wilaki

Q17.1 makrotiaQ17.2 mikrotiaQ17.3 sxva araswori formis yuri

miniSnebuli yuri

Q17.4 araswori mdebareobis yuriyurebis dabla mdebareoba

ar igulisxmeba: kisris yuri (Q 18.2)Q17.5 warziduli yuri

Ramuris yuri

Q17.8 yuris sxva dazustebuli Tandayolili mankebiyuris wilis Tandayolili ararseboba

Q17.9 yuris Tandayolili manki, dauzustebeliyuris Tandayolili anomalia, romelic sxvagvarad ar aris dazustebuli

Q16

Q17

} Tvalis, romelic ar aris dazustebuli

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535

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

saxisa da kisris sxva Tandayolili mankebi

ar igulisxmeba: kurdRlis tuCi da mglis xaxa (Q 35-Q 37)mdgomareobebi, romelTa klasifikacia mocemulia Q 67.0-Q 67.4-SiTavis qalasa da saxis Zvlebis Tandayolili mankebi (Q 75.-); ciklopia (Q 87.0)kbil-saxis anomaliebi [Tankbilvis anomaliis CaTvliT] (K 07.-)mankiani sindromebi, romelic iwvevs saxis damaxinjvebas (Q 87.0)persistenciuli far-enis sadinari (Q 89.2)

Q18.0 salayuCe napralis wiaRi, fistula da kistasalayuCe rudimenti (kvali)

Q18.1 preaurikuluri (yuriswina) wiaRi da kistafistula:

. yuris niJaris, Tandayolili

. kiser-yuris

Q18.2 salayuCe napralis sxva mankebisalayuCe napralis manki, romelic sxvagvarad ar aris dazustebuli

kisris (kisris gverdiTi) fistula

otocefalia

Q18.3 kisris nakecebiyelis pterigiumi

Q18.4 makrostomiaQ18.5 mikrostomiaQ18.6 makroxeilia

tuCis hipertrofia, Tandayolili

Q18.7 mikroxeiliaQ18.8 saxisa da kisris sxva dazustebuli Tandayolili mankebi

Sua:

. kista

. fistula saxisa da kisris

. wiaRi

Q18.9 saxisa da kisris Tandayolili manki, dauzustebelisaxisa da kisris Tandayolili anomalia, romelic sxvagvarad ar aris dazustebuli

sisxlis mimoqcevis sistemis Tandayolili mankebi

(Q20-Q28)gulis kamerebisa da damakavSirebeli struqturebis Tandayolili mankebi

ar igulisxmeba: deqstrokardia sawinaaRmdego mdebareobiT (situs inversus)(Q 89.3)winagulebis ganlageba sarkisebri asaxviT (situs inversus) (Q 89.3)

Q20.0 saerTo arteriuli Reroarteriuli Reros persistencia

Q20.1 magistralur sisxlZarRvTa gamosvla marjvena parkuWidantausig-bingis sindromi

Q20.2 magistralur sisxlZarRvTa gamosvla marcxena parkuWidanQ20.3 parkuWovan sisxlZarRvovani kavSiris darRveva

aortis deqstropozicia

magistralur sisxlZarRvTa transpozicia (sruli)

Q20.4 parkuWi ormagi SesavliTsaerTo parkuWi

samsakniani orwinaguliani guli

erTi parkuWi

Q20.5 winagul-parkuWovani kavSiris darRveva

Q18

}

Q20

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536

avadmyofobaTa saerTaSoriso klasifikacia

koregirebuli transpozicia

L-transpozicia

parkuWTa inversia

Q20.6 winagulTa danamatebis izomerizmiwinagulTa danamatebis izomerizmi aspleniiT an polispleniiT

Q20.8 gulis kamerebisa da damakavSirebeli struqturebis sxva Tandayolili mankebiQ20.9 gulis kamerebisa da damakavSirebeli struqturebis Tandayolili manki,

dauzustebeli

gulis Zgidis Tandayolili mankebi

ar igulisxmeba: gulis Zgidis SeZenili defeqti (I 51.0)

Q21.0 parkuWTaSua Zgidis defeqtiQ21.1 winagulTaSua Zgidis defeqti

gvirgvinovani sinusis defeqti

Ria anu persistirebuli:. ovaluri xvreli. meoradi Zgidis defeqti (tipi II)

venuri wiaRis defeqti

Q21.2 winagul-parkuWovani Zgidis defeqtisaerTo winagul-parkuWovani arxi

sruli winagul-parkuWovani arxi

winagulTaSua pirveladi Zgidis defeqti (tipi I)

Q21.3 falos tetradaparkuWTaSua Zgidis defeqti filtvis arteriis Reros stenoziT an atreziiT, aortis

deqstropoziciiT da marjvena parkuWis hipertrofiiT

Q21.4 aorta-filtvis arteriis Reros defeqtiaortis Zgidis defeqti

aorta-filtvis arteriis Reros sarkmeli

Q21.8 parkuWSua Zgidis defeqtTan dakavSirebuli mdgomareobanieizenmengeris sindromi

falos pentada

Q21.9 gulis ZgideebTan dakavSirebuli Tandayolili mankebi, dauzustebeliZgidis (gulis) defeqti, romelic sxvagvarad ar aris dazustebuli

filtvis arteriis da samkariani sarqvlebis Tandayolili mankebi

Q22.0 filtvis arteriis sarqvlis atreziaQ22.1 filtvis arteriis sarqvlis Tandayolili stenoziQ22.2 filtvis arteriis sarqvlis Tandayolili naklovaneba

filtvis arteriis sarqvlis Tandayolili regurgitacia

Q22.3 filtvis arteriis sarqvlis sxva Tandayolili mankebifiltvis arteriis sarqvlis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

Q22.4 samkariani sarqvlis stenozisamkariani sarqvlis atrezia

Q22.5 ebSteinis anomaliaQ22.6 hipoplaziuri marjvena gulis sindromiQ22.8 samkariani sarqvlis sxva Tandayolili mankebiQ22.9 samkariani sarqvlis Tandayolili manki, dauzustebeli

aortisa da orkariani sarqvlebis Tandayolili mankebiQ23

Q21

Q22

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537

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Q23.0 aortis sarqvlis Tandayolili stenoziaortis Tandayolili:

. atrezia

. stenoziar igulisxmeba: Tandayolili subaortuli stenozi (Q 24.4)

romelic Sedis hipoplaziuri marcxena gulis sindromSi (Q 23.4)Q23.1 aortis sarqvlis Tandayolili naklovaneba

aortis orkariani sarqveli

Tandayolili aortaluri naklovaneba

Q23.2 Tandayolili mitraluri stenoziTandayolili mitraluri atrezia

Q23.3 Tandayolili mitraluri naklovanebaQ23.4 hipoplaziuri marcxena gulis sindromi

aortis Sesavlis an sarqvlis atrezia an gamoxatuli hipoplazia, aswvrivi aortis hipoplaziiT

da marcxena parkuWis defeqturi ganviTarebiT (mitraluri sarqvlis stenoziT an atreziiT)

Q23.8 aortisa da mitraluri sarqvlebis sxva Tandayolili mankebiQ23.9 aortisa da mitraluri sarqvlebis Tandayolili manki, dauzustebeli

gulis sxva Tandayolili mankebi

ar igulisxmeba: endokardiuli fibroelastozi (I 42.4)

Q24.0 deqstrokardiaar igulisxmeba: deqstrokardia situs mversus-iT) (Q 89.3)

winagulebis danamatTa izomerizmi (aspleniiT an polispleniiT) (Q 20.6)winagulebis ganlageba sarkisebri asaxviT situs inversus-iT (Q 89.3)

Q24.1 levokardiaQ24.2 samwinaguliani guliQ24.3 marjvena parkuWis gasavlis stenoziQ24.4 Tandayolili subaortuli stenoziQ24.5 gvirgvinovan arteriaTa mankebi

Tandayolili gvirgvinovani (arteriis) anevrizma

Q24.6 gulis Tandayolili sruli blokadaQ24.8 gulis sxva dazustebuli Tandayolili mankebi

Tandayolili:

. marcxena parkuWis divertikuli

. manki:

. miokardiumis

. perikardiumisgulis araswori mdebareoba (malpozicia)

gulis avadmyofoba

Q24.9 gulis Tandayolili manki, dauzustebeliTandayolili:

. anomalia

. avadmyofoba

msxvili arteriebis Tandayolili mankebi

Q25.0 Ria arteriuli sadinariRia botalis sadinari

persistirebuli arteriuli sadinari

Q25.1 aortis koarqtaciaaortis koarqtacia (arteriuli sadinris wina)(arteriuli sadinris Semdgomi)

Q25.2 aortis atrezia

Q24

Q25

} gulis. romelic sxvagvarad ar aris dazustebuli

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538

avadmyofobaTa saerTaSoriso klasifikacia

} filtvis aretriis

Q25.3 aortis stenoziaortis stenozi, sarqvelzeda

ar igulisxmeba: aortis Tandayolili stenozi (Q 23.0)Q25.4 aortis sxva Tandayolili mankebi

ararseboba

aplaziaTandayolili: aortis. anevrizma. dilataciavalsalvis wiaRis anevrizma (gamskdari)aortis ormagi rkali [aortis sisxlZarRvovani rgoli]aortis hipoplaziadarCenili:. aortis rkalis nadrekebi. marjvena aortis rkali

ar igulisxmeba: aortis hipoplazia hipoplaziuri marcxena gulis sindromis dros (Q 23.4)Q25.5 filtvis arteriis atreziaQ25.6 filtvis arteriis stenoziQ25.7 filtvis arteriis sxva Tandayolili mankebi

aberantiuli filtvis arteria

ageneziaanevrizmaanomaliahipoplazia

filtvis arteriul-venuri anevrizma

Q25.8 magistralur sisxlZarRvTa sxva Tandayolili mankebiQ25.9 magistralur sisxlZarRvTa Tandayolili manki, dauzustebeli

msxvili venebis Tandayolili mankebi

Q26.0 Rru venebis Tandayolili stenoziRru venebis (qveda)(zeda) Tandayolili stenozi

