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Arterial Switch Arterial Switch with Abnormal Coronaries with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 with Abnormal Coronaries with Abnormal Coronaries Francois Lacour Francois Lacour-Gayet, MD Gayet, MD Professor and Chief Professor and Chief Pediatric Cardiac Surgery Pediatric Cardiac Surgery Montefiore Children’s Hospital, Montefiore Children’s Hospital, Einstein College of Medicine, Einstein College of Medicine, New York City New York City

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Page 1: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Arterial SwitchArterial Switch

with Abnormal Coronarieswith Abnormal Coronaries

ASO, Cx. Coronaries AATS, SF 2012

with Abnormal Coronarieswith Abnormal Coronaries

Francois LacourFrancois Lacour--Gayet, MDGayet, MDProfessor and Chief Professor and Chief Pediatric Cardiac SurgeryPediatric Cardiac Surgery

Montefiore Children’s Hospital, Montefiore Children’s Hospital,

Einstein College of Medicine, Einstein College of Medicine,

New York CityNew York City

Page 2: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

DisclosureDisclosure

• None

ASO, Cx. Coronaries AATS, SF 2012

Page 3: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Yacoub Classification

ASO, Cx. Coronaries AATS, SF 2012Yacoub MH, RadleyYacoub MH, Radley--Smith R.M. Smith R.M. Thorax. 1978;33:418. Thorax. 1978;33:418.

Page 4: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

C C PlanchePlanche, F , F LacourLacour--GayetGayet et al et al Pediatric Cardiology 1998; 19: 297Pediatric Cardiology 1998; 19: 297--307307

Marie Lannelongue Classification

Based on the Course of the Coronaries

��Normal course:Normal course: 60%60%

��Looping courses: Looping courses: 35%35%

ASO, Cx. Coronaries AATS, SF 2012

��Looping courses: Looping courses: 35%35%

-- posterior posterior 20%20%

-- anterioranterior 1%1%

-- double loopingdouble looping 14%14%

��IntraIntra--mural course:mural course: 5%5%

Page 5: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

C C PlanchePlanche, F , F LacourLacour--GayetGayet et al et al Pediatric Cardiology 1998; 19: 297Pediatric Cardiology 1998; 19: 297--307307

Marie Lannelongue Classification

Based on the Course of the Coronaries

��Normal course:Normal course: 60%60%

��Looping courses: Looping courses: 35%35%

ASO, Cx. Coronaries AATS, SF 2012

��Looping courses: Looping courses: 35%35%

-- posterior posterior 20%20%

-- anterioranterior 1%1%

-- double loopingdouble looping 14%14%

��IntraIntra--mural course:mural course: 5%5%

Page 6: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Right SinusRight Sinus Left SinusLeft Sinus

Normal Course: 60%

ASO, Cx. Coronaries AATS, SF 2012

Not applicable to situs inversusNot applicable to situs inversus

Page 7: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Posterior Looping Course: 20%

ASO, Cx. Coronaries AATS, SF 2012

19%19% 1%1%

Page 8: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Anterior Looping Course: 1%

ASO, Cx. Coronaries AATS, SF 2012

Page 9: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Double Looping Course: 14%

Taussig Bing

ASO, Cx. Coronaries AATS, SF 2012

Page 10: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Kinking of

Posterior Vessel

Risks Depending on CourseRisks Depending on Course

ASO, Cx. Coronaries AATS, SF 2012

Stretching of

Anterior Vessel

Page 11: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Single OstiumSingle Ostium

ASO, Cx. Coronaries AATS, SF 2012

Anterior

Looping

Posterior

Looping

Double

Looping

Page 12: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Nearly ALL CASESNearly ALL CASES

ASO, Cx. Coronaries AATS, SF 2012

Page 13: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Intramural Course: 5%

Most Complex Form

Single ostium

ASO, Cx. Coronaries AATS, SF 2012

Yacoub type C Yacoub type B

Page 14: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

ASO TechniquesASO TechniquesClosed aortaClosed aorta

��Opened aorta: Opened aorta:

-- TrapTrap--doordoor

�� No trapNo trap--doordoor

ASO, Cx. Coronaries AATS, SF 2012

�� CustodiolCustodiol cardioplegiacardioplegia

�� No circulatory arrestNo circulatory arrest

��LecompteLecompte ManeuverManeuver

��PA reconstruction: PA reconstruction:

PantaloonPantaloon autologous pericardiumautologous pericardium

Page 15: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Aorta

High

Division of the Great VesselsDivision of the Great Vessels

Shorten the NeoShorten the Neo--AortaAorta

ASO, Cx. Coronaries AATS, SF 2012

PA

Low

Page 16: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

LargeLarge coronary buttonscoronary buttons

ASO, Cx. Coronaries AATS, SF 2012

The more complex, the more dissection The more complex, the more dissection

Page 17: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

LeftLeft buttonbutton

ASO, Cx. Coronaries AATS, SF 2012

No trap-door

Page 18: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

RightRight buttonbutton

ASO, Cx. Coronaries AATS, SF 2012

Page 19: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Right button in high positionRight button in high position

ASO, Cx. Coronaries AATS, SF 2012

Page 20: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

IntraIntra--mural coursemural course

ASO, Cx. Coronaries AATS, SF 2012

Yacoub Type C

Page 21: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Yacoub Type BYacoub Type B

ASO, Cx. Coronaries AATS, SF 2012

Page 22: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

IntraIntra--mural coronarymural coronaryYacoub type B

ASO, Cx. Coronaries AATS, SF 2012

C Planche C, F Lacour-Gayet et al. JTCVS 1988; 96: 354-63

Yacoub Type BRotation 180Rotation 180ºº

Page 23: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Yacoub type B,

No coronary relocation

ASO, Cx. Coronaries AATS, SF 2012

P Aubert et al, British Heart Journal 1978; 40: 204-10

Page 24: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Yacoub type B,

No coronary relocation

ASO, Cx. Coronaries AATS, SF 2012

N Moat et al JTCVS 1992, 103, 872-6

S Takeuchi, 1990; 50: 1000-2

Page 25: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Infundibular coronary branchInfundibular coronary branch

ASO, Cx. Coronaries AATS, SF 2012

VERY FREQUENTVERY FREQUENT

Page 26: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Excentric OstiumExcentric Ostium

ASO, Cx. Coronaries AATS, SF 2012

Page 27: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Malaligned CommissuresMalaligned Commissures

ASO, Cx. Coronaries AATS, SF 2012

Important

Page 28: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

AortoAorto--Pulmonary Diameter MismatchPulmonary Diameter Mismatch

ASO, Cx. Coronaries AATS, SF 2012

Page 29: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Side by side vesselsSide by side vessels

ASO, Cx. Coronaries AATS, SF 2012

Page 30: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

ExampleExample

ASO, Cx. Coronaries AATS, SF 2012

TGA-IVS

Double looping + Intra Mural + Side by Side

Page 31: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Harvesting common buttonHarvesting common button

ASO, Cx. Coronaries AATS, SF 2012

Page 32: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Incising the stenosed left ostiumIncising the stenosed left ostium

ASO, Cx. Coronaries AATS, SF 2012

Page 33: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Creating two buttonsCreating two buttons

ASO, Cx. Coronaries AATS, SF 2012

Page 34: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Results Results

ASO, Cx. Coronaries AATS, SF 2012

Results Results

Page 35: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Denver Children’s, 2002-2010

101 consecutive Arterial Switch, 49% cx ASO

Hospital Mortality : 0%

ATS, June 2012ATS, June 2012

ASO, Cx. Coronaries AATS, SF 2012

Hospital Mortality : 0%

• Coronary Failure: 2 patients

•1 transplantation, single ostium

•1 late death, DORV, Malaligned commissure

• 3 angioplasty

• No late reoperation

Page 36: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Survival Curve, 101 ASO

90%

95%

100%

99%

ASO, Cx. Coronaries AATS, SF 2012

50%

55%

60%

65%

70%

75%

80%

85%

90%

1 2 3 4 5 6 7 8 9 100 6M 1Y 2Y 3Y 4Y 5Y 6Y 7Y 8Y

ATS, June 2012ATS, June 2012

Page 37: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Mean LOS:13D

Complications: 25%

Most frequent in complex forms

No AV block

Failure to rescue: none

101 Arterial Switch101 Arterial Switch

ASO, Cx. Coronaries AATS, SF 2012

Failure to rescue: none

Risk Factor for Morbidity:

Malaligned commissures

Aortic arch repair

Coronary anatomy no more a risk factor

Page 38: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

1198 ASO, 1198 ASO,

Mean follow up 59MMean follow up 59M

324 coronary angiograms324 coronary angiograms

2% coronary reoperation2% coronary reoperation

Intra mural coronary p=0.002Intra mural coronary p=0.002

Late Coronary Complications after ASOLate Coronary Complications after ASO

Coronary events after arterial switch operation for TGA. Legendre A, Losay J, Serraf A et al. Coronary events after arterial switch operation for TGA. Legendre A, Losay J, Serraf A et al.

Circulation 2003, Suppl 1:II 186Circulation 2003, Suppl 1:II 186--9090

ASO, Cx. Coronaries AATS, SF 2012

Intra mural coronary p=0.002Intra mural coronary p=0.002

��Late Coronary Control in complex coronaryLate Coronary Control in complex coronary(CT Scan, MRI, coronarography)(CT Scan, MRI, coronarography)

Page 39: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

Late dilation of the neoLate dilation of the neo--aortaaorta

A Baruteau, V Lambert, Marie Lannelongue, Paris

2026 ASO2026 ASO, 1982-2012

118 Adult > 18Y with complex ASOMean Follow up 21.2 Y

�60% dilatation of the neo-aortic root

�8% reoperation for aortic regurgitation

ASO, Cx. Coronaries AATS, SF 2012

�8% reoperation for aortic regurgitation

�1,5% coronary reoperation

Page 40: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

ASO: They do wellASO: They do well

ASO, Cx. Coronaries AATS, SF 2012

WilliamWilliam, 20Y, French Junior Formula 1 Champion., 20Y, French Junior Formula 1 Champion.

Arterial Switch, Oct. 1991

Page 41: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

William, 20YWilliam, 20Y

Arterial Switch, 1991

ASO, Cx. Coronaries AATS, SF 2012

William

Page 42: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

ASO, Cx. Coronaries AATS, SF 2012

Page 43: Arterial Switch with Abnormal Coronariesaz9194.vo.msecnd.net/pdfs/120401/11.07.pdf · Arterial Switch with Abnormal Coronaries ASO, Cx. Coronaries AATS, SF 2012 Francois LacourFrancois

ASO, Cx. Coronaries AATS, SF 2012