Cystic FibrosisCystic Fibrosis By:By:

Shanelle JohnsonShanelle JohnsonCaleb MartinCaleb MartinRafail LuziRafail Luzi

Christopher AlvaradoChristopher Alvarado

CaseCase David Smith,34David Smith,34 Caucasian Caucasian Born with cystic fibrosisBorn with cystic fibrosis He had delayed growth in teen years He had delayed growth in teen years Weight LossWeight Loss Nasal Congestion Nasal Congestion Has Cystic FibrosisHas Cystic Fibrosis

What is Cystic FibrosisWhat is Cystic Fibrosis A passed down through family which A passed down through family which

causes thick sticky mucus that causes thick sticky mucus that builds up in the lungs, digestive builds up in the lungs, digestive tract, and other body parts.tract, and other body parts.

Most common lung disease in Most common lung disease in children and young adults.children and young adults.

Life threatening disease.Life threatening disease.

History of Cystic FibrosisHistory of Cystic Fibrosis Cystic fibrosis did not exist until the late Cystic fibrosis did not exist until the late

1930’s.1930’s. In the 1930’s a Swiss pediatrician Dr. In the 1930’s a Swiss pediatrician Dr.

Fanconi called this disease celiac syndrome.Fanconi called this disease celiac syndrome. Dr. Dorothy Anderson was the first to give Dr. Dorothy Anderson was the first to give

the disease it’s definitive description. the disease it’s definitive description. In the 1940’s Drs. Sydney Farber and Harry In the 1940’s Drs. Sydney Farber and Harry

Shwachman say vitamin A was the cause of Shwachman say vitamin A was the cause of Cystic Fibrosis.Cystic Fibrosis.

In 2000, they say the median life In 2000, they say the median life expectancy has reached 37 years in 2005.expectancy has reached 37 years in 2005.

Organs affected by Cystic Organs affected by Cystic FibrosisFibrosis

SinusesSinuses Lungs Lungs Skin Skin Liver Liver Pancreas Pancreas IntestinesIntestines Reproductive OrgansReproductive Organs

CausesCauses Caused by a defected gene that causes the Caused by a defected gene that causes the

body to produce abnormal thick sticky fluid body to produce abnormal thick sticky fluid called mucus.called mucus.

The mucus builds up in the breathing The mucus builds up in the breathing passages of the lungs and pancreas.passages of the lungs and pancreas.

Built up mucus in the lungs could be life Built up mucus in the lungs could be life threatening.threatening.

Children usually be diagnosed by 2 years Children usually be diagnosed by 2 years old.old.

Lungs get clogged makes it hard for patient Lungs get clogged makes it hard for patient to breath. to breath.

SymptomsSymptoms New BornNew Born- Delayed GrowthDelayed Growth- Failure to gain weight normally during childhoodFailure to gain weight normally during childhood- No bowel movements in first 24 to 48 hours of lifeNo bowel movements in first 24 to 48 hours of life- Salty tasting skinSalty tasting skin Bowel FunctionBowel Function- Belly pain from constipation- Belly pain from constipation- Increased gas, bloating, or swollenIncreased gas, bloating, or swollen- Nausea/ loss of appetiteNausea/ loss of appetite Related to lungsRelated to lungs-Fatigue -Fatigue -Cough-Cough-Increased mucus-Increased mucus

TreatmentTreatmentTreatment for lungsTreatment for lungs Antibiotics to prevent lung and sinus Antibiotics to prevent lung and sinus

infection.infection. Inhaled medicines to clear the airways.Inhaled medicines to clear the airways. Lung problems could be treated through Lung problems could be treated through

aerobic exercise.aerobic exercise.Treatment for bowelTreatment for bowel Pancreatic enzymes to help absorb protein Pancreatic enzymes to help absorb protein

and fats.and fats.Monitor at homeMonitor at home Avoid smoking, dust, dirt, fumes, household Avoid smoking, dust, dirt, fumes, household

chemicals, fireplace smoke, and mold. chemicals, fireplace smoke, and mold.

Doctors deal with Cystic Doctors deal with Cystic FibrosisFibrosis

PulmonologistPulmonologist Social Worker Social Worker Physical Therapist Physical Therapist

Social WorkerSocial Worker Help people overcome their problemsHelp people overcome their problems Graduate degree and experience Graduate degree and experience May engaged research, advocacy, and May engaged research, advocacy, and

consultingconsulting Specialized field:Specialized field:

ChildrenChildren FamiliesFamilies AdolescentsAdolescents ElderlyElderly

900 hours of supervised field internship 900 hours of supervised field internship

Pulmonologist Pulmonologist Specialized in the field of pulmary Specialized in the field of pulmary

medicine:medicine: Diagnosis & treatment of disease Diagnosis & treatment of disease

condition and abnormalities of the lungs condition and abnormalities of the lungs and cardio- pulmonary system and and cardio- pulmonary system and respiratory tractrespiratory tract

Internal medicine, physicians become Internal medicine, physicians become certifiedcertified

Specialize in critical care trained in the Specialize in critical care trained in the management and treatment management and treatment

Physical Therapist Physical Therapist Type of treatment that helps with Type of treatment that helps with

health problems make it hard.health problems make it hard. Move around & do everyday Move around & do everyday May relieve pain May relieve pain Graduate degree from accredited Graduate degree from accredited

physical therapy program to become physical therapy program to become license. license.

VisualsVisuals

Final TreatmentFinal Treatment There is There is NO cureNO cure Prevent any further life Prevent any further life

complicationscomplications Engage at least 3 times a week in a Engage at least 3 times a week in a

workout regimentworkout regiment & lastly antibiotics & lastly antibiotics (zithromax)(zithromax)

AntibioticsAntibioticsZithromax Zithromax (500mg) used to reduce infections (500mg) used to reduce infections

and mucus from the lungs of the patients.and mucus from the lungs of the patients.Take once a day with or without food, 5 Take once a day with or without food, 5

times a week.times a week.It may cause upset stomach , diarrhea , It may cause upset stomach , diarrhea ,

vomiting and etc. David Smith will vomiting and etc. David Smith will have to come in for a consultation.have to come in for a consultation.

Laboratory ResultsLaboratory Results•Aldosterone-Upright: 4-31 ng/dl Aldosterone-Upright: 4-31 ng/dl •Amylase-30-100 U/LiterAmylase-30-100 U/Liter•Bilirubin-Total: 0.2-1.2,mg/dl;direct<0.3 Bilirubin-Total: 0.2-1.2,mg/dl;direct<0.3 mg/dl mg/dl •BUN:7-20 mg/dlBUN:7-20 mg/dl•Calcium-8.8-10.3 mg/dlCalcium-8.8-10.3 mg/dl•CO2(total)-23-30 meq/lCO2(total)-23-30 meq/l•Creatine-0.5-1.4 mg/dlCreatine-0.5-1.4 mg/dl

Insurance Verification Insurance Verification FormForm

Name of primary insurance carrier: David Matt Name of primary insurance carrier: David Matt Smith.Smith.

Subscriber: David Matt Smith.Subscriber: David Matt Smith. My Benefits, etc.My Benefits, etc. I have a limit of $80.00 or number of visits of 5.I have a limit of $80.00 or number of visits of 5. Benefits are covered yearly from 3.4.78 through etc.Benefits are covered yearly from 3.4.78 through etc. My calendar deductible is $10.00My calendar deductible is $10.00 Co-pay Visits: $20.00Co-pay Visits: $20.00 My Insurance is not Contracted.My Insurance is not Contracted.

I spoke with Chris Chambers of my insurance carrier I spoke with Chris Chambers of my insurance carrier on 3/6/12, their contact number is 345-547-8900.on 3/6/12, their contact number is 345-547-8900.

SourcesSources "A History of Cystic Fibrosis." "A History of Cystic Fibrosis." Cystic FibrosisCystic Fibrosis. N.p., n.d. . N.p., n.d.

Web. 1 June 2012. Web. 1 June 2012. <http://www.aboutcysticfibrosis.com/cystic-fibrosis-<http://www.aboutcysticfibrosis.com/cystic-fibrosis-history.htm>.history.htm>.

"Cystic Fibrosis - When To Call a Doctor - Watchful waiting "Cystic Fibrosis - When To Call a Doctor - Watchful waiting - Children's Health." - Children's Health." Health Information, Resources, Tools Health Information, Resources, Tools & News Online - EverydayHealth.com& News Online - EverydayHealth.com. N.p., n.d. Web. 1 . N.p., n.d. Web. 1 June 2012. <http://www.everydayhealth.com/health-June 2012. <http://www.everydayhealth.com/health-center/cystic-fibrosis-when-to-call-a-doctor.aspx>.center/cystic-fibrosis-when-to-call-a-doctor.aspx>.

"Cystic fibrosis - PubMed Health." "Cystic fibrosis - PubMed Health." National Center for National Center for Biotechnology InformationBiotechnology Information. N.p., n.d. Web. 1 June 2012. . N.p., n.d. Web. 1 June 2012. <http://www.ncbi.nlm.nih.gov/pubmedhealth/PMH0001167<http://www.ncbi.nlm.nih.gov/pubmedhealth/PMH0001167/>./>.

MLA formatting by BibMe.org.MLA formatting by BibMe.org.