curs malformatiile laringelui
DESCRIPTION
Curs orl marie curieTRANSCRIPT
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Malformaiile faringelui
Dan Cristian Gheorghe
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Insuficienta velo-palatina
Congenitala Secundara (dobandita)
Tratament: UPPP logopedie
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Palatoschizis
Izolat In cadrul unor sindroame congenitale Pierre-Robin
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Maladia Crouzon
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Tiroida ectopic
Defect de coborre a glandei tiroide n viaa fetal
Incidena: Raport pe sexe: 3-4/1 (femei) 1:4000 1:8000
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Localizri
Baza limbii Submandibular Laringian Traheal Mediastinal Esofagian Mediastinal Intracardiac
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Clinic
Asimptomatic Senzaie de corp strin Dispnee Disfonie Hemoragii severe(1)
1. Chiu, T. T., et al. (2002). "Massive bleeding from an ectopic lingual thyroid follicular adenoma during pregnancy." Am J Otolaryngol 23(3): 185-188.
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Explorri
Dozare hormoni tiroidieni: T3, T4, fraciile libere de T3 i T4, TSH
Ecografia regiunii cervicale Scintigrafia cu Tc-99m CT, RMN (n indicaii chirurgicale) Biopsia aspirativ cu ac fin (+/- ecografie)?
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Tratament
Monitorizare pacient asimptomatic Exerez chirurgical:
Hemoragii severe Tulburari de respiraie/deglutiie Malignizare
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Evoluie
Risc malignizare crescut (discuii)?(1,2)
1. Cherif, L., et al. (2004). "[Ectopic thyroid: two cases]." Ann Endocrinol (Paris) 65(3): 233-237. 2. Klubo-Gwiezdzinska, J., et al. (2011). "Clinical review: Ectopic cervical thyroid carcinoma--review of the
literature with illustrative case series." J Clin Endocrinol Metab 96(9): 2684-2691.
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Chistele latero-cervicale (branhiale)
Pe marginea anterioara a scm
Tratament: chirurgical
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Chistul de tract tireoglos
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Fistula de tract tireoglos