Q26.1 marcxena zeda Rru venaQ26.2 filtvis venebis sruli anomaluri drenaJiQ26.3 filtvis venebis nawilobrivi anomaluri drenaJiQ26.4 filtvis venebis anomaluri kavSirebiQ26.5 karis venuri sistemis anomaluri kavSirebiQ26.6 karis vena - RviZlis arteriuli fistulaQ26.8 msxvili venebis sxva Tandayolili mankebi

Rru venis (qveda)(zeda) ararseboba

qveda Rru venis kenti veniT gagrZelebadarCenili marcxena ukana mTavari vena

~Turquli xmlis~ sindromi

Q26.9 msxvili venis Tandayolili manki, dauzustebeliRru venis (qveda)(zeda) anomalia, romelic sxvagvarad ar aris dazustebuli

periferiuli sisxlZarRvovani sistemis sxva Tandayolili mankebi

ar igulisxmeba: anomaliebi:

. Tavis tvinisa da precerebruli sisxlZarRvebis (Q 28.0--Q 28.3)

. gvirgvinovani sisxlZarRvebis (Q 24.5)

. filtvis arteriis (Q 25.5-Q 25.7)Tandayolili baduris anevrizma (Q 14.1); hemangioma da limfangioma (D 18.-)

Q27.0 Wiplaris arteriis Tandayolili ararseboba da hipoplaziaWiplaris erTi arteria

Q26

}

Q27

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539

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Q27.1 Tirkmlis arteriis Tandayolili stenoziQ27.2 Tirkmlis arteriis sxva Tandayolili mankebi

Tirkmlis arteriis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

Tirkmlis mravali arteria

Q27.3 periferiuli arteriul-venuri mankiarteriul-venuri anevrizma

ar igulisxmeba: SeZenili arteriul-venuri anevrizma (I 77.0)

Q27.4 Tandayolili flebeqtaziaQ27.8 periferiuli sisxlZarRvovani sistemis sxva dazustebuli Tandayolili mankebi

aberaciuli laviwqveSa arteria

ararsebobaatreziaTandayolili. anevrizma (periferiuli). striqtura, arteriis

. varikozi

Q27.9 periferiuli sisxlZarRvovani sistemis Tandayolili manki, dauzustebeliarteriis an venis anomalia, romelic sxvagvarad ar aris dazustebuli

sisxlis mimoqcevis sistemis sxva Tandayolili mankebi

ar igulisxmeba: Tandayolili anevrizma:

. romelic sxvagvarad ar aris dazustebuli (Q 27.8)

. gvirgvinovani (Q 24.5)

. periferiuli (Q 27.8)

. filtvis (Q 25.7)

. baduris (Q 14.1)gamskdari:. Tavis tvinis arteriul-venuri manki (I 60.8)

. precerebruli sisxlZarRvebis manki (I 72.-)

Q28.0 precerebruli sisxlZarRvebis arteriul-venuri mankiTandayolili arteriul-venuri precerebruli anevrizma (gaumskdari)

Q28.1 precerebruli sisxlZarRvebis sxva mankebiTandayolili:

. precerebruli sisxlZarRvebis manki, romelic sxvagvarad ar aris dazustebuli

. precerebruli anevrizma (gaumskdari)

Q28.2 Tavis tvinis sixlZarRvebis arteriul-venuri mankiTavis tvinis arteriul-venuri manki, romelic sxvagvarad ar aris dazustebuli

Tandayolili arteriul-venuri cerebruli anevrizma (gaumskdari)

Q28.3 Tavis tvinis sisxlZarRvebis sxva mankebiTandayolili:. cerebruli anevrizma (gaumskdari). Tavis tvinis sisxlZarRvebis manki, romelic sxvagvarad ar aris dazustebuli

Q28.8 sisxlis mimoqcevis sistemis sxva dazustebuli Tandayolili mankebiTandayolili anevrizma, dazustebuli lokalizaciiT, romelic ar aris Setanili sxva klasifikaciebSi

Q28.9 sisxlis mimoqcevis sistemis Tandayolili manki, dauzustebeli

sasunTqi sistemis Tandayolili mankebi

(Q30-Q34)cxviris Tandayolili mankebi

ar igulisxmeba: cxviris Zgidis Tandayolili gamrudeba (Q 67.4)Q30.0 qoanis atrezia

Q28

Q30

arteriis an venis, romelic ar aris Setanili sxvaklasifikaciebSi}

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540

avadmyofobaTa saerTaSoriso klasifikacia

} beWdisebri xrtilis, xorxsarqvelis, yiis,xorcis an farisebri xrtilis

}

atrezia

Tandayolili stenozi

Q30.1 cxviris agenezia da ganviTarebaSi CamorCenacxviris Tandayolili ararseboba

Q30.2 napralovani, naxeTqisebri da naWdevisebri cxviriQ30.3 Tandayolili dacxriluli cxviris ZgideQ30.8 cxviris sxva Tandayolili mankebi

damatebiTi cxviri

cxviris wiaRTa kedlebis Tandayolili anomalia

Q30.9 cxviris Tandayolili manki, dauzustebeli

xorxis Tandayolili mankebi

Q31.0 xorxis apkixorxis apki:

. romelic sxvagvarad ar aris dazustebuli

. yiis

. yiisqveda

Q31.1 Tandayolili yiisqveda stenoziQ31.2 xorxis hipoplaziaQ31.3 laringoceleQ31.4 xorxis Tandayolili stridori

Tandayolili stridori (xorxis), romelic sxvagvarad ar aris dazustebuli

Q31.8 xorxis sxva Tandayolili mankebiararseboba

ageneziaatreziafarisebri xrtilis napralixorxis Tandayolili stenozi, romelic ar aris Setanili sxva klasifikaciebSixorxsarqvelis naxeTqi

beWdisebri xrtilis ukana naprali

Q31.9 xorxis Tandayolili manki, dauzustebeli

traqeisa da bronqebis Tandayolili mankebi

ar igulisxmeba: Tandayolili bronqoeqtazia (Q 33.4)Q32.0 Tandayolili traqeomalaciaQ32.1 traqeis sxva Tandayolili mankebi

traqeis xrtilis anomalia

traqeis atreziaTandayolili:. gafarToeba. manki traqeis. stenozi

. traqeocele

Q32.2 Tandayolili bronqomalaciaQ32.3 bronqis Tandayolili stenoziQ32.4 bronqis sxva Tandayolili mankebi

ar arseboba

agneziaTandayolili manki,romelic sxvagvarad ar aris dazustebuli

divertikuli

Q31

Q32

cxviris xvrelebis (wina, ukana)}

bronqis}

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541

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

filtvis Tandayolili mankebi

Q33.0 Tandayolili kisturi filtviTandayolili:

. fiWuri filtvi

. filtvis avadmyofoba:

. kisturi

. polikisturi

ar igulisxmeba: filtvis kisturi avadmyofoba, SeZenili an dauzustebeli (J 98.4)Q33.1 filtvis damatebiTi wiliQ33.2 filtvis sekvestraciaQ33.3 filtvis agenezia

filtvis ararseboba (wilis)

Q33.4 Tandayolili bronqeqtaziaQ33.5 eqtopiuri qsovili filtvSiQ33.6 filtvis hipoplazia da displazia

ar igulisxmeba: piltvis hipoplazia, dakavSirebuli dRenaklulobasTan (P 28.0)Q33.8 filtvis sxva Tandayolili mankebiQ33.9 filtvis Tandayolili manki, dauzustebeli

sasunTqi sistemis sxva Tandayolili mankebi

Q34.0 plevris anomaliaQ34.1 Suasayris Tandayolili kistaQ34.8 sunTqvis sistemis sxva dazustebuli Tandayolili mankebi

cxvir-xaxis atrezia

Q34.9 sunTqvis sistemis Tandayolili manki, dauzustebeliTandayolili:. ararseboba. anomalia, romelic sxvagvarad ar aris

dazustebuli

tuCis naprali da sasis naprali

(Q35-Q37)ar igulisxmeba: robinis sindromi (Q 87.0)

sasis naprali

igulisxmeba: sasis naWdevi; palatoSiziar igulisxmeba: mglis xaxa kurdRlis tuCiT (Q 37.-)

Q35.0 magari sasis naprali, ormxriviQ35.1 magari sasis naprali, calmxrivi

magari sasis naprali, romelic sxvagvarad ar aris dazustebuli

Q35.2 rbili sasis naprali, ormxriviQ35.3 rbili sasis naprali, calmxrivi

rbili sasis naprali, romelic sxvagvarad ar aris dazustebuli

Q35.4 magari sasis naprali rbili sasis napraliT, ormxriviQ35.5 magari sasis naprali rbili sasis napraliT, calmxrivi

magari sasis naprali rbili sasis napraliT, romelic sxvagvarad ar aris dazustebuli

Q35.6 sasis naprali, SuaQ35.7 naqis napraliQ35.8 sasis naprali, dauzustebeli, ormxriviQ35.9 sasis naprali, dauzustebeli, calmxrivi

sasis naprali, romelic sxvagvarad ar aris dazustebuli

Q33

Q34

Q35

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542

avadmyofobaTa saerTaSoriso klasifikacia

tuCis naprali

igulisxmeba: xeiloSizi; Tandayolili tuCis naWdevi; kurdRlis tuCi; labium leporinumar igulisxmeba: tuCisa da magari sasis defeqti (Q 37.-)

