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Franco-BritishPaediatricNephrologyMeeting
1-3December2016InstitutImagine
HôpitalUniversitaireNecker-EnfantsMalades24,BdduMontarnasse,75015.Paris
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DAY1:Thursday1stDecember2016
Part1:IntroductionandtransplantationChairs ChristianJacquelinet(France);DavidHughes(UK)
14h00-14h15 Welcome ChristinePietrementandRémiSalomon
14h15-14h30 OrganisationofpaediatricnephrologyservicesinFrance
ChristinePietrement
14h30-14h45 OrganisationofpaediatricnephrologyservicesinUK MartinChristian14h45-15h15 PaediatrictransplantexperienceinFrance Marie-AliceMacher15h15-15h45 PaediatrictransplantexperienceinUK StephenMarks
15h45-16h15 oralcommunications:
Pre-emptivekidneytransplantationisassociatedwithimprovedgraftsurvivalinchildren:datafromtheFrenchrenalreplacementtherapyregistry.MathildeReydit,BordeauxProphylaxieducytomégalovirusaprèstransplantationrénalechezl'enfant:versunallongementdeladuréedetraitement?(Cytomegalovirusprophylaxisafterkidneytransplantationinchildren:longerisbetter.)AlexisRybak,HôpitalRobertDebré,ParisInfection-relatedhospitalizationsafterkidneytransplantationinchildren:incidence,riskfactorsandcost.JulienHogan,HôpitalRobertDebré,ParisInterestofepitopeloadforevaluatingtheHLAcompatibilityinpediatricrenaltransplantation.MélissaOuldRabah,HôpitalNecker-EnfantsMalades,Paris
16h15-16h45
Coffeebreak/posters/exhibitors
Part2:SteroidsensitivenephroticsyndromeChairs NickWebb(UK);VincentGuigonis(France)
16h45-17h00 Managementofnewly-presentingnephroticsyndromeinFrance
ClaireDossier
17h00-17h15 Managementofnewly-presentingnephroticsyndromeinUK
NickWebb
17h15-17h30 ManagementofSDNSandRituximabexperienceinUK
RodneyGilbert
17h30-17h45 ManagementofSDNSandRituximabexperienceinFrance
VincentGuigonis
17h45-18h15 oralcommunications:
Rituximabforfrequentlyrelapsingnephroticsyndromeorsteroiddependentnephroticsyndrome:whatisthelowesteffectivedose?AndrewMaxted,NottinghamEffetsecondairedurituximabprescritchezdesenfantsayantunsyndromenéphrotique.Etuderétrospectivemulticentrique.[Adverseeffectsofrituximabusedinchildrenwithidiopathicnephroticsyndrome.Amulticentricretrospectivestudy.]FannyLaliève,LimogesRituximabandintravenousimmunoglobulininthetreatmentofsteroid-dependentnephroticsyndrome.JulienHogan,HôpitalRobertDebré,ParisSyndromenéphrotiquecongénitaletinfantilenon-génétique:nouvellesapprochesdiagnostiquesetthérapeutiques.(Non-geneticcongenitalandinfantilenephroticsyndrome:newdiagnosticandtherapeuticmanagement.)Jean-MariedeGuillebondeResnes,RobertDebréHospital,Paris
18h15-17h15 PaediatricnephrologytraininginFranceandtheUK.Sessionfortraineesonly
DAY2:Friday2ndDecember2016
08h00-08h45HorizonPharmabreakfastsymposium–seeseparateprogrammefordetails
Part3:EthicalissuesininfancyChairs PierreCochat(France);JanDudleyUK)
09h00-09h20 ManagementofESRDininfancyinUK HeatherLambert09h20-09h40 ManagementandethicalapproachesinFrance RachelVieux09h40-10h00 Generaldiscussion
10h00-11h00 oralcommunications:
Cakutome,ahigh-throughputtoolformoleculardiagnosisandidentificationofnovelcausativegenesforCAKUTpatientsLaurenceHeidet,HôpitalNecker-EnfantsMalades,ParisFrenchcohortoftransientantenatalBarttersyndromewithMAGED2mutations.AnneLegrand,HôpitalEuropéenGeorgesPompidou,ParisAretrospectivereviewofpaediatricpatientswithBartterandGitelmansyndrome.PatrickWalsh,NewcastleFistuleartérioveineuseparmicrochirurgiechezl’enfantdemoinsde20Kg:expériencemonocentrique.[Autologousarteriovenousfistulaeusingmicrosurgeryforhemodialysisinyoungchildrenweighing20kgorless:singlecenterexperience.]VasilikiKarava,HôpitalRobertDebré,ParisAsnapshotofacutekidneyinjuryintertiarypaediatriccentresintheUnitedKingdom.GeorgeVerghese,LiverpoolTimetoSTOPacutekidneyinjury.AmandaNewnham,LeedsAutomatedestimatedGFRreportinginchildrenusingaheight-independentformula.AndrewLunn,NottinghamEffectofnonsteroidalanti-inflammatorydrugsinchildrenwithBarttersyndrome.JulienHogan,HôpitalRobertDebré,Paris
11h00-11h30
Coffeebreakandpostersession(tour)
Part4:ResearchandpatientsupportChairs RachelLennon(UK);DenisMorin(France)
11h30-11h45 ResearchthemesinUK RachelLennon11h45-12h00 ResearchthemesinFrance OliviaBoyer12h00-12h15 PatientsupportinFrance DenisMorin12h15-12h30 PatientsupporttheUK MichelleRossiter12h30-13h00 Oralcommunications:
Inter-observervariabilityofthehistologicalclassificationoflupusglomerulonephritisinchildrenLouiseOni,LiverpoolMycophenolicacidareaunderthecurveisassociatedwiththerapeuticresponseinpediatriclupusnephritis.AstridGodron,BordeauxOutcomefollowingswitchbetweenbrandnameandgenerictacrolimusinpaediatricpopulation.SwethaVijayan,NottinghamEvaluationdeseffetspharmacodynamiquesd’uneformulationinnovanted’alcalinisantsàlibérationprolongéesurlesparamètresurinaireