{ carpal fusion jalal jalal shokouhi-md, isr kimia kahrizi-md, prof. of medical genetics mohammad...

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{ Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar Pashaei-PhD, Boniad daneshname negari, Iran Aliakbar Ameri-MD, Jaam e jam [email protected] www.medimage.ir

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Page 1: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

{

Carpal fusion

Jalal Jalal Shokouhi-MD, ISRKimia Kahrizi-MD, Prof. of medical geneticsMohammad hossein Herischi-MD,PhD-Baku, Republic AzerbaijanShahyar Pashaei-PhD, Boniad daneshname negari, IranAliakbar Ameri-MD, Jaam e jam

j a l a l j a l a l s h o k o uh i@ho tma i l . c om

www.medimage. i r

Page 2: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar
Page 3: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

1. Hereditary2. Non-hereditary

Causes:

Page 4: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

Carpal fusion is hereditary and nonhereditary conditions in acrocallosal syndrome, acromegaly, apert, arthrograyposis, carpenter syndrome, chromosal abnormalities, EEC syndrome, F syndrome, fetal alcohol syndrome, holt oram S. leopard S., multiple synostosis S., oligosyndactyly S., Pfeiffer-likes, scleroderma, split hand and foot, stickler S., thalidomide embryopathy, turner syndrome and many other conditions (taybi syndrome book).Sometimes there is no known causative disease

Page 5: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

Technic = X-ray

Page 6: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

Hand bone anomalies are more common in syndromes or other congenital or non-hereditary conditions but polydactyly, syndactyly or oligodactyly and carpal fusions are interesting.X-ray is the modality of choice but MRI and X-ray CT with multiplanar reconstructions can be use for diagnosis.

Page 7: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

Short second phalanx of fifth finger

Page 8: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

Short second phalanx of fifth fingerRight hand with three metacarpal and phalanx, fused carpal bones

Page 9: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

Fused right carpal bones capitate and hamate

Page 10: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar

Gallery

Page 11: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar
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Page 13: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar
Page 14: { Carpal fusion Jalal Jalal Shokouhi-MD, ISR Kimia Kahrizi-MD, Prof. of medical genetics Mohammad hossein Herischi-MD,PhD-Baku, Republic Azerbaijan Shahyar
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THANK YOU FOR YOUR ATTENTION