Q36.0 tuCis naprali, ormxriviQ36.1 tuCis naprali, SuaQ36.9 tuCis naprali, calmxrivi

tuCis naprali, romelic sxvagvarad ar aris dazustebuli

sasis naprali tuCis napralTan erTad

Q37.0 magari sasis naprali tuCis napraliT, ormxriviQ37.1 magari sasis naprali tuCis napraliT, calmxrivi

magari sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli

Q37.2 rbili sasis naprali tuCis napraliT, ormxriviQ37.3 rbili sasis naprali tuCis napraliT, calmxrivi

rbili sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli

Q37.4 magari da rbili sasis naprali tuCis napraliT, ormxriviQ37.5 magari da rbili sasis naprali tuCis napraliT, calmxrivi

magari da rbili sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli

Q37.8 dauzustebeli sasis naprali tuCis napraliT, ormxriviQ37.9 dauzustebeli sasis naprali tuCis napraliT, calmxrivi

sasis naprali tuCis napraliT, romelic sxvagvarad ar aris dazustebuli

saWmlis momnelebeli sistemis sxva Tandayolili mankebi

(Q38-Q45)enis, piris da xaxis sxva Tandayolili mankebi

ar igulisxmeba: makrostomia (Q 18.4); mikrostomia (Q 18.5)Q38.0 tuCebis Tandayolili mankebi, romlebic ar aris Setanili sxva

klasifikaciebSiTandayolili:. tuCis fistula. tuCis manki, romelic sxvagvarad ar aris dazustebulivan der vudis sindromiar igulisxmeba: tuCis naprali (Q 36.-). sasis napraliT (Q 37.-)makroxeilia (Q 18.6)mikroxeilia (Q 18.7)

Q38.1 ankiloglosiadabmuli ena

Q38.2 makroglosiaQ38.3 enis sxva Tandayolili mankebi

aglosiaormagi enaTandayolili:. enis Sexorceba. enis naprali. enis manki, romelic sxvagvarad ar aris dazustebulihipoglosiaenis hipoplazia

mikroglosia

Q38.4 sanerwyve jirkvlebisa da sadinarebis Tandayolili mankebi

Q36

Q37

Q38

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543

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

ararseboba

damatebiTi sanerwyve jirkvlis an sadinarisatrezia

sanerwyve jirkvlis Tandayolili fistula

Q38.5 sasis Tandayolili mankebi, romlebic ar aris Setanili sxva klasifikaciebSinaqis ararseboba

sasis Tandayolili manki, romelic sxvagvarad ar aris dazustebulimaRalTaRiani sasa

ar igulisxmeba: sasis naprali (Q 35.-); enis napraliT (Q 37.-)Q38.6 piris Rrus sxva Tandayolili mankebi

piris Rrus Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

Q38.7 xaxis jibexaxis divertikuli

ar igulisxmeba: xaxis jibis sindromi (D 28.1)Q38.8 xaxis sxva Tandayolili mankebi

xaxis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

saylapavis Tandayolili mankebi

Q39.0 saylapavis atrezia fistulis gareSesaylapavis atrezia, romelic sxvagvarad ar aris dazustebuli

Q39.1 saylapavis atrezia traqeo-saylapavis fistuliTsaylapavi milis atrezia saylapav-bronquli fistuliT

Q39.2 traqeo-saylapavis Tandayolili fistula atreziis gareSeTandayolili sasule-saylapavis fistula, romelic sxvagvarad ar aris dazustebuli

Q39.3 saylapavis Tandayolili stenozi da striqturaQ39.4 saylapavis apkiQ39.5 saylapavis Tandayolili dilataciaQ39.6 saylapavis divertikuli

saylapavi milis jibe

Q39.8 saylapavi milis sxva Tandayolili mankebiararseboba

Tandayolili gadanacvleba saylapavi mili (-is)

gaoreba

Q39.9 saylapavi milis Tandayolili manki, dauzustebeli

alimenturi traqtis zeda nawilis sxva Tandayolili mankebi

Q40.0 Tandayolili hipertrofiuli pilorusis stenoziTandayolili an infantiluri:

. Seviwoeba

. hipertrofia

. spazmi pilorusis

. stenozi

. striqtura

Q40.1 saylapavis milis xvrelis Tandayolili TiaqarikuWis kardiuli nawilis gadanacvleba saylapavi milis xvrelis gavliT

ar igulisxmeba: Tandayolili diafragmuli Tiaqari (Q 79.0)Q40.2 kuWis sxva dazustebuli mankebi

Tandayolili:

. kardiaspazmi

. kuWis gadaadgileba

Q39

Q40

}

}

}

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544

avadmyofobaTa saerTaSoriso klasifikacia

. kuWis divertikuli

. qviSis saaTisebri kuWikuWis gaorebamegalogastria

mikrogastria

Q40.3 kuWis Tandayolili manki, dauzustebeliQ40.8 alimenturi traqtis zeeda nawilis sxva dazustebuli Tandayolili mankebiQ40.9 alimenturi traqtis zeda nawilis Tandayolili manki, dauzustebeli

Tandayolili:

. anomalia alimenturi traqtis zeda nawilis,

. deformacia romelic sxvagvarad ar aris dazustebuli

wvrili nawlavis Tandayolili ararseboba, atrezia da stenozi

igulisxmeba: wvrili nawlavis anu nawlavis Tandayolili obstruqcia, okluzia dastriqtura, romelic sxvagvarad ar aris dazustebuli

ar igulisxmeba: mekoniumiT gamowveuli gauvaloba (E 84.1)Q41.0 Tormetgoja nawlavis Tandayolili ararseboba, atrezia da stenoziQ41.1 mlivi nawlavis Tandayolili ararseboba, atrezia da stenozi

“vaSlis qerqis” sindromi

gauxvretavi (xvrelis gareSe) mlivi nawlavi

Q41.2 TeZos nawlavis Tandayolili ararseboba, atrezia da stenoziQ41.8 wvrili nawlavebis sxva dazustebuli nawilebis Tandayolili ararseboba,

atrezia da stenoziQ41.9 wvrili nawlavebis, dauzustebeli nawilis, Tandayolili ararseboba,

atrezia da stenozi, romelic sxvagvarad ar aris dazustebuli

msxvili nawlavis Tandayolili ararseboba, atrezia da stenozi

igulisxmeba: msxvili nawlavis Tandayolili obstruqcia, okluzia an striqtura

Q42.0 swori nawlavis Tandayolili ararseboba, atrezia da stenozifistulasTan erTad

Q42.1 swori nawlavis Tandayolili ararseboba, atrezia da stenozi fistulis gareSegauxvretavi (xvrelis gareSe) swori nawlavi

Q42.2 yiTas Tandayolili ararseboba, atrezia da stenozi fistulasTan erTadQ42.3 yiTas Tandayolili ararseboba, atrezia da stenozi fistulis gareSe

gauxvretavi (xvrelis gareSe) yiTa

Q42.8 msxvili nawlavis sxva nawilebis Tandayolili ararseboba, atrezia da stenoziQ42.9 msxvili nawlavis, dauzustebeli nawilis, Tandayolili ararseboba, atrezia

da stenozi

nawlavTa sxva Tandayolili mankebi

Q43.0 mekelis divertikulidarCenili:

. omfalur-mezenteriuli sadinari

. yviTris sadinari

Q43.1 hirSprungis avadmyofobaaganglionozi

Tandayolili (aganglionuri) megakoloni

Q43.2 kolinjis sxva Tandayolili funqciuri dazianebebikolinjis Tandayolili dilatacia

Q43.3 nawlavTa fiqsaciis Tandayolili mankebiTandayolili Sexorcebani [Wimebi]:

}

Q42

Q41

Q43

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545

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

. badeqonis, anomaluri

. peritoneumisjeksonis apkikolinjis malrotaciarotacia:. ukmarisoba. dausrulebeli brma nawlavisa da kolinjis. naklovaneba

saerTo (universaluri) jorjali

Q43.4 nawlavis gaormagebaQ43.5 eqtopiuri yiTaQ43.6 swori nawlavisa da yiTas Tandayolili fistula

ar igulisxmeba: Tandayolili fistula:

. swornawlav-saSos (Q 52.2)

. Sardsaden-swori nawlavis (Q 64.7)piloniduri (kudusunis) fistula anu wiaRi swori nawlavis (L 05.-)ararsebobiT, atreziiT da stenoziT (Q 42.0, Q 42.2)

Q43.7 darCenili kloakakloaka, romelic sxvagvarad ar aris dazustebuli

Q43.8 nawlavTa sxva dazustebuli Tandayolili mankebiTandayolili:. brma maryuJis sindromi. divertikuliti, kolinjis. divertikuli, nawlavisdoliqokolinjimegaloapendiqsimegaloduodenumimikrokolinjitranspozicia:. apendiqsis (danamatis). kolinjis

. nawlavis

Q43.9 nawlavTa Tandayolili manki, dauzustebeli

naRvlis buStis, naRvlis sadinarebisa da RviZlis Tandayolili mankebi

Q44.0 naRvlis buStis agenezia, aplazia da hipoplazianaRvlis buStis Tandayolili ararseboba

Q44.1 naRvlis buStis sxva Tandayolili mankebinaRvlis buStis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

RviZliSida naRvlis buSti

Q44.2 naRvlis sadinarebis atreziaQ44.3 naRvlis sadinarebis Tandayolili stenozi da striqturaQ44.4 qoledoqusis (naRvlis saerTo sadinris) kistaQ44.5 naRvlis sadinarebis sxva Tandayolili mankebi

RviZlis damatebiTi sadinari

naRvlis sadinris Tandayolili manki, romelic sxvagvarad ar aris dazustebuligaormageba:. naRvlis sadinaris

. naRvlis buStis sadinaris

Q44.6 RviZlis kisturi avadmyofobaRviZlis kistofibrozuli avadmyofoba

Q44.7 RviZlis sxva Tandayolili mankebidamatebiTi RviZli

}

Q44

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546

avadmyofobaTa saerTaSoriso klasifikacia

alajilis sindromiTandayolili:. RviZlis ararseboba. hepatomegalia

. RviZlis manki, romelic sxvagvarad ar aris dazustebuli

saWmlis momnelebeli sistemis sxva Tandayolili mankebi

ar igulisxmeba: Tandayolili:

. diafragmuli Tiaqari (Q 79.0);

. saylapavi milis xvrelis Tiaqari (Q 40.1)Q45.0 pankreasis agenezia, aplazia da hipoplazia

pankreasis Tandayolili ararseboba

Q45.1 rgolisebri pankreasi (nalisebri)Q45.2 Tandayolili pankreasuli kistaQ45.3 pankreasisa da pankreasis sadinaris sxva Tandayolili mankebi

damatebiTi pankreasi

pankreasisa an pankreasis sadinaris Tandayolili manki, romelic sxvagvarad ar aris dazustebuliar igulisxmeba: Saqriani diabeti:

. Tandayolili (E 10.-)

. neonataluri (P 70.2)pankreasis kistofibrozi (E 84.-)

Q45.8 saWmlis momnelebeli sistemis sxva dazustebuli Tandayolili mankebialimenturi traqtis ararseboba (sruli)(nawilobrivi), romelic sxvagvarad ar aris dazustebuli

gaormageba saWmlis momnelebeli organoebis, romelicmalpozicia, Tandayolili sxvagvarad ar aris dazustebuli

Q45.9 saWmlis momnelebeli sistemis Tandayolili manki, dauzustebeliTandayolili:. anomalia saWmlis momnelebeli sistemis, romelic

. deformacia sxvagvarad ar aris dazustebuli

sasqeso organoebis Tandayolili mankebi

(Q50-Q56)ar igulisxmeba: androgen-rezistentuli sindromi (E 34.5)

qromosomebis ricxvisa da formis anomaliebTan dakavSirebuli sindromebi (Q 90-Q 99)testikuluri feminizaciis sindromi (E 34.5)

sakvercxeebis, falopiusis milebisa da ganieri iogis Tandayolili mankebi

Q50.0 sakvercxis Tandayolili ararsebobaar igulisxmeba: terneris sindromi (Q 96.-)

Q50.1 sakvercxis Canasaxovani kistaQ50.2 sakvercxis Tandayolili SemogrexaQ50.3 sakvercxis sxva Tandayolili mankebi

damatebiTi sakvercxe

sakvercxis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

zonriseburi sakvercxe

Q50.4 falopiusis milis embrionuli kistafibriuli (foCebis) kista

Q50.5 ganieris iogis embrionuli kistakista:

. epooforonis

. gartneris sadinris

. paraovariuli

Q45

}

}

Q50

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547

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Q50.6 falopiusis milisa da ganieri iogis sxva Tandayolili mankebiararseboba

damatebiTi falopiusis mili(s) an ganieri iogi(s)atrezia

falopiusis milis an ganieri iogis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

saSvilosnosa da saSvilosnos yelis Tandayolili mankebi

Q51.0 saSvilosnos agenezia da aplaziasaSvilosnos Tandayolili ararseboba

Q51.1 ormagi saSvilosno ormagi yeliTa da saSoTiQ51.2 saSvilosnos sxva gaormageba

saSvilosnos gaormageba, romelic sxvaggvarad ar aris dazustebuli

Q51.3 orrqiani saSvilosnoQ51.4 calrqiani saSvilosnoQ51.5 saSvilosnos yelis agenezia da aplazia

saSvilosnos yelis Tandayolili ararseboba

Q51.6 saSvilosnos yelis embrionuli kistaQ51.7 Tandayolili fistula saSvilosnosa da saWmlis momnelebel da saSarde

traqtebs SorisQ51.8 saSvilosnosa da saSvilosnos yelis sxva Tandayolili mankebisaSvilosnosa

da saSvilosnos yelis hipoplaziaQ51.9 saSvilosnosa da saSvilosnos yelis Tandayolili manki, dauzustebeli

qalis sasqeso organoebis sxva Tandayolili mankebi

Q52.0 saSos Tandayolili ararsebobaQ52.1 ormagi saSo

Zgidiani saSo

ar igulisxmeba: ormagi saSo ormagi saSvilosnoTi da yeliT (Q 51.1)Q52.2 Tandayolili swor-nawlav - saSos fistula

ar igulisxmeba: kloaka (Q 43.7)Q52.3 mTliani (xvrelis gareSe) saqalwule apkiQ52.4 saSos sxva Tandayolili mankebi

saSos Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

kista:. nakis arxis, Tandayolili

. saSos embrionuli

Q52.5 bageebis SexorcebaQ52.6 savnebos (klitoris) Tandayolili mankiQ52.7 vulvis sxva Tandayolili mankebi

Tandayolili:

. ararseboba

. kista vulvis

. manki, romelic sxvagvarad ar aris dazustebuli

Q52.8 qalis sasqeso organoebis sxva dazustebuli Tandayolili mankebiQ52.9 qalis sasqeso organoebis Tandayolili manki, dauzustebeli

Camousvleli saTesle jirkvali

Q53.0 eqtopiuri saTesle jirkvalicalmxrivi an ormxrivi eqtopiuri saTesle jirkvali

Q53.1 Camousvleli saTesle jirkvali, calmxrivi

Q51

Q52

}

}

Q53

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548

avadmyofobaTa saerTaSoriso klasifikacia

Q53.2 Camousvleli saTesle jirkvali, ormxriviQ53.9 Camousvleli saTesle jirkvali, dauzustebeli

kriptorqizmi, romelic sxvagvarad ar aris dazustebuli

hipospadia

ar igulisxmeba: epispadia (Q 64.0)Q54.0 hipospadia, asos Tavis

hipospadia:

. gvirgvinovani

. jirkvlovani

Q54.1 hipospadia, asos sxeulisQ54.2 hipospadia, aso - saTesle parkisQ54.3 hipospadia, SorisisQ54.4 asos Tandayolili gamrudebaQ54.8 sxva hipospadiaQ54.9 hipospadia, dauzustebeli

mamakacis sasqeso orgaoebis sxva Tandayolili mankebi

ar igulisxmeba: Tandayolili hidrocele (P 83.5); hipospadia (Q 54.-)Q55.0 saTesle jirkvlis ararseboba da aplazia

monorqizmi

Q55.1 saTesle jirkvlisa da saTesle parkis hipoplaziasaTesle jirkvlebis Sexorceba

Q55.2 saTesle jirkvlisa da saTesle parkis sxva Tandayolili mankebisaTesle jirkvlisa da saTesle parkis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

poliorqizmiretraqciuli saTesle jirkvali

moZravi saTesle jirkvali

Q55.3 Teslis gamomtani sadinaris atreziaQ55.4 Teslis gamomtani sadinaris, saTeslis danamatis (epididimisis),

saTesle buStukebisa da winamdebare jirkvlis (prostatis) sxva Tandayolili mankebi

ararseboba an aplazia:. prostatis. saTesle bagirakisTeslis gamomtani sadinaris, epididimisis, saTesle buStukebisa da prostatis Tandayolili

manki, romelic sxvagvarad ar aris dazustebuli

Q55.5 asos Tandayolili ararseboba da aplaziaQ55.6 asos sxva Tandayolili mankebi

asos Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

asos gamrudeba (gverdiTi)

asos hipoplazia

Q55.8 mamakacis sasqeso organoebis sxva dazustebuli Tandayolili mankebiQ55.9 mamakacis sasqeso organos Tandayolili manki, dauzustebeli

Tandayolili:

. anomalia mamakacis sasqeso organosi, romelic sxvagvarad

. deformacia ar aris dazustebuli

ganusazRvreli sqesi da fsevdohermafroditizmi

ar igulisxmeba: fsevdohermafroditizmi:

. qalis, adrenokortikuli dazianebiT (E 25.-)

. mamakacis, androgen-rezistentobiT (E 34.5)

. dazustebuli qromosomuli aberaciiT (Q 96-Q 99)

Q55

}

Q54

Q56

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549

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Q56.0 hermafroditizmi, romelic ar aris Setanili sxva klasifikaciebSiO ovotestis (sasqeso jirkvali sakvercxisa da saTeslis komponentebiT)

Q56.1 mamakacis fsevdohermafroditizmi, romelic ar aris Setanili sxvaklasifikaciebSimamakacis fsevdohermafroditizmi, romelic sxvagvarad ar aris dazustebuli

Q56.2 qalis fsevdohermafroditizmi, romelic ar aris Setanili sxva klasifikaciebSiqalis fsevdohermafroditizmi, romelic sxvagvarad ar aris dazustebuli

Q56.3 fsevdohermafroditizmi, dauzustebeliQ56.4 ganusazRvreli sqesi, dauzustebeli

ormagi sasqeso organoebi

saSarde sistemis Tandayolili mankebi

(Q60-Q64)Tirkmlis agenezia da Tirkmlis sxva reduqciuli defeqtebi

igulisxmeba: Tirkmlis atrofia: Tandayolili, infantiluri

Tirkmlis Tandayolili ararseboba

Q60.0 Tirkmlis agenezia, calmxriviQ60.1 Tirkmlis agenezia, ormxriviQ60.2 Tirkmlis agenezia, dauzustebeliQ60.3 Tirkmlis hipoplazia, calmxriviQ60.4 Tirkmlis hipoplazia, ormxriviQ60.5 Tirkmlis hipoplazia, dauzustebeliQ60.6 poteris sindromi

Tirkmlis kisturi avadmyofoba

ar igulisxmeba: Tirkmlis SeZenili kista (N 28.1); poteris sindromi (Q 60.6)Q61.0 Tirkmlis erTi Tandayolili kista

Tirkmlis kista (Tandayolili)(erTi)

Q61.1 polikisturi Tirkmeli, bavSvTa tipisQ61.2 polikisturi Tirkmeli, mozrdilTa tipisQ61.3 polikisturi Tirkmeli, dauzustebeliQ61.4 Tirkmlis displaziaQ61.5 kista Tirkmlis tvinovan nivTierebaSi

Rrublisebri Tirkmeli, romelic sxvagvarad ar aris dazustebuli

Q61.8 Tirkmlis sxva kisturi avadmyofobebifibrokisturi: Tirkmeli, Tirkmlis degeneracia an avadmyofoba

Q61.9 Tirkmlis kisturi avdmyofoba, dauzustebelimekel-gruberis sindromi

Tirkmlis menjis Tandayolili obstruqciuli defeqtebi da SardsawveTis

Tandayolili mankebi

Q62.0 Tandayolili hidronefroziQ62.1 SardsawveTis atrezia da stenozi

Tandayolili okluzia:

. SardsawveTis

. menj-SardsawveTis segmentis

. SardsawveT-Sardis buStis xvrelis

gauvali SardsawveTi

Q61

Q62

Q60

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550

avadmyofobaTa saerTaSoriso klasifikacia

Q62.2 Tandayolili megaloureteriSardsawveTis Tandayolili dilatacia

Q62.3 Tirkmlis menjisa da SardsawveTis sxva obstruqciuli defeqtebiTandayolili ureTerocele

Q62.4 SardsawveTis ageneziaSardsawveTis ararseboba

Q62.5 SardsawveTis gaormageba (ormagi SardsawveTi)SardsawveTi damatebiTi

SardsawveTi ormagi

Q62.6 SardsawveTis mdebareobis mankebigadaxra

gadaadgilebaeqtopiuri

implantacia, anomaluri

Q62.7 Tandayolili Sardis buSt-SardsawveT-Tirkmlis refluqsiQ62.8 SardsawveTis sxva Tandayolili mankebi

SardsawveTis anomalia, romelic sxvagvarad ar aris dazustebuli

Tirkmlis sxva Tandayolili mankebi

ar igulisxmeba: Tandayolili nefrozuli sindromi (N 04.-)Q63.0 damatebiTi TirkmeliQ63.1 wilakebiani, SeerTebuli da nalisebri TirkmeliQ63.2 eqtopiuri Tirkmeli

Tandayolili gadaadgilebuli Tirkmeli

Tirkmlis malrotacia

Q63.3 hiperplaziuri da giganturi TirkmeliQ63.8 Tirkmlis sxva dazustebuli Tandayolili mankebi

Tirkmlis Tandayolili kenWi (konkrementi)

Q63.9 Tirkmlis Tandayolili manki, dauzustebeli

saSarde sistemis sxva Tandayolili mankebi

Q64.0 epispadiaar igulisxmeba: hipospadia (Q 54.-)

Q64.1 Sardis buStis eqstrofiaSardis buStis eqtopia

Sardis buStis eqstroversia

Q64.2 Sardsadenis Tandayolili ukana sarqvlebiQ64.3 Sardsadenisa da Sardis buStis yelis sxva atrezia da stenozi

Tandayolili:

. Sardis buStis yelis obstruqcia

. striqtura

. Sardsadenis

. Sardsadenis gareTa xvrelis

. SardisbuSt-Sardsadenis xvrelis

gauvali Sardsadeni

Q64.4 uraxusis mankiuraxusis kista

Ria uraxusi

uraxusis prolapsi

Q64.5 Sardis buStisa da Sardsadenis Tandayolili ararseboba

} SardsawveTi(s) an SardsawveTis xvreli(s)

Q63

Q64

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551

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Q64.6 Sardis buStis Tandayolili divertikuliQ64.7 Sardis buStisa da Sardsadenis sxva Tandayolili mankebi

damatebiTi: Sardis buSti, Sardsadeni

Tandayolili:. Sardis buStis Tiaqari. Sardis buStisa da Sardsadenis manki, romelic sxvagvarad ar aris dazustebuli. prolapsi:

. Sardis buStis (lorwovani garsis)

. Sardsadenis

. Sardsadenis gareTa xvrelis

. Sardsaden - swori nawlavis fistula

ormagi: Sardsadeni, Sardsadenis gareTa xvreli

Q64.8 saSarde sistemis sxva dazustebuli Tandayolili mankebiQ64.9 saSarde sistemis Tandayolili manki, dauzustebeli

Tandayolili:

. anomalia saSarde sistemis, romelic sxvagvarad

. deformacia ar aris dazustebuli

Zval-kunTovani sistemis Tandayolili mankebi da deformaciebi

(Q65-Q79)menj-barZayis saxsris Tandayolili deformaciebi

ar igulisxmeba: menj-barZayis tkacuna saxsari (R29.4)Q65.0 menj-barZayis saxsris Tandayolili amovardniloba, calmxriviQ65.1 menj-barZayis saxsris Tandayolili amovardniloba, ormxriviQ65.2 menj-barZayis saxsris Tandayolili amovardniloba, dauzustebeliQ65.3 menj-barZayis saxsris Tandayolili qveamovardniloba, calmxriviQ65.4 menj-barZayis saxsris Tandayolili qveamovardniloba, ormxriviQ65.5 menj-barZayis saxsris Tandayolili qveamovardniloba, dauzustebeliQ65.6 aramdgradi menj-barZayis saxsari

menj-barZayis saxsris Cveuli amovardniloba

menj-barZayis saxsris Cveuli qveamovardniloba

Q65.8 menj-barZayis saxsris sxva Tandayolili deformaciebibarZayis Zvlis yelis anteverzia

tabuxis fosos Tandayolili displaziamenj-barZayis saxsris Tandayolili:. amobruneba (Signidan gareT)(valgusuri)

. Cabruneba (garedan SigniT)(varusuli)

Q65.9 menj-barZayis saxsris Tandayolili deformacia, dauzustebeli

terfebis Tandayolili deformaciebi

ar igulisxmeba: terfebis reduqciuli defeqtebi (Q72.-)amobrunebuli deformaciebi (SeZenili)(valgusuri) (M21.0)Cabrunebuli deformaciebi (SeZenili)(varusuli) (M21.1)

Q66.0 terfis eqvinovarusuli deformaciaQ66.1 terfis kalkaneurvarusuli deformaciaQ66.2 Metatarsus varus (varusuli winaterfi)Q66.3 terfebis sxva Tandayolili varusuli deformaciebi

varusuli fexis ceri TiTi, Tandayolili

Q66.4 terfis kalkaneur-valgusuri deformaciaQ66.5 Tandayolili brtyelterfianoba

}

Q65

Q66

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552

avadmyofobaTa saerTaSoriso klasifikacia

brtyeli terfi

. Tandayolili

. rigiduli

. spazmuri (gadmobrunebuli)

Q66.6 terfebis sxva Tandayolili valgusuri deformaciebiM Metatarsus valgus (valgusuri winaterfi)

Q66.7 Pes cavus (Rrma-TaRovani terfi)Q66.8 terfebis sxva Tandayolili deformaciebi

mrude terfi, romelic sxvagvarad ar aris dazustebuli

CaquCisebri TiTi (fexis), Tandayoliliterfis deformacia: romelic sxvagvarad ar aris dazustebuli, asimetriuliukana terfis Zvlebis Serwyma

vertikaluri koWis Zvali

Q66.9 terfebis Tandayolili deformacia, dauzustebeli

Tavis, saxis, xerxemlisa da gulmkerdis Tandayolili Zval-kunTovani deformaciebi

ar igulisxmeba: Tandayolili mankebis sindromebi, romelTa klasifikacia mocemulia Q87.-Sipoteris sindromi (Q60.6)

Q67.0 saxis asimetriaQ67.1 kompresiuli saxeQ67.2 doliqocefaliaQ67.3 plagiocefaliaQ67.4 Tavis qalas, saxisa da ybebis sxva Tandayolili deformaciebi

Tavis qalas CaRrmavebani

cxviris Zgidis gamrudeba, Tandayolilisaxis naxevris atrofia an hiperplaziamiWyletili an mogrexili cxviri, Tandayoliliar igulisxmeba: kbil-saxis anomaliebi [Tankbilvis CaTvliT](K07.-)

aTaSanguri unagira cxviri (A50.5)Q67.5 xerxemlis Tandayolili deformacia

Tandayolili sqoliozi:

. romelic sxvagvarad ar aris dazustebuli

. posturuliar igulisxmeba: bavSvTa odiopaTiuri sqoliozi (M41.0)

sqoliozi, gamowveuli Zvlis Tandayolili mankiT (Q76.3)Q67.6 Pectus excavatum

Tandayolili mewaRis gulmkerdi

Q67.7 Pectus carinatumTandayolili qaTmis gulmkerdi

Q67.8 gulmkerdis sxva Tandayolili deformaciebigulmkerdis kedlis Tandayolili deformacia, romelic sxvagvarad ar aris dazustebuli

sxva Tandayolili Zval-kunTovani deformaciebi

ar igulisxmeba: kidur(eb)is reduqciuli defeqtebi (Q71-Q73)Q68.0 mkerd-laviw-dvrilisebri kunTis Tandayolili deformacia

Tandayolili (mkerd-dvrilovani) kisermrudoba

mkerd-laviw-dvrilisebri (kunTis) kontraqtura

mkerd-dvrilovani simsivne (Tandayolili)

Q68.1 mtevnis Tandayolili deformaciaTandayolili TiTmrudoba

niCbisebri xeli (Tandayolili)

Q68.2 muxlis Tandayolili deformacia

Q67

Q68

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553

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Tandayolili: molaylaye muxli, rekurvaciuli muxli

Q68.3 barZayis Zvlis Tandayolili deformaciaar igulisxmeba: barZayis Zvlis (yelis) anteversia (Q65.8)

Q68.4 didi wvivis Zvlisa da mcire wvivis Zvlis Tandayolili deformaciaQ68.5 fexis grZeli Zvlebis Tandayolili deformacia, dauzustebeliQ68.8 sxva dazustebuli Tandayolili Zval-kunTovani deformaciebi

Tandayolili:

. deformacia: laviwis, idayvis, winamxris, beWis

. gadaadgileba: idayvis, mxris sartylis

polidaqtilia

Q69.0 damatebiTi TiT(eb)i (xelis)Q69.1 damatebiTi cer(eb)i (xelis)Q69.2 damatebiTi TiT(eb)i (fexis)

damatebiTi ceri (fexis)

Q69.9 polidaqtilia, dauzustebelimravali TiT(eb)i, romelic sxvagvarad ar aris dazustebuli

sindaqtilia

Q70.0 Sexorcebuli TiTebi (xelis)TiTebis kompleqsuri sindaqtilia sinostozTan erTad

Q70.1 apkiani TiTebi (xelis)TiTebis martivi sindaqtilia sinostozis gareSe

Q70.2 Sexorcebuli TiTebi (fexis)fexis TiTebis kompleqsuri sindaqtilia sinostozTan erTad

Q70.3 apkiani TiTebi (fexis)fexis TiTebis martivi sindaqtilia sinostozis gareSe

Q70.4 polisindaqtiliaQ70.9 sindaqtilia, dauzustebeli

simfalangia, romelic sxvagvarad ar aris dazustebuli

zeda kiduris reduqciuli defeqtebi

Q71.0 zeda kidur(eb)is Tandayolili sruli ararsebobaQ71.1 mxrisa da winamxris Tandayolili ararseboba mtevnis arsebobasTan erTadQ71.2 orive, winamxrisa da mtevnis Tandayolili ararsebobaQ71.3 xelis mtevnisa da TiT(eb)is Tandayolili ararsebobaQ71.4 sxivis Zvlis sigrZivi reduqciuli defeqti

mrude xeli (Tandayolili)

sxivisZvlismieri mrude xeli

Q71.5 idayvis Zvlis sigrZivi reduqciuli defeqtiQ71.6 kiborCxalis-marwuxisebri xeliQ71.8 zeda kidur(eb)is sxva reduqciuli defeqtebi

Tandayolili mokle zeda kidur(eb)i

Q71.9 zeda kiduris reduqciuli defeqti, dauzustebeli

qveda kiduris reduqciuli defeqtebi

Q72.0 qveda kidur(eb)is Tandayolili sruli ararsebobaQ72.1 barZayisa da kanWis Tandayolili ararseboba terfis arsebobasTan erTadQ72.2 orive kanWisa da terfis Tandayolili ararseboba

Q72

Q69

Q70

Q71

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554

avadmyofobaTa saerTaSoriso klasifikacia

Q72.3 terfisa da fexis TiT(eb)is Tandayolili ararsebobaQ72.4 barZayis Zvlis sigrZivi reduqciuli defeqti

barZayis Zvlis proqsimaluri adgilobrivi defeqti

Q72.5 didi wvivis Zvlis sigrZivi reduqciuli defeqtiQ72.6 mcire wvivis Zvlis sigrZivi ruduqciuli defeqtiQ72.7 gaxleCili terfiQ72.8 qveda kidur(eb)is sxva reduqciuli defeqtebi

Tandayolili mokle qveda kidur(eb)i

Q72.9 qveda kiduris reduqciuli defeqti, dauzustebeli

dauzustebeli kiduris reduqciuli defeqtebi

Q73.0 dauzustebeli kidur(eb)is Tandayolili ararsebobaamelia, romelic sxvagvarad ar aris dazustebuli

Q73.1 fokomelia, dauzustebeli, kidur(eb)isfokomelia, romelic sxvagvarad ar aris dazustebuli

Q73.8 dauzustebeli kidur(eb)is sxva reduqciuli defeqtebidauzustebeli kidur(eb)is sigrZivi reduqciuli deformacia

eqtromelia, romelic sxvagvaradar aris dazustebuli kidurebis, romelichemimelia, romelic sxvagvarad sxvagvarad ar arisar aris dazustebuli dazustebuli

reduqciuli defeqti

kidur(eb)is sxva Tandayolili mankebi

ar igulisxmeba: polidaqtilia (Q69.-); kiduris reduqciuli defeqti (Q71-Q73)sindaqtilia (Q70.-)

Q74.0 zeda kidur(eb)is sxva Tandayolili mankebi, mxris sartylis CaTvliTmajis damatebiTi Zvlebi

laviw-qalas dizostozilaviwis Tandayolili fsevdoarTrozimakrodaqtilia (xelis TiTebis)madelungis deformaciasxiv-idayvis sinostoziSprengelis deformacia

samfalangiani ceri (xelis)

Q74.1 muxlis Tandayolili mankiTandayolili: kviristavis ararseboba; kviristavis amovardniloba

muxli: amobrunebuli, Cabrunebulirudimentuli kviristaviar igulisxmeba: Tandayolili: muxlis amovardniloba (Q68.2); rekurvaciuli muxli (Q68.2);

arTrosteonoqo displazia

frCxilis kviristavis sindromi (Q87.2)Q74.2 qveda kidur(eb)is sxva Tandayolili mankebi, menjis CaTvliT

Tandayolili: gava-TeZos saxsris Sexorceba, manki, koW-wvivis (saxsris), gava-TeZos (saxsris)

ar igulisxmeba: barZayis Zvlis (yelis) anteversia (Q65.8)Q74.3 Tandayolili mravlobiTi arTrogripoziQ74.8 kidur(eb)is sxva dazustebuli Tandayolili mankebiQ74.9 kidur(eb)is dauzustebeli Tandayolili manki

kidur(eb)is Tandayolili anomalia, romelic sxvagvarad ar aris dazustebuli

Tavis qalasa da saxis Zvlebis sxva Tandayolili mankebi

ar igulisxmeba: saxis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli (Q18.-)

Q74

Q73

}

Q75

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555

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

Tandayolili mankebis sindromebi, romelTa klasifikacia mocemulia Q87-Sikbil-saxis anomaliebi [Tankbilvis CaTvliT] (K07.-)Tavisa da saxis Zval-kunTovani deformaciebi (Q67.0--Q67.4)Tavis qalas defeqtebi, dakavSirebuli Tavis tvinis iseT Tandayolili

anomaliebTan, rogoricaa: anencefalia (Q00.0); encefalocele (Q01.-);hidrocefalia (Q03.-); mikrocefalia (Q02)

Q75.0 kraniosinostoziakrocefalia

Tavis qalas gauvali Sexorcebaoqsicefalia

trigonocefalia

Q75.1 qala-saxis dizostozikruzonis avadmyofoba

Q75.2 hipertelorizmiQ75.3 makrocefaliaQ75.4 qveda-yba-saxis dizostoziQ75.5 Tval-qveda-ybis dizostoziQ75.8 Tavis qalasa da saxis Zvlebis sxva dazustebuli Tandayolili

mankebi

Tavis qalas Zvlis ararseboba, TandayoliliSublis Tandayolili deformacia

platibazia

Q75.9 Tavis qalasa da saxis Zvlebis Tandayolili manki, dauzustebeliTandayolili anomalia:

. saxis Zvlebis, romelic sxvagvarad ar aris dazustebuli

. Tavis qalas, romelic sxvagvarad ar aris dazustebuli

xerxemlisa da gulmkerdis Tandayolili mankebi

ar igulisxmeba: xerxemlisa da gulmkerdis Tandayolili Zval-kunTovani deformaciebi

(Q67.5-Q67.8)Q76.0 faruli Spina bifida

ar igulisxmeba: meningocele (spinuri)(Q05.-)spina bifida (Ria)(kisturi)(Q05.-)

Q76.1 klipel-feilis sindromikisris Sexorcebis sindromi

Q76.2 Tandayolili spondilolisToziTandayolili spondilolizi

ar igulisxmeba: spondilolisTozi (SeZenili)(M43.1); spondilolizi (SeZenili) (M43.0)Q76.3 Tandayolili sqoliozi, gamowveuli Zvlis Tandayolili mankiT

hemivertebruli Sexorceba anu segmentaciis darRveva sqolioziT

Q76.4 xerxemlis sxva Tandayolili mankebi, romlebic ar aris dakavSirebuli sqoliozTanTandayolili:

. malis ararseboba

. malebis Serwyma

. kifozi

. lordozi

. gava-welis (saxsris)(midamos) manki dauzustebeli an sqoliozTan kavSiris gareSenaxevarmalaxerxemlis mankiplatispondilozi

malebis simravle

Q76

}

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556

avadmyofobaTa saerTaSoriso klasifikacia

Q76.5 kisris neknineknebis simravle kisris midamoSi

Q76.6 neknebis sxva Tandayolili mankebidamatebiTi nekni

Tandayolili:. neknis ararseboba. neknebis Sexorceba. neknebis mankebi, romlebic sxvagvarad ar aris dazustebuli

ar igulisxmeba: mokle neknis sindromi (Q77.2)Q76.7 mkerdis Zvlis Tandayolili manki

mkerdis Zvlis Tandayolili ararseboba

mkerdis Zvlis naprali (sternum bifidum)Q76.8 gulmkerdis yafazis sxva Tandayolili mankebiQ76.9 gulmkerdis yafazis Tandayolili manki, dauzustebeli

osteoqondrodisplazia lulovani Zvlebisa da xerxemlis zrdis defeqtebiT

ar igulisxmeba: mukopolisaqaridozi (E76.0-E76.3)Q77.0 aqondrogenezi

hipoqondrogenezi

Q77.1 Tanatotropuli dabali aRnagobaQ77.2 mokle neknis sindromi

asfiqsiis gamomwvevi gulmkerdis displazia [junis]

Q77.3 wertilovani qondrodisplaziaQ77.4 aqondroplazia

hipoqondroplazia

Q77.5 distrofiuli displaziaQ77.6 qondroeqtodermuli displazia

elis-van kreveldis sindromi

Q77.7 spondiloepifizuri displaziaQ77.8 sxva osteoqondrodisplazia lulovani Zvlebisa da xerxemlis zrdis defeqtebiTQ77.9 osteoqondrodisplazia lulovani Zvlebisa da xerxemlis zrdis

defeqtebiT, dauzustebeli

sxva osteoqondrodisplazia

Q78.0 arasruli osteogenezimsxvrevadi Zvlebi (Fragilitas ossium)osteopsaTirozi

Q78.1 Zvlebis mravlobiTi dazianebiT mimdinare fibrozuli displaziaolbrait (-mak-kiun)(Sternberg)is sindromi

