cemento ossifyng fibroma of the ethmoidal cells
DESCRIPTION
CEMENTO OSSIFYNG FIBROMA OF THE ETHMOIDAL CELLS, diagnosis, treatmentTRANSCRIPT
CEMENTO OSSIFYNG FIBROMA OF THE
ETHMOIDAL CELLSA CASE REPORT
Department of Otorhinolaryngology and Head & Neck Surgery Sestre milosrdnice hospital Zagreb
D.Shejbal, Baudoin T, Geber G, Drviš P, Stevanović S
CEMENTIFYNG FIBROMAS
• Rare benign tumors which arise from the peridontal membrane
• Multipotent cells: fibrous tissue, cementum, lammelar bones ( psammous desmo osteoblastomas)
1. Mandibula
2. Maxilla
3. Very rare in
PNS
DEVELOPMENTthree distinct stage
• I. osteolytic: cellular tissue only/ no calcified deposite
• II. Cementoblastic stage: becomes calcified and radiopaque
• III. Mature inactive stage: calcified and encapsulated ( 3,8 cm)
• Immature
• Aggressive manner
• destructive
• recidivism
PROBLEMS
• Ethmoidal location
Incoplete migration and differentiaition into peridontal membrane
( mesodermal origin)
-female, 9 years
-family history: normal, -personal history: allergy
to dermatophagoydes, pollenosis
Labaratory data, chest x ray: nornal
TWO MONTHS AGOPain in forehead, right eye,
diminished vision
ANT. RHYNOSCOPYHiperemy mucous membrane, Globe form. in middle meatus
like a conha bullosa
NMR
mucocoellae of anterior et
posterior ethmoid cells destruction lamina orbitalis
• Cemento ossifyng fybroma in the ethmoidal cells are very rare ( up to 10 cases)
• psammous desmo osteoblastomas
• Probably, this is a SECOND CASE which is a cystic lesion has performed
• Suggested craniofacial ressection/ parents refused• Micro endoscopic tumor ressection/ other hospital• Dacrocystorhinostomy• Transnasal endoscopic adenotomy• No signs of rhinoliqurrhea• Small residual tumor in the area of lamina
papyracea and no signs of dural lesion