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10/23/2018 1 persistent fetal vasculature Norrie’s disease. ROP

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Page 1: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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persistent fetal vasculature Norrie’s disease.

ROP

Page 2: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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• Coats' disease

FEVR

PERSISTANT FEATAL VASCULATUREPFV

Page 3: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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PHPV

PERSISTANT FEATAL VASCULATURE (PFV)

Page 4: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Coat's

Page 5: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Coat's MRI Criteria

Coat's prognosis

Page 6: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Coat's prognosis

After 1 year of surgery

FEVR

• It is a retinal vascular disease in which the peripheral retinal vessels fail to grow into the far peripheral retina,leavingarea of avascular retina• It is a life long activeretinal vascular disease

with variable periods of quiescence

Page 7: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Infant 4 ms of age presenting with leukocoria.There is no history of prematurity

OD OS

Page 8: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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FAOD OS

Vitrectomy

Page 9: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Page 10: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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thinretinal layers

Page 11: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Infant aged 6 msPresenting with Rt leukocoria

FA

Page 12: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Abnormal Peripheral vascular pattern

OCT

Page 13: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Page 14: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Page 15: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Page 16: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Page 17: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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Page 18: persistent fetal vasculature Norrie’s disease.eos-egypt.com/presentations/summer2018/010003.pdf•Coats' disease FEVR PERSISTANT FEATAL VASCULATURE PFV. 10/23/2018 3 PHPV PERSISTANT

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