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DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department of Pediatrics Section of Cardiology

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Page 1: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5

YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT

Bee Jane T. Martinez, MDUP-PGH Department of Pediatrics

Section of Cardiology

Page 2: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

To discuss-ductal stenting and its technique-ductal stenting compared to mBTS-different vascular access

Page 3: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

GENERAL DATA:KB, 5/M

Tetralogy of Fallot with Pulmonary Valve Atresia with a restrictive vertical PDA supplying the pulmonary arteries

Page 4: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

- cyanosis at birth

- 6 to 10 months

- saturations 52% at room air

- mBTS ductal stenting

Page 5: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

PHYSICAL EXAMINATION: •dusky lips, RV heave, loud and single S2 with no murmur, cyanotic and clubbed nail beds. •cyanotic and clubbed nail beds

Page 6: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

DIAGNOSTICSDIAGNOSTICS• 2D-echocardiography showed Tetralogy of Fallot

(TOF) with Pulmonary valve atresia (PVA). The

pulmonary arteries were small and confluent and

were supplied by vertical ductus

Page 7: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

DIAGNOSTICSDIAGNOSTICS•Angiogram showed vertical ductus supplying small

confluent PAs not accessible for pda stenting from

the femoral arteries

Page 8: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department
Page 9: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

Internal Carotid Artery

Subclavain Artery

Page 10: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department
Page 11: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department
Page 12: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

• Over the past three decades, the technique of ductal stenting has markedly improved along side developments in catheter and stent technology

• Ductal stenting has been almost exclusively done in newborn infants as a short-term palliation.

Xu W, Xia C, Zhang Z, et al. Efficacy of arterial duct stenting in neonatal pulmonary atresia with intact ventricular septum. Jul 2011; 39(7): 621-624.

Page 13: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

• Vascular access • Femoral artery, femoral vein, right

axillary or left axillary artery …. • Right carotid arteriotomy …used in low

birth weight neonates…• In our patient, the left carotid

arteriotomy

Alwi M. Stenting the ductus arteriosus: Case selection, technique and possible complications. Ann Pediatr Cardiol. Jan-Jun 2008;

1(1): 38–45

Schneider M, Zartner, Sidiropoulos P, et al. Stent implantation of the arterial duct in newborns with duct-dependent circulation. European Heart Journal. 1998;19: 1401–1409

Page 14: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

• Post ductal stenting, the saturations at room air increased from a baseline of 52% to 85%

• Post ductal stenting, there was an improvement in the degree of blood flow toward both PAs.

• The child had a rapid recovery and was discharged 24 hours after the procedure.

LPA

RPA

Page 15: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

PDA STENTING mBTS

Cost Charity Pay

P40, 000P120,000-170,000

P40,000P200,000

Duration of hospital stay

2 days 5-7 days

Complications Bleeding, stent occlusion

Scarring, adhesions,

bleeding, shunt occlusion,

phrenic nerve injury,

Page 16: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

• ductal stenting in older children, like those in neonates, can also be safely and effectively performed as an alternative to mBTS

• unique technique with low complication rates

• hospital stay of the patient was shorter in ductal stenting compared with mBTS

Page 17: DUCTAL STENTING THROUGH LEFT INTERNAL CAROTID ARTERY IN A 5 YEAR OLD MALE WITH PULMONARY VALVE ATRESIA: A CASE REPORT Bee Jane T. Martinez, MD UP-PGH Department

THANK YOU