Q78.2 osteopetrozialbers-Sonabergis sindromi

Q78.3 progresuli diafizuri displaziakamurati-engelmanis sindromi

Q78.4 enqodromatozimafuCis sindromi

olies avadmyofoba

Q78.5 metafizuri displaziapailis sindromi

Q78.6 mravlobiTi Tandayolili egzostozebi

Q77

Q78

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557

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

diafizuri aklazia

Q78.8 sxva dazustebuli osteoqondrodisplaziaosteopoikilozi

Q78.9 osteoqondrodisplazia, dauzustebeliqondrodistrofia, romelic sxvagvarad ar aris dazustebuli

osteodistrofia, romelic sxvagvarad ar aris dazustebuli

Zval-kunTovani sistemis Tandayolili mankebi, romlebic ar aris Setanili

sxva klasifikaciebSi

ar igulisxmeba: Tandayolili (mkerd-dvrilovani) kisermrudoba (Q68.0)Q79.0 Tandayolili diafragmuli Tiaqari

ar igulisxmeba: Tandayolili Tiaqris xvreli (Q40.1)Q79.1 diafragmis sxva Tandayolili mankebi

diafragmis ararseboba

diafragmis Tandayolili manki, romelic sxvagvarad ar aris dazustebuli

diafragmis eventracia (relaqsacia)

Q79.2 egzomfalosiomfalocele

ar igulisxmeba: Wipis Tiaqari (K 42.-)Q79.3 gastroSiziQ79.4 “Camovardnili muclis” sindromiQ79.5 muclis kedlis sxva Tandayolili mankebi

ar igulisxmeba: Wipis Tiaqari (K 42.-)Q79.6 elers-danlosis sindromiQ79.8 Zval-kunTovani sistemis sxva Tandayolili mankebi

ararseboba: kunTis, myesis

damatebiTi kunTiTandayolili amiotrofiaTandayolili: momWeri Wimebi, myesis damokleba

polandis sindromi

Q79.9 Zval-kunTovani sistemis Tandayolili manki, dauzustebeliTandayolili:

. anomalia, romelic sxvagvarad ar aris dazustebuli

. deformacia, romelic sxvagvarad ar aris dazustebuli

. Zval-kunTovani sistemis, romelic sxvagvarad ar aris dazustebuli

sxva Tandayolili mankebi

(Q80-Q89)Tandayolili iqTiozi

ar igulisxmeba: refsumis avadmyofoba (G60.1)Q80.0 vulgaruli iqTioziQ80.1 X-SeWiduli iqTioziQ80.2 qerclisebri iqTiozi

koloiduri bavSvi

Q80.3 Tandayolili buStukovani iqTioziformuli eriTrodermaQ80.4 “masxarasebri nayofi”Q80.8 sxva Tandayolili iqTioziQ80.9 Tandayolili iqTiozi, dauzustebeli

Q79

Q80

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558

avadmyofobaTa saerTaSoriso klasifikacia

buStukovani epidermolizi

Q81.0 martivi buStukovani epidermoliziar igulisxmeba: kokeinis sindromi (Q87.1)

Q81.1 letaluri buStukovani epidermoliziherlicis sindromi

Q81.2 distrofiuli buStukovani epidermoliziQ81.8 sxva buStukovani epidermoliziQ81.9 buStukovani epidermolizi, dauzustebeli

kanis sxva Tandayolili mankebi

ar igulisxmeba: enteropaTiuli akrodermatiti (E83.2)Tandayolili eriTropoezuri porfiria (E80.0)poloniduri kista anu wiaRi (L05.-)sterj-veber-dimitris sindromi (Q85.8)

Q82.0 memkvidruli limfedemaQ82.1 pigmenturi qserodermaQ82.2 mastocitozi

pigmenturi urtikaria

ar igulisxmeba: avTvisebiani mastocitozi (C96.2)Q82.3 pigmentis SeukaveblobaQ82.4 eqtodermuli displazia (anpidrozuli)

ar igulisxmeba: elis-van kreveldis sindromi (Q77.6)Q82.5 Tandayolili ara-simsivnuri xali

xali, romelic sxvagvarad ar aris dazustebuli

xali:. alisferi. portveinisferi. sisxlsavse. marwyvisebri. sisxlZarRvovani, romelic sxvagvarad ar aris dazustebuli. meWeWovaniar igulisxmeba: rZiani yavisebri laqebi (L81.3)

. lentigo (L81.4)xali:. romelic sxvagvarad ar aris dazustebuli (D22.-). araneus (I78.1). melanocituri (D22.-). pigmenturi (D22.-). obobasebri (I78.1). varskvlavisebri (I78.1)

Q82.8 kanis sxva dazustebuli Tandayolili mankebixelisgulis paTologiuri nakecebi

kanis damatebiTi wanazardebikeTilTvisebiani ojaxuri pemfigusi [heili-heilis]dune kani (hiperelastikuri)dermatoglifiuri anomaliebixelisgulisa da fexisgulis memkvidruli keratozi

folikuluri keratozi [darie-vaitis]

ar igulisxmeba: elers-danlosis sindromi (Q79.6)Q82.9 kanis Tandayolili manki, dauzustebeli

Q81

Q82

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559

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

sarZeve jirkvlis Tandayolili mankebi

ar igulisxmeba: mkerdis kunTis ararseboba (Q79.8)Q83.0 sarZeve jirkvlis Tandayolili ararseboba dvrilis ararsebobasTan erTadQ83.1 damatebiTi sarZeve jirkvlebi

mravlobiTi sarZeve jirkvlebi

Q83.2 dvrilis ararsebobaQ83.3 damatebiTi dvrili

mravlobiTi dvrilebi

Q83.8 sarZeve jirkvlis sxva Tandayolili mankebisarZeve jirkvlis hipoplazia

Q83.9 sarZeve jirkvlis Tandayolili manki, dauzustebeli

sxeulis safarvelis sxva Tandayolili mankebi

Q84.0 Tandayolili gamelotebaTandayolili etriqozi (uTmoba)

Q84.1 Tmis Tandayolili morfologiuri dazianebebi, romelic ar aris Setanilisxva klasifikaciebSimZivisebri Tma

monileTriqsi (funjisebri Tma)rgolisebri Tma

ar igulisxmeba: menkesis xveuli Tmis sindromi (E83.0)Q84.2 Tmis sxva Tandayolili mankebi

Tandayolili: hipertriqozi, Tmis manki, romelic sxvagvarad ar aris dazustebuli

darCenili lanugo (RinRli, pirveladi)

Q84.3 anoniqiaar igulisxmeba: frCxil-kviristavis sindromi (Q87.2)

Q84.4 Tandayolili leikoniqiaQ84.5 gafarToebuli da hipertrofiuli frCxilebi

Tandayolili onixauqsisi

paqionixia

Q84.6 frCxilebis sxva Tandayolili mankebiTandayolili: mrude frCxili, koilonixia, frCxilis manki, romelic sxvagvarad ar aris dazustebuli

Q84.8 sxeulis safarvelis sxva dazustebuli Tandayolili mankebikanis Tandayolili aplazia

Q84.9 sxeulis safarvelis Tandayolili manki, dauzustebeliTandayolili:

. anomalia, romelic sxvagvarad ar aris dazustebuli sxeulis safarvelis, romelic

. deformacia, romelic sxvagvarad ar aris dazustebuli sxvagvarad ar aris dazustebuli

fakomatozebi, romlebic ar aris Setanili sxva klasifikaciebSi

ar igulisxmeba: ataqsia telangieqtazia [luis-baris] (G11.3)ojaxuri disavtonomia [rilei-deis] (G90.1)

Q85.0 neirofibromatozi (araavTvisebiani)von reklinghauzenis avadmyofoba

Q85.1 tuberozuli skleroziburnevilis avadmyofoba

epiloia

Q85.8 sxva fakomatozebi, romlebic ar aris Satanili sxva klasifikaciebSisindromi: paic-egersis, sterj-veber (-dimitri)-is, von hipel-lindaus

ar igulisxmeba: mekel-gruberis sindromi (Q61.9)

Q83

Q84

}

Q85

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560

avadmyofobaTa saerTaSoriso klasifikacia

Q85.9 fakomatozi, araspecifikurifakomatozi, romelic sxvagvarad ar aris dazustebuli

Tandayolili mankebis sindromebi, gamowveuli cnobili egzogenuri

mizezebiT, romlebic ar aris Setanili sxva klasifikaciebSi

ar igulisxmeba: iodis-deficitTan-dakavSirebuli hipoTiroidizmi (E00-E02)placentiTa da dedis rZiT gadasuli nivTierebebis arateratogenuli efeqtebi (P04.-)

Q86.0 nayofis alkoholuri sindromi (dismorfuli)Q86.1 nayofis hidantoinuri sindromi

midous sindromi

Q86.2 dismorfizmi, gamowveuli varfariniTQ86.8 sxva Tandayolili mankebis sindromebi, gamowveuli cnobili egzogenuri mizezebiT

sxva dazustebuli Tandayolili mankebis sindromebi mravlobiTi sistemebis

dazianebiT

Q87.0 Tandayolili mankebis sindromebi upiratesad saxis ieris dazianebiTakrocefalopolisindaqtiliaakrocefalosindaqtilia [apertis]kriptofTalmuri sindromiciklopiasindromi: goldenharis, mebius, pir-saxe-TiTebis, robinis, triCer kolinzis

mstvenavi saxe

Q87.1 Tandayolili mankebis sindromebi upiratesad dakavSirebuli dabal aRnagobasTansindromi:

. aarskogis

. kokeinis

. de lanJes

. dubovicis

. nunanis

. prader-vilis

. robinov-silvermen-smitis

. rasel-silveris

. sekelis

. smit-lemli-opicis

ar igulisxmeba: elis-van kreveldis sindromi (Q77.6)Q87.2 Tandayolili mankebis sindromebi upiratesad kidurebis dazianebiT

sindromi:

. holt-oramis

. klipel-trenone-veberis

. frCxilisebri kviristavis

. rubinStain-teibis

. sirenomeliuri

. Trombocitopeniuri sxivis Zvlis ararsebobiT [TAR]

. VATERQ87.3 ganviTarebis Tandayolili mankebis sindromebi, romlebic Seexeba adreul

Warb zrdassindromi: bekviT-videmanis, zotos, viaveris

Q87.4 marfanis sindromiQ87.5 ganviTarebis Tandayolili mankebis sxva sindromebi ConCxis sxva cvlilebebiTQ87.8 sxva dazustebuli ganviTarebis Tandayolili mankebis sindromebi,

romlebic ar aris Setanili sxva klasifikaciebSisindromi: alportis, laurens - mune (-barde)-bidlis, zelvegeris

Q86

Q87

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561

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

sxva Tandayolili mankebi, romlebic ar aris Setanili sxva klasifikaciebSi

Q89.0 elenTis ganviTarebis Tandayolili mankebiasplenia (Tandayolili)

Tandayolili splenomegalia

ar igulisxmeba: winagulis yurebis izomurizmi (aspleniiT an polispleniiT) (Q 20.6)Q89.1 Tirkmelzeda jirkvlis ganviTarebis Tandayolili mankebi

ar igulisxmeba: Tirkmelzeda jirkvlis Tandayolili hiperplazia (E25.0)Q89.2 sxva endokrinuli jirkvlebis ganviTarebis Tandayolili mankebi

farisebraxlo an farisebri jirkvlis ganviTarebis Tandayolili mankebi

persistuli farisebr-enis sadinari

farisebr-enis kista

Q89.3 Situs inversus (gaukuRmarTebuli ganlageba)deqstrokardia Situs inversus-Tan erTad

winagulis sarkisebri (anareklisebri) ganlageba Situs inversus-Tan erTadgaukuRmarTebuli an ganivi ganlageba: muclis Rrusa da gulmkerdis Rrus organoebisSinagan organoTa transpozicia: gulis Rrus, gulmkerdis

ar igulisxmeba: deqstrokardia, romelic sxvagvarad ar aris dazustebuli (Q 24.0)Q89.4 Sezrdili tyupebi

kraniopagusidicefaliaormagi monstrifigofagusi

Torakopagusi

Q89.7 ganviTarebis mravlobiTi Tandayolili mankebi, romlebic ar arisSetanili sxva klasifikaciebSimonstri, romelic sxvagvarad ar aris dazustebuli

mravlobiTi Tandayolili:. anomaliebi, romelic sxvagvarad ar aris dazustebuli. deformaciebi, romelic sxvagvarad ar aris dazustebuliar igulisxmeba: ganviTarebis Tandayolili mankebis sindromebi, mravlobiTi sistemebis

dazianebiT (Q 87.-)Q89.8 sxva dazustebuli ganviTarebis Tandayolili mankebiQ89.9 ganviTarebis Tandayolili mankebi, dauzustebeli

Tandayolili

. anomalia, romelic sxvagvarad ar aris dazustebuli

. deformacia, romelic sxvagvarad ar aris dazustebuli

qromosomuli darRvevebi, romlebic ar aris Setanili sxva klasifikaciebSi

(Q90 - Q99)daunis sindromi

Q90.0 trosomia 21, meiozuri gauTiSvelobaQ90.1 trisomia 21, mozaicizmi (mitozuri gauTiSveloba)Q90.2 trisomia 21, translokaciaQ90.9 daunis sindromi, dauzustebeli

trisomia 21, romelic sxvagvarad ar aris dazustebuli

edvardsis sindromi da pataus sindromi

Q91.0 trisomia 18, meiozuri gauTiSvelobaQ91.1 trisomia 18, mozaicizmi (mitozuri gauTiSveloba)

Q89

Q90

Q91

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562

avadmyofobaTa saerTaSoriso klasifikacia

Q91.2 trisomia 18, translokaciaQ91.3 edvardsis sindromi, dauzustebeliQ91.4 trisomia 13, meiozuri gauTiSvelobaQ91.5 trisomia 13, mozaicizmi (mitozuri gauTiSveloba)Q91.6 trisomia 13, translokaciaQ91.7 pataus sindromi, dauzustebeli

autosomebis nawilobrivi trisomiebi da sxva trisomiebi, romlebic ar

aris Setanili sxva klasifikaciebSi

igulisxmeba: arabalansirebuli translokaciebi da inserciebi

ar igulisxmeba: 13, 18, 21 qromosomebis trisomiebi (Q 90 - Q 91)Q92.0 mTliani qromosomis trisomia, meiozuri gauTiSvelobaQ92.1 mTliani qromosomis trisomia, mozaicizmi (mitozuri gauTiSveloba)Q92.2 didi nawilobrivi trisomia

mTliani mxari an metia gaormagebuli

Q92.3 mcire nawilobrivi trisomiamTlian mxarze naklebia gaormagebuli

Q92.4 gaormageba, romelic mxolod prometafazaSi CansQ92.5 gaormageba, danarCeni kompleqsuri cvlilebebiTQ92.6 eqstra markeruli qromosomebiQ92.7 triploidia da poliploidiaQ92.8 sxva dauzustebeli trosomiebi da autosomebis nawilobrivi trisomiebiQ92.9 autosomebis trisomia da nawilobrivi trisomia, dauzustebeli

autosomebis monosomiebi da deleciebi, romlebic ar aris Setanili

sxva klasifikaciebSi

Q93.0 mTliani qromosomis monosomia, meiozuri gauTiSvelobaQ93.1 mTliani qromosomis monosomia, mozaicizmi (mitozuri gauTiSveloba)Q93.2 qromosoma, gardaqmnil rgolad an dicentruladQ93.3 4 qromosomis mokle mxris delecia

volf - hirSxornis sindromi

Q93.4 5 qromosomis mokle mxris deleciakatis knavilis (Cri-du-chat) sindromi

Q93.5 qromosomis Semadgeneli nawilebis sxva deleciebiQ93.6 deleciebi, romelic mxolod prometafazaSi CansQ93.7 deleciebi sxva kompleqsuri gardaqmnebiTQ93.8 autosomebis sxva deleciebiQ93.9 autosomebis delecia, dauzustebeli

balansirebuli gardaqmnebi da struqturuli markerebi, romelic ar aris

Setanili sxva klasifikaciebSi

igulisxmeba: robertsonis da balansirebuli reciprokuli translokaciebi da inserciebi

Q95.0 balansirebuli translokacia da insercia normul individSiQ95.1 qromosomis inversia normul individSiQ95.2 balansirebuli autosomuri gardaqmnebi aranormalur individSiQ95.3 balansirebuli sasqeso/autosomuri gardaqmnebi aranormalur individSiQ95.4 individebi markeruli heteroqromatiniTQ95.5 individebi autosomis msxvrevadi ubnebiTQ95.8 sxva balansirebuli gardaqmnebi da struqturuli markerebiQ95.9 balansirebuli gardaqmna da struqturuli markeri, dauzustebeli

Q92

Q95

Q93

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563

Tandayolili mankebi, deformaciebi da qromosomuli darRvevebi

terneris sindromi

ar igulisxmeba: nunenis sindromi (Q 87.1)Q96.0 kariotipi 45,XQ96.1 kariotipi 46,X iso (Xq)Q96.2 kariotipi 46,X aranormuli sasqeso qromosomiT, garda iso (Xq)Q96.3 mozaicizmi, 45,X/46, XX an XYQ96.4 mozaicizmi, 45,X/ sxva ujreduli xazi (ebi) aranormuli sasqeso qromosomiTQ96.8 terneris sindromis sxva variantebiQ96.9 terneris sindromi, dauzustebeli

sasqeso qromosomebis sxva darRvevebi, qalis fenotipi, romelic ar

aris Setanili sxva klasifikaciebSi

ar igulisxmeba: terneris sindromi (Q 96.-)Q97.0 kariotipi 47, XXXQ97.1 qali samze meti X qromosomiTQ97.2 mozaicizmi, xazebi X qromosomebis sxvadasxva raodenobiTQ97.3 qali 46, XY kariotipiTQ97.8 sasqeso qromosomebis sxva dazustebuli anomaliebi, qalis fenotipiQ97.9 sasqeso qromosomis anomalia, qalis fenotipi, dauzustebeli

sasqeso qromosomebis sxva darRvevebi, mamakacis fenotipi, romelic ar

aris Setanili sxva klasifikaciebSi

Q98.0 klainefelteris sindromi, kariotipi 47,XXYQ98.1 klainefelteris sindromi, mamakaci orze meti X qromosomiTQ98.2 klainefelteris sindromi, mamakaci 46,XX kariotipiTQ98.3 sxva tipis mamakaci, 46,XX kariotipiTQ98.4 klainefelteris sindromi, dauzustebeliQ98.5 kariotipi 47,XYYQ98.6 mamakaci struqturulad aranormuli sasqeso qromosomiTQ98.7 mamakaci sasqeso qromosomis mozaicizmiTQ98.8 sasqeso qromosomebis sxva dazustebuli anomaliebi, mamakacis fenotipiQ98.9 sasqeso qromosomis anomalia, mamakacis fenotipi, dauzustebeli

sxva qromosomuli darRvevebi, romlebic ar aris Setanili sxva

klasifikaciebSi

Q99.0 qimera 46,XX/46,XYqimera 46,XX/46,XY WeSmariti hermafroditi

Q99.1 46, XX WeSmariti hermafroditi46, XX zonriseburi gonadebiT46, XY zonriseburi gonadebiTsufTa gonadebis disgenezia

Q99.2 fragiluri X qromosomafragiluri X qromosomis sindromi

Q99.8 sxva dazustebuli qromosomuli darRvevebiQ99.9 qromosomuli darRveva, dauzustebeli

Q97

Q98

Q96

Q99