retinitis pigmentosa ast

13
REFERAT R E T I N I T I S P I G M E N T O S A Disusun oleh : Astria Puspita Sari 1310221021 Pembimbing : dr. Naila Karima, Sp.M

Upload: astriapuspitasari

Post on 06-Feb-2016

66 views

Category:

Documents


2 download

DESCRIPTION

Retinitis pigmentosa

TRANSCRIPT

Page 1: Retinitis pigmentosa AST

REFERAT R E T I N I T I S P I G M E N T O

S A

Disusun oleh :Astria Puspita Sari

1310221021

Pembimbing :dr. Naila Karima, Sp.M

Page 2: Retinitis pigmentosa AST
Page 3: Retinitis pigmentosa AST
Page 4: Retinitis pigmentosa AST
Page 5: Retinitis pigmentosa AST
Page 6: Retinitis pigmentosa AST

PATOFISIOLOGI

Page 7: Retinitis pigmentosa AST
Page 8: Retinitis pigmentosa AST

Myron Yanoff: •Decreased night vision (nyctalopia) dan decreased color vision•Kehilangan penglihatan perifer (loss of peripheral vision)•Penglihatan kabur (blurry vision)•Terdapat gumpalan pigmen (pigment clumping) atau "bone spicule formation" di retina perifer•Terdapat area atrofi pigmen retina

Chantal Simon, •Biasanya pertama tampak pada masa remaja (adolescence).•Terdapat black pigment flecks di retina dan optic atrophy.•Dapat berkembang menjadi kebutaan.

Page 9: Retinitis pigmentosa AST

PEMERIKSAAN

Funduskopi ERG

Formal visual field

Color testing

Adaptasi gelap

Genetic subtyping

Page 10: Retinitis pigmentosa AST

PENATALAKSANAAN

- Vitamin A larut air 10000-15000

- zinc

Vitamin E , C , karoten

Vitamin A, beta caroten, DHA, acetazolamide, lutein, vitamin E, vitamin C

Page 11: Retinitis pigmentosa AST

Diagnosis banding

Page 12: Retinitis pigmentosa AST

Kesimpulan

Page 13: Retinitis pigmentosa AST

TERIMA KASIH