hirsutism

9
HIRSUTISM Hirsutism DURU SHAH 1,2,3,4 & SUKHPREET PATEL 5 1 Gynaecworld Assisted Fertility Unit, 2 Breach Candy Hospital, 3 Jaslok Hospital and Research Centre, 4 Sir HN Hospital and Research Centre, Mumbai, India and 5 Gynaecworld, Mumbai, India (Received 11 July 2008; accepted 16 July 2008) Abstract Hirsutism is a distressing and relatively common problem, affecting 5 to 10% of women in the reproductive age group. It is usually a sign of androgen excess, the commonest cause being the polycystic ovarian syndrome (PCOS). Diagnosis depends mainly on assessment of the clinical symptoms and laboratory values of various hormones. Antiandrogens combined with various cosmetic therapies form the mainstay of treatment. Keywords: Hirsutism, polycystic ovarian syndrome, adrenal, antiandrogens The hair is the richest ornament of women’ – Martin Luther Introduction The richest ornament, when inappropriately placed, can be a cause of terrible distress for a woman. Hirsutism is a distressing and relatively common problem, affecting 5–10% of women in the repro- ductive age group [1]. It is defined as excess terminal hair growth in a female in a typically male distribution. It may be the result of either androgen excess or increased sensitivity of the hair follicles to normal levels of androgens. The current review deals with the various aspects of hirsutism such as its causes, diagnosis and management. Physiology of hair growth Besides the soles, palms and lips, the entire skin surface of the human body is covered with hair. The number of hair follicles that humans are born with remains more or less constant throughout life, and depends greatly on racial and constitutional factors. As defined earlier, hirsutism is the presence of excess terminal hair growth in a female in a typically male distribution. To understand this definition, it is essential to understand the normal physiology of hair growth. Hair can be classified in two different ways. 1. Structurally, hair may be of three different types, namely, lanugo, vellus and terminal hair. Lanugo is the soft downy hair that covers the fetus at birth, and is usually shed in the few months that follow. Vellus hairs are the small, straight, fair and non- pigmented hair that cover the apparently hairless areas of the body. Terminal hairs are the larger, curlier and darker, hence more visible hairs. Although they are normally present on the scalp, eyebrows, eyelashes, axillae and pubic area in both sexes, they are also seen on the face, back and abdomen in males. 2. Depending on its sensitivity to sex steroids, hairs may also be classified into sexual and non-sexual. Hair which responds to the sex hormones is termed sexual hair. Sexual hair grows on the face, lower abdomen, anterior thighs, the chest, breasts, pubic area, and in the axillae. Phases of hair growth Hair undergoes three distinct phases of growth, namely, anagen, catagen and telogen. Hair appears to Correspondence: Duru Shah, Kwality House, Above Chinese Room Restaurant, Kemps Corner, Mumbai 400 026, India. E-mail: [email protected] Gynecological Endocrinology, March 2009; 25(3): 140–148 ISSN 0951-3590 print/ISSN 1473-0766 online ª 2009 Informa Healthcare USA, Inc. DOI: 10.1080/09513590802531567 Gynecol Endocrinol Downloaded from informahealthcare.com by Michigan University on 11/02/14 For personal use only.

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HIRSUTISM

Hirsutism

DURU SHAH1,2,3,4 & SUKHPREET PATEL5

1Gynaecworld Assisted Fertility Unit, 2Breach Candy Hospital, 3Jaslok Hospital and Research Centre, 4Sir HN Hospital and

Research Centre, Mumbai, India and 5Gynaecworld, Mumbai, India

(Received 11 July 2008; accepted 16 July 2008)

AbstractHirsutism is a distressing and relatively common problem, affecting 5 to 10% of women in the reproductive age group. It isusually a sign of androgen excess, the commonest cause being the polycystic ovarian syndrome (PCOS). Diagnosis dependsmainly on assessment of the clinical symptoms and laboratory values of various hormones. Antiandrogens combined withvarious cosmetic therapies form the mainstay of treatment.

Keywords: Hirsutism, polycystic ovarian syndrome, adrenal, antiandrogens

‘The hair is the richest ornament of women’ – Martin

Luther

Introduction

The richest ornament, when inappropriately placed,

can be a cause of terrible distress for a woman.

Hirsutism is a distressing and relatively common

problem, affecting 5–10% of women in the repro-

ductive age group [1]. It is defined as excess terminal

hair growth in a female in a typically male distribution. It

may be the result of either androgen excess or

increased sensitivity of the hair follicles to normal

levels of androgens. The current review deals with

the various aspects of hirsutism such as its causes,

diagnosis and management.

Physiology of hair growth

Besides the soles, palms and lips, the entire skin

surface of the human body is covered with hair. The

number of hair follicles that humans are born with

remains more or less constant throughout life, and

depends greatly on racial and constitutional factors.

As defined earlier, hirsutism is the presence of excess

terminal hair growth in a female in a typically male

distribution. To understand this definition, it is

essential to understand the normal physiology of hair

growth.

Hair can be classified in two different ways.

1. Structurally, hair may be of three different types,

namely, lanugo, vellus and terminal hair. Lanugo is

the soft downy hair that covers the fetus at birth,

and is usually shed in the few months that follow.

Vellus hairs are the small, straight, fair and non-

pigmented hair that cover the apparently hairless

areas of the body. Terminal hairs are the larger,

curlier and darker, hence more visible hairs.

Although they are normally present on the scalp,

eyebrows, eyelashes, axillae and pubic area in

both sexes, they are also seen on the face, back

and abdomen in males.

2. Depending on its sensitivity to sex steroids, hairs

may also be classified into sexual and non-sexual.

Hair which responds to the sex hormones is

termed sexual hair. Sexual hair grows on the

face, lower abdomen, anterior thighs, the chest,

breasts, pubic area, and in the axillae.

Phases of hair growth

Hair undergoes three distinct phases of growth,

namely, anagen, catagen and telogen. Hair appears to

Correspondence: Duru Shah, Kwality House, Above Chinese Room Restaurant, Kemps Corner, Mumbai 400 026, India. E-mail: [email protected]

Gynecological Endocrinology, March 2009; 25(3): 140–148

ISSN 0951-3590 print/ISSN 1473-0766 online ª 2009 Informa Healthcare USA, Inc.

DOI: 10.1080/09513590802531567

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be growing continuously in humans due to the lack of

synchrony between the phases of different hair

follicles. Therefore, although some of the follicles

grow actively in the anagen phase, the others may be

in the telogen or resting phase. The ratio of the

duration of the anagen to telogen phase is different for

hair belonging to different areas of the body. Although

the anagen phase for hair on the scalp may last a few

years, it may only last a few months for body hair. The

sex hormones have an effect on the duration of the

various phases of hair growth (Table I).

Effect of sex hormones on hair

Amongst the sex steroids, androgens are of utmost

importance for regulating the distribution pattern

and characteristic of hair. At puberty, with the

increase in the amount of circulating androgens,

there is stimulation of sexual hair. Although this gives

rise to axillary and pubic hair in both sexes, it also

stimulates sexual hair on other sites in the male, such

as the face, chest, etc. Thus, the soft vellus hair is

converted to the dark, coarse, pigmented terminal

hair. In the presence of an excess of androgens or an

increase in the sensitivity of hair follicles to circulat-

ing androgens, stimulation of sexual hair may

similarly manifest as hirsutism in females.

Androgens have a paradoxical effect on scalp hair,

leading to balding. This is due to a reduction of the

anagen phase and regression of scalp hair to vellus

hair [1,2]. Therefore, associated balding may be

observed in hirsute women.

Androgens in women

Androgens in women can arise from three different

sources

1. Ovary

2. Adrenal

3. Peripheral conversion

Testosterone, androstenedione, and dehydroe-

piandrosterone sulphate (DHEAS) are secreted in

varying proportions from the ovary and adrenal gland

(Figure 1). Therefore, measurement of these levels is

an indirect evidence of the source and therefore, the

cause of hirsutism. Although an excess of DHEAS

exclusively indicates an adrenal origin, testosterone

elevations are usually of ovarian origin, and andros-

tenedione may be of adrenal or ovarian origin.

Dihydrotestosterone (DHT) is a potent metabolite

of testosterone, formed in the hair follicle, with the

help of 5a reductase. However, the levels of DHT

may be normal in hirsute women. This is due to its

rapid metabolism before it is secreted from the skin

into the circulation [3].

Approximately 80 and 19% of testosterone is

protein bound to sex steroid binding globulin

(SHBG) and albumin, respectively, thus, leaving

only 1% unbound. Because androgenicity is depen-

dent on mainly the unbound fraction of testosterone,

it is important to measure the free testosterone levels.

Besides, any factor which reduces the SHBG levels,

such as hyperinsulinaemia, leads to an excess of

circulating testosterone, and may therefore, manifest

as hirsutism.

However, because androstenedione and DHEAS

are not significantly protein bound, their biologically

available hormone activity is well reflected by their

routine immunoassay.

Ovarian and adrenal androgen secretion are under

the control of luteinising hormone (LH) and

adrenocorticotropic hormone (ACTH), respectively.

Unlike estrogen, androgens do not control LH

and ACTH secretion, and so there is no negative

Table I. Effect of sex hormones on sexual hair.

Hormone Effect on hair

Estrogens Shorten telogen phase

Reduce rate of hair growth ! thinner,

less pigmented hair

Progestogens Variable effect depending on their

androgenic activity

Androgens Lengthen anagen phase

Increase hair follicle size

Increase hair follicle diameter

Increase sebum secretionFigure 1. Sources of androgens in women.

Hirsutism 141

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feedback mechanism. Therefore, excess ovarian and

adrenal production can readily occur.

Causes of hirsutism

The causes of hirsutism can be classified into

Ovarian, adrenal, iatrogenic and idiopathic (Figure 2).

Hirsutism: the ovarian component

Polycystic ovarian syndrome

Polycystic ovarian syndrome (PCOS) is responsible

for the majority of women presenting with hirsutism

[2].

It is usually slow progressing, starts around

puberty, and gradually worsens with time, if not

treated. Hirsutism due to PCOS may be accompa-

nied by acne, weight gain, cycle irregularity, inferti-

lity and hair loss from the scalp. Hyperpigmentation

or acanthosis nigricans may also be observed in 5%

of obese women with insulin resistance.

In our personal series of over 500 PCOS patients,

46% presented to us with the complaint of hirsutism.

Only 38% of these demonstrated an elevated free

testosterone levels.

The ovary is usually the source of androgen excess

in women with PCOS. Hyperinsulinaemia further

exacerbates the problem by stimulating the thecal

cells and reducing the SHBG (Figure 3). Insulin

resistance can occur in up to 50% of patients with

PCOS [4,5].

Increase in weight also results in a reduction in the

SHBG, thereby increasing the free testosterone.

Therefore, weight loss is an extremely important

measure in treatment of hirsutism for women with

PCOS (Figure 4).

Laboratory investigations may reveal elevated

LH and insulin values. Further, an increase in

testosterone, androstenedione and DHEAS may also

be observed [6]. The best measures of objectively

measuring hyperandrogenism are free testosterone

levels or the free testosterone index. However, not

all patients with PCOS have elevated circulating

androgen levels, and not all circulating andro-

gens will be accounted for with these tests. In our

personal series of over 500 PCOS patients, 46%

presented to us with the complaint of hirsutism.

Only 38% of these demonstrated an elevated

free testosterone levels. Testosterone values do

not usually exceed 200 ng/dL in women with

PCOS.

Diagnosing PCOS can sometimes pose a dilemma

to the physician. During the last 20–30 years many

definitions for PCOS have been presented, as it

became clear that the description of Stein and

Leventhal represented only one end of the spectrum.

On 28 January 2004, the European Society for

Human Reproduction and Embryology and the

American Society for Reproductive Medicine co-

sponsored the Rotterdam PCOS consensus work-

shop group to revise the guidelines for diagnosis and

management that the National Institutes of Health

released in 1990 [4,5]. The revised guidelines have

been briefly mentioned.

The Rotterdam panel concluded that PCOS

encompasses a broader variety of manifestations of

ovarian dysfunction than those included in the

original diagnostic criteria defined by the National

Institutes of Health in 1990. Although the cardinal

features are hyperandrogenism and polycystic ovary

morphology, no single criterion is sufficient for

clinical diagnosis.

To be diagnosed with PCOS by the Rotterdam

criteria, a woman must have two of the following

three manifestations: irregular or absent ovulation,

elevated levels of androgenic hormones, and/or

enlarged ovaries containing at least 12 follicles each.

Other conditions with similar signs, such as andro-

gen-secreting tumors or Cushing’s syndrome, must

Figure 2. Causes of Hirsutism.

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be ruled out. Polycystic ovaries with normal ovarian

function and without hyperandrogenism should not

be considered PCOS without further workup.

The panel also recommended that women with

PCOS be evaluated for metabolic syndrome with

measurements for abdominal obesity, triglycerides,

high-density lipoproteins, hypertension, and fasting

and two-hour glucose tolerance.

Further, they clarified the ultrasound criteria for

polycystic ovaries. Polycystic ovaries are defined as

those found on ultrasound to contain 12 or more

follicles measuring 2–9 mm in diameter and/or have

an increased volume of 10 mL or greater. Only one

ovary meeting these criteria is necessary to meet the

definition of polycystic ovaries. Women found to

have incidental polycystic ovaries on an ultrasound

performed for another indication should not be

considered to have PCOS unless there is corroborat-

ing clinical evidence of the syndrome [4,5]. Poly-

cystic ovaries on pelvic ultrasound may be seen in 60

to 97% of women with hirsutism [2].

Hyperthecosis

The term hyperthecosis refers to the presence of

nests of luteinised theca cells in the ovarian stroma

secondary to differentiation of the ovarian interstitial

cells into steroidogenically active luteinised stromal

cells. These nests or islands are scattered throughout

the stroma of the ovary, rather than being confined to

areas around cystic follicles in PCOS. The symptoms

of hyperthecosis are very similar to that of PCOS [7].

However, they usually suffer from a greater degree of

hyperandrogenism, and their testosterone levels may

exceed 150–200 ng/dL [8]. Besides, the LH and

FSH values of these women are usually within

normal limits.

Ovarian neoplasm

Rapidly developing hirsutism or virilisation warrants

the need to search for neoplasms. Less than 1% of

Figure 3. Mechanism of hirsutism in PCOS.

Figure 4. Mechanism of action of weight loss.

Hirsutism 143

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ovarian neoplasms secrete androgens. Ovarian neo-

plasms such as sex cord stromal tumors are rare and

usually responsible for rapidly developing hirsutism

with total testosterone values exceeding 200 ng/dL.

Sex cord Stromal tumors may be of various types,

namely, Granulosa cell tumors, Leydig cell tumors,

Sertoli–Leydig cell tumors and thecomas. Of these,

the Sertoli–Leydig and Leydig tumors are most

common. Although the Sertoli–Leydig cell tumours

are seen during the reproductive years, the Leydig

cell tumors generally present at or after menopause.

They are both usually unilateral and benign. Occa-

sionally, some primary ovarian epithelial tumors can

also secrete excess androgen. Thecomas are rarely

responsible for hirsutism in pregnant women. Eva-

luation with the help of transvaginal ultrasound,

computed tomography and MRI may help in

diagnosing ovarian neoplasms.

Hirsutism: the adrenal component

Cushing’s syndrome

Hypercortisolism secondary to excessive ACTH

production can be either from the pituitary gland

(Cushing’s disease), or from ectopic ACTH secre-

tion by a non-pituitary tumor (Cushing’ syndrome).

Even though it is an uncommon cause for hirsutism,

the morbidity and mortality related with it if

untreated warrants attention and treatment. Endo-

crine and radiological evaluation is essential to make

a diagnosis of Cushing’s disease or syndrome.

Endocrine evaluation includes ACTH levels, basal

and post corticotrophin releasing hormone (CRH)

injection, and the low and high dexamethasone

suppression test. Although ACTH levels may be

normal or high in pituitary or ectopic ACTH

secretion disorders, they are usually low in adrenal

neoplasms. Computed tomography and magnetic

resonance imaging are also useful modalities in

diagnosing a pituitary adenoma.

Congenital adrenal hyperplasia

Late onset congenital adrenal hyperplasia (CAH) is

responsible for 2–5% of women with hirsutism [2]. It

is almost always due to 21-hydroxylase deficiency,

the enzyme responsible for the conversion of 17a-

hydroxyprogesterone to 11-Deoxycortisol, thus lead-

ing to a reduction in circulating glucocorticoids [9].

This in turn leads to stimulation of ACTH, resulting

in hyperplasia of the adrenal cortex and an increase

of androgens (Figure 5).

CAH is often confused with PCOS, because the

initiation and progress of both are very similar,

starting around puberty, and gradually increasing

with age. They are also both associated with irregular

periods and polycystic ovaries on ultrasound.

However, basal elevated levels of 17a-hydroxypro-

gesterone levels and a positive ACTH stimulation

test is diagnostic of CAH due to 21-hydroxylase

deficiency. Women with CAH demonstrate an

increase in 17a-hydroxyprogesterone levels after

injection of a single dose of 0.25 mg of synthetic

ACTH (Synacthen), is diagnostic of late onset CAH.

Hirsutism: idiopathic

The term idiopathic hirsutism should be applied only

to women with normal ovulatory function and

circulating androgen levels, keeping in mind that a

history of regular menstrual cycles is not adequate to

rule out an ovulatory dysfunction and PCOS [10].

Less than 20% of women with hirsutism are

diagnosed as idiopathic, when the condition is strictly

defined [10]. Increase in skin 5a reductase levels

seems to be the primary pathology in idiopathic

hirsutism. As mentioned earlier, levels of DHT may

be normal despite an increase in 5a reductase activity

due to its quick metabolism in the skin. These

patients usually respond to 5a reductase inhibitor

therapy, and reduction of androgen secretion with

the help of oral contraceptive pills (OCPs) is of

limited value [10].

Hirsutism: iatrogenic

Hirsutism is occasionally due to the side effects of

drugs such as danazol, glucocorticoids, testosterone,

OCPs containing androgenic progesterones, etc.

Figure 5. Mechanism of hirsutism in congenital adrenal

hyperplasia.

144 D. Shah & S. Patel

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Therefore, history of drug use is important and

alternative medication should be offered to the

patient.

Diagnosis

Diagnosis of the cause of hirsutism is essential in

order to offer appropriate management to the patient.

Hirsutism should be differentiated from hypertricho-

sis and virilisation. Hypertrichosis is the excessive

growth of androgen independent vellus hair in non-

sexual areas. It is commonly familial, and can also be

seen in conditions such as hypothyroidism, anorexia

nervosa and malnutrition.

Virilisation is a condition in which in addition to

hirsutism, other symptoms of androgen excess such

as clitoromegaly, deepening of voice, increase in

muscle mass and libido, and breast atrophy are also

present.

The diagnosis of hirsutism can be simplified by

proceeding in an organised manner; starting

from history, physical examination and finally

investigations.

History

The history should reveal the onset and progression

of the problem. Although PCOS and late CAH start

at puberty and progress gradually, conditions such

as Cushing’s and androgen secreting tumors occur

at any age and are rapidly progressing. The most

common causes of hirsutism are PCOS and idio-

pathic hirsutism [11]. History of use of drugs

mentioned earlier, may reveal the cause of hirsut-

ism. The presence of menstrual irregularity, acne,

hair loss, clitoromegaly, hoarseness of voice, ab-

dominal weight gain, are the other symptoms of

androgen excess which should be enquired about.

Since thyroid disorders and hyperprolactinaemia

may rarely lead to hirsutism, symptoms regarding

thyroid disorders and galactorrhoea must be

looked into.

Physical examination

Basic physical examination should include height,

weight and calculation of BMI. The degree of

hirsutism can be assessed using the Ferriman–

Gallwey scoring system. This involves grading nine

body areas from zero to four, from no hirsutism to

the presence of severe hirsutism [12]. A score of eight

or more is suggestive of hirsutism. Signs of virilisa-

tion and galactorrhoea should be looked for during

the examination. Pelvic examination may rarely

reveal a palpable ovarian mass.

Moon face, striae, buffalo hump and supraclavi-

cular fat may suggest the diagnosis of Cushing’s

syndrome.

Investigations

Measurement of levels of the various androgenic

hormones may help in diagnosing the source of

androgen production. Serum testosterone levels

poorly correlate with severity of symptoms. However,

it is a useful indicator of serious pathology, and levels

more than 200 ng/dL should warrant further inves-

tigation for neoplasms. Low levels of SHBG are

observed in women with PCOS and are inversely

related to free testosterone levels. Patients with

polycystic ovaries may also exhibit high levels of LH.

Though DHEAS elevations are usually observed in

adrenal pathology, mildly elevated values may be

observed in PCOS. In the presence of DHEAS levels

of more that 700 mg/dL, with or without testosterone

elevation, an androgen producing adrenal tumor

should be strongly suspected [13].

Measurement of basal elevated levels of 17a-

hydroxyprogesterone levels, and an increase in its

level after injection of synthetic ACTH, is diagnostic

of late onset CAH.

Cushing’s syndrome can be evaluated with the

help of ACTH levels, basal and post CRH injection,

and the low and high dexamethasone suppression

test. Although ACTH levels may be normal or high

in pituitary or ectopic ACTH secretion disorders,

they are usually low in adrenal neoplasms. Com-

puted tomography and magnetic resonance imaging

are also useful modalities in diagnosing a pituitary

adenoma.

Treatment options for hirsutism

The management of hirsutism includes cosmetic

and medical management. Although medical

management is required to suppress the cause,

cosmetic treatment is equally essential for patient

satisfaction.

Androgen hormones can be blocked at multiple

levels with the help of anti-androgen therapy. These

include OCPs, cyproterone acetate (CPA), finaster-

ide, spironolactone and flutamide. They may func-

tion via one or multiple mechanisms (Figure 6). In

women with PCOS, insulin sensitisers also seem to

play a role in reduction of hirsutism [14].

Combination OCPs

Combination OCPs commonly contain ethinyl es-

tradiol with a varying progestational agent. The

androgenic activity of progestational agents vary

widely. However, when combined with ethinyl

estradiol, the net effect of the OCP is antiandrogenic

[15]. This antiandrogenic effect is achieved by

decreasing ovarian androgen production and by

increasing the SHBG, thereby reducing the circulat-

ing androgen fraction [16] (Figure 7).

Hirsutism 145

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The commonly prescribed OCPs for hirsutism

include a combination of 30 mg of ethinyl estradiol

with either 2 mg of CPA or 3 mg of drosperinone

(DRSP). A similar reduction in hirsutism scores has

been noted with OCPs containing CPA and DRSP

[17].

CPA is a 17-hydroxyprogesterone acetate deriva-

tive that competes with DHT for binding to the

androgen receptor and reduces LH levels which

decrease testosterone and androstenedione levels

[18].

DRSP, however, has both antiandrogen as well as

antimineralocorticoid activity. OCPs containing

DRSP affect adrenal steroidogenesis by reducing

synthesis and release of androgens in response to

ACTH, leaving adrenal production of cortisol un-

changed [6]. Therefore, this drug is effective in the

treatment of hyperandrogenism not only by causing

blockade of ovarian steroid production but also by

acting on the adrenals to reduce adrenal androgen

synthesis. OCPs containing ethinyl estradiol with

DRSP exert a significant antiandrogenic activity, and

is especially effective in improving facial hirsutism.

The beneficial effect is most obvious after six cycles

and continues thereafter at a slower rate [19].

The safety of DRSP has been a matter of concern,

especially with regard to venous thromboembolism.

A recent study based on 142,475 women years of

observation was conducted to compare risks of

adverse cardiovascular and other events associated

with the use of DRSP containing OCPs and other

OCPs. They concluded that the risks of serious

events in users of a DRSP containing OCP are

similar to those associated with the use of other

OCPs [20].

The addition of antiandrogens to OCPs as an add-

on therapy is controversial. However, a recent meta-

analysis included five comparisons of antiandrogens

combined with OCPs versus OCPs alone. These

comparisons showed no significant difference in end-

of-study hirsutism scores between treatment groups

[21]. Besides, addition of higher doses of CPA to

OCPs containing 2 mg of CPA provides no addi-

tional benefit [22].

CPA

CPA is a 17-hydroxyprogesterone acetate derivative

that competes with DHT for binding to the androgen

receptor and reduces LH levels which decrease

testosterone and androstenedione levels [10]. It is

not available in the United States but is used widely

in other countries both alone and as a component of

a combination OCP.

There are no clinical trials comparing CPA alone

with placebo. However, when CPA combined with

ethinyl estradiol as an OCP was compared to

placebo, there was a significant subjective reduction

in hair growth [22]. In studies where CPA was

compared with other drug modalities no difference in

clinical outcome was noted [22]. There were,

however, endocrinological differences in androgen

and estrogen levels between different drug therapies

[22].

Spironolactone

Spironolactone blocks the androgen receptor, inhi-

bits androgen production, and inhibits the 5a

Figure 6. Mechanism of action of anti-androgen drugs.

Figure 7. Mechanism of action of OCPs.

146 D. Shah & S. Patel

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reductase enzyme. Because it is an aldosterone

antagonist and a diuretic, its side effects include

polyuria, nocturia, dizziness, and hyperkalemia.

Other side effects such as irregular menstrual cycles

experienced by some women, and feminisation of the

male fetus, may be taken care of by the addition of

OCPs.

Spironolactone is commonly used in the dose of

100 mg per day for the treatment of hirsutism. The

Cochrane Database review involved a study of

spironolactone versus placebo or other antiandrogens

for hirsutism [23]. They concluded that 6 months of

treatment with 100 mg/day spironolactone compared

with placebo was associated with a statistically

significant subjective improvement in hair growth

and Ferriman–Galwey scores. Further, spironolac-

tone 100 mg/day is superior to finasteride 5 mg/day

and low dose CPA 12.5 mg/day (first 10 days of

cycle) up to 12 months after the end of treatment

[23].

Finasteride

Finasteride is a 5a reductase inhibitor, which reduces

the conversion of testosterone to the more potent

DHT. It is prescribed in the dose of 5 mg per day for

the treatment of hirsutism. Because finasteride can

cause feminisation of the male fetus, women of

reproductive age group must use effective contra-

ception during its use and they should be warned that

a 3-month drug-free period is required before they

get pregnant [8].

In comparison with other antiandrogen therapies,

although finasteride is equally effective to CPA and

ethinyl estradiol combination [24,25], it seems less

beneficial when compared with spironolactone [23].

Flutamide

Flutamide is a nonsteroidal androgen receptor

blocker used in the dose of 250–500 mg per day for

the treatment of hirsutism. It can especially be used

in women in whom estrogen therapy is contra-

indicated. Flutamide can cause feminisation of the

male fetus and women of reproductive age group

must use effective contraception.

Although flutamide is effective in reducing hirsut-

ism, potential hepatotoxicity, occasionally fatal,

limits the usefulness of this drug in hirsutism.

Insulin sensitisers

Hirsutism is frequently encountered in women with

PCOS, who also exhibit relative insulin resistance.

Besides, obesity has a negative impact on the

efficacy of treatments for hirsutism, thus weight

loss is necessary for a successful treatment

program [26].

There is promising data regarding the effects of

insulin sensitisers in the treatment of hirsutism,

particularly in patients with PCOS [14]. Data suggest

that hirsutism may be effectively treated by reducing

hyperinsulinaemia [27].

In comparison with OCPs containing CPA,

the latter was found to be responsible for

profound suppression of androgen activity, in

contrast to metformin, which induced negligible

change [27].

Meta-analysis of comparisons of other antian-

drogens (spironolactone and flutamide) with

metformin, showed that the antiandrogen group

had significantly lower hirsutism scores than the

metformin group, but with large inconsistency across

studies [21]. Further, meta-analysis also revealed

that patients receiving a combination of flutamide

and metformin had significantly lower hirsutism

scores than patients receiving metformin alone [21].

Cosmetic treatment for hirsutism

Drugs are only partially effective on terminalised

hairs, and removal of these hairs is usually required.

Therefore, management of hirsutism is generally

based upon a dual approach: a pharmacological

therapy to reduce androgen secretion and/or andro-

gen action, and removal of terminal hair already

present. Electrolysis and laser photothermolysis are

considered the most effective cosmetic procedures,

although the effects of these methods should not be

considered permanent [28]. The application of

eflornithine hydrochloride 13.9% topical cream

may also be useful to ameliorate unwanted facial

hair growth [29].

Conclusion

Hirsutism has a significant negative impact on

psychosocial development and is usually a sign of

an underlying endocrine abnormality – namely,

androgen excess. A combination of one or more

treatments, including oral contraceptives, insulin

sensitisers, peripheral androgen blockade (spirono-

lactone, flutamide, CPA, or finasteride), and

mechanical/cosmetic amelioration and destruction

of unwanted hair (electrology and, potentially, laser

hair removal), is usually beneficial to the patient.

Overall, although hirsutism is a frequent and distres-

sing abnormality often signalling an underlying

endocrine disorder, a systematic approach to evalua-

tion will uncover the etiology, and combination

therapy will provide satisfactory treatment for most

patients.

Declaration of interest: The authors report no

conflicts of interest. The authors alone are respon-

sible for the content and writing of the study.

Hirsutism 147

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