artropatia hemofilica

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pediatrie

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CoagulopatiiHemofiliaAGenetic:--boalgonozomal recesiv-FVIIIC -Xq 28- femeile prttoare- brba!ii bolnaviF VIII C valoare normal " #$ %#$& Formeclinice :

'ever: F VIII C sb % &(e)ie: % # &*+oar: # 2# &CoagulopatiiHemofiliaAClinic:- ,emartroz- ,ematoamemsclare -ctanate - .pista/is - Gingivoragii - ,ematrie - (sclare : psoas - 0one pericloase: orbitar1 faringe1 etc2 - '3C 4Cele mai frecvente s5ngerri articlare : la nivell gennc6ilor1 coatelor1 gleznei +i mai rar 7n articla!ia +ol)li1 mrli sa pmnli2 4'5ngerrile msclare : iliopsoas1 gastrocnemian1 fle/ori ai antebra!li 4Instalarea artropatiei 6emofilice " trei sta)ii: 8%9 6emartroz act: 829 sinovit cronic: 8;9 artrit )egenerativ2,aemop6ilia,aemop6ilia,aemop6ilia,aemop6iliaCoagulopatiiHemofiliaAecombinate1?ogenate

CoagulopatiiHemofiliaA

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