defectos congenitos de pared abdominal
DESCRIPTION
DEFECTOS CONGENITOS DE PARED ABDOMINAL. DEFECTOS CONGENITOS PARED ABDOMINAL. EMBRIOLOGIA 3ª SEMANA: CUATRO PLIEGUES SOMATICOS: 1 PLIEGUE CEFALICO 2 PLIEGUES LATERALES 1 PLIEGUE CAUDAL 18ª SEMANA: FUSION HACIA EL CORDON UMBILICAL. FORMACION DE LA PARED ANTERIOR TORACICA Y ABDOMINAL. - PowerPoint PPT PresentationTRANSCRIPT
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DEFECTOS CONGENITOS DE PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
EMBRIOLOGIA
3ª SEMANA:
CUATRO PLIEGUES SOMATICOS:
• 1 PLIEGUE CEFALICO• 2 PLIEGUES LATERALES• 1 PLIEGUE CAUDAL
18ª SEMANA:
• FUSION HACIA EL CORDON UMBILICAL.
• FORMACION DE LA PARED ANTERIOR TORACICA Y ABDOMINAL.
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DEFECTOS CONGENITOS PARED ABDOMINAL
FISIOPATOLOGIA
FALLA EN LA MIGRACION Y FUSION:
PLIEGUE CEFALICO:
CELOSOMIA SUPERIOR
SINDROME DE CANTRELL
PLIEGUE CAUDAL:
CELOSOMIA INFERIOR
SINDROME LINEA MEDIA INFERIOR
PLIEGUES LATERALES:
CELOSOMIA MEDIA
ONFALOCELE
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
PATOLOGIAS MAS COMUNES
ONFALOCELE
GASTROSQUISIS
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DEFECTOS CONGENITOS PARED ABDOMINAL
ONFALOCELE
GASTROSQUISIS
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DEFECTOS CONGENITOS PARED ABDOMINAL
CARACTERISTICAS ONFALOCELE GASTROSQUISIS
LOCALIZACION
DEFECTO
ANILLO
UMBILICAL
LATERAL AL
CORDON ( DER.)
TAMAÑO DEL
DEFECTO4 – 10 CM < 4 CM
LOCALIZACION
DEL CORDONSOBRE EL SACO SOBRE LA PIEL
POSICION DEL HIGADO HERNIADO IN SITU
APARIENCIA DEL INTESTINO
NORMAL EDEMATOSO
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DEFECTOS CONGENITOS PARED ABDOMINAL
CARACTERISTICAS ONFALOCELE GASTROSQUISIS
CAVIDAD ABDOMINAL PEQUEÑA CASI NORMAL
MALROTACION INTESTINAL
PRESENTE PRESENTE
ATRESIA INTESTINAL RARO COMUN
ISQUEMIA MESENTERIO RARO COMUN
ANOMALIAS ASOCIADAS 40 – 80 % RARO
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DEFECTOS CONGENITOS PARED ABDOMINAL
CARACTERISTICAS ONFALOCELE GASTROSQUISIS
NEC RARO 18 %
MALABSORCION AUSENTE FRECUENTE
PREMATURIDAD 10 – 20 % 50 – 60 %
EDAD MATERNA > 20 AÑOS < 20 AÑOS
PRONOSTICO DE SOBREVIDA
CON CARDIOPATIA: 20%
SIN CARDIOPATIA: 70%70 – 90 %
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
HEPATONFALOCELE
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
ONFALOCELE CON SACO ROTO
GASTROSQUISIS
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
MANEJO INICIAL
• PROTECCION ASAS EVISCERADAS• VENOCLISIS (GASTROSQUISIS : 180CC/KG/DIA)
• MANTENIMIENTO TEMPERATURA• DESCOMPRESION GASTRICA• DECUBITO LATERAL• ANTIBIOTICOS• TRANSFERENCIA COORDINADA
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DEFECTOS CONGENITOS PARED ABDOMINAL
MANEJO QUIRURGICO
ONFALOCELE GASTROSQUISIS
> 8 CM < 8 CMREANIMACION
HIDROELECTROLITICA
SACO INTEGRO SACO ROTO
ESCLEROTERAPIADEL SACO
MANEJO DE LAEVENTRACION
SILO
CIERREPRIMARIO
CON HIPERTENSION ABDOMINAL
SIN HIPERTENSIONABDOMINAL
CIERRE DEFINITIVO UCI - RN
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
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DEFECTOS CONGENITOS PARED ABDOMINAL
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GRACIAS