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1 health technology assessment indonesia pencegahan thalassemia hasil kajian HTA 2009 dirjen bina pelayanan medik kementrian kesehatan republik indonesia 2 Usefulness of Cell Counter-Based Parameters and Formulas in Detection of -Thalass emia Trait in Areas of High Prevalence. rathod DA, kaur Amarjeet, Patel Vinod 3 haemoglobinopathies in southeast asia suthat fucharoen and pranee winichaagoon thalasemia research center, institute of molecular biosciences, mahidol universi ty, nakhonpathom, thailand 4 World Health Organization/Thalassaemia International Federation. Prosiding dari: Joint meeting on the prevention and control of haemoglobinopathies. Nicosia-Cyp rus: World Health Organization/Thalassaemia International Federation, 1994:20. 5 Riset Kesehatan Dasar Depkes 2007. 6 Wahidiyat PA. Komplikasi pada talasemia mayor. Dalam: Subanada IB, Kumara Wati KD, Sidiartha IGL, Lingga Utama IMGD, Supartha M, Setyorini A dkk, penyunting. Pendidikan Kedokteran Berkelanjutan Ilmu Kesehatan Anak X FK UNUD/RSUP Sanglah. Denpasar: Bagian IKA FK UNUD, 2010.h.119-32. 7 http://www.idai.or.id/saripediatri/pdfile/13-4-12.pdf profil pertumbuhan, hemoglobin pre transfusi, kadar ferritin, dan usia tulang an ak pada thallasemia mayor 8 clinical hematology and fundamentals of hemostasis fourth edition pengarang; denise M. Harmening BAB 12, hemolityc anemias; intracorpuscular defects; Thalassemia halaman 186 9 buku ajar ilmu penyakit dalam jilid 2 edisi 5 bab 220 thalassemia: manifestasi klinis, pendekatan diagnosis, dan thalassemia i ntermedia halaman 1388 10 kapita selekta hematologi A.V. hoffbrand - J.E pettit - P.A.H Moss edisi 4 bab 6 kelainan genetik pada hemoglobin halaman 69-70 11 http://www.idai.or.id/saripediatri/pdfile/13-4-3.pdf Kebutuhan Transfusi Darah Pasca-Splenektomipada Thalassemia Mayor Murti Andriastuti, Teny Tjitra Sari, Pustika Amalia Wahidiyat, Siti Ayu Putriasi h Departemen Ilmu Kesehatan Anak Fakultas Kedokteran Universitas Indonesia RS Cipt o Mangunkusumo, jakarta 12 http://www.who.int/genomics/public/geneticdiseases/en/index2.html 13 pathology kumar robbin chapter 12 halaman 403 14 clinical hematology and fundamentals of hemostasis fourth edition pengarang; denise M. Harmening BAB 12, hemolityc anemias; intracorpuscular defects; Thalassemia halaman 193 15 artikel indian J Med Res 134, october 2011 abnormal haemoglobins: detection and characterization henri wajcman and kamran moradkhani INESRM, universite Paris-Est 16 Thalasemia major in adults; short stature, hyperpigmentation, inadequate chelati on, and transfusion transmitted infection are key features anupam prakash and ramesh aggarwal 4 maret 2012 released http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3309622/#sec1-4title 17 beta thalassemia renzo galanello and raffaella origa published 2010 may 21 http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2893117/ 18 http://www.thalassemia.org.cy/english/thalassemia/therapy_treatment.htm#1 pancryprian thalassemia association conventional treatment for thalassemia 19 thalassemia major: the present and the future marina baldini 4 maret 2012 http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3309623/ 20 management of adult and adolescent thalassemia M.D. Cappellini centro anemie congenite-policlinico hospital IRCCS, univerisity of milan, italy 21 guideline: splenectomy in beta-thalassemia major http://www.ithanet.eu/ithapedia/index.php/Guideline:Splenectomy_in_%CE%B2-thalas semia_major 22 anemia, blood transfusions, iron overload and myelodysplastic syndromes: a handbook for adult MDS patient MDS foundation 23 Peraturan pemerintah Republik Indonesia nomor 18 tahun 1980 BAB I Pasal 1 24 university of michigan hospitals and health centers adult blood transfusion clinical guidelines 25 buku ajar ilmu penyakit dalam jilid 2 edisi 5 bab 189 darah dan komponen: komposisis, indikasi dan cara pemberian halaman 1191-1196 26 Sudoyo, A.W., Setiyohadi, B., Alwi, I., et. al. (2006). Buku Ajar Ilmu Penyakit Dalam. Jakarta : Pusat penerbitan Departemen Ilmu Penyakit Dalam FKUI 27 Possible risks of blood transfusions http://www.cancer.org/treatment/treatmentsandsideeffects/treatmenttypes/bloodpro ductdonationandtransfusion/blood-product-donation-and-transfusion-possible-trans fusion-risks 28 adverse reactions of blood products http://library.med.utah.edu/WebPath/TUTORIAL/BLDBANK/BBTXRXN.html 29 buku ajar ilmu penyakit dalam jilid 2 edisi 5 bab 188 dasar-dasar transfusi darah halaman 1185 30 risk of blood transfusion http://www.nhs.uk/Conditions/Blood-transfusion/Pages/Risks.aspx 31 harmening halaman 75 32 harmening halaman 569-575