Download - Vascular anomalies
Vascular Anomalies: Recognition
Objective
• By the end of the presentation the participants will be able to recognize vascular lesions on clinical appearance.
ISSVA 2014• The International Society for the Study of Vascular
Anomalies was founded in 1992 during the International Workshop on Vascular Anomalies held in 1990 in Amsterdam.
• The term anomalies encompasses hemangiomas and vascular malformations. The purpose of the Society is to promote, on a national and international level, clinical and scientific research in all fields, that will lead to advances in knowledge concerning all aspects of vascular anomalies.
Vascular anomaliesVascular Tumors Vascular malformations
Infantilehemangioma
Congenitalhemangioma
NICH RICH
• Capillary malformation • Venous malformation• Lymphatic malformation
• Arterial malformation • Arteriovenous fistula• Arteriovenous malformation
Combined types
Slow flow Fast flow
Differentiating Features
TUMOR• True tumors, with
proliferation of the vascular endothelium
• >3:1 female : male• Small or absent at birth• Rapid growth during infancy • Self-limited• Diagnosis: Clinical +
appearence
MALFORMATION• No tumor, comprised of
dysplastic vessels• 1:1 female : male• Present at birth• Growth proportional to child• Never disappear• Diagnosis: MRI, Doppler
ultrasonography, angiography
RICH
NICH
Infantile Hemangioma
Tufted hemangioma
Spindle cell hemangioma
Pyogenic granuloma
Kaposiform hemangioendothelioma
Retiform hemangioendothelioma
Papillary intralymphaticangioendothelioma
Composite hemangioendothelioma
Kaposi sarcoma
Angiosarcoma
Capillary Malformations
CM with bone or soft tissue overgrowth
Sturge Weber Syndrome
Hereditary hemorrhagic telengiectasia
Nevus simplex
27
Lymphatic Malformations
In the oral cavity appear as multiple translucent non-compressible cysts or vesicles of <2 cm.
containing viscous clear fluid, producing apebbly or warty surface resembling “frogspawn” or “tapioca pudding”.
MICROCYSTIC LM ( Outdated term Lymphangioma)
Macro Cystic LM
Gorham Stout disease
Primary Lymphedema
Common Venous Malformation
Familial cutaneomucosal vascular malformation
Blue rubber bleb nevus syndrome
Glomuvenous malforation
Sporadic AVM
AVM in HHT
Arterio venous fistula
Conclusion
• Vascular tumors are to be differentiated from vascular anomalies.
• The distinction is possible by history and careful clinical examination most of the time.
• In doubtful cases, biopsy is required.
Thank you
• QUESTIONS?• Or test will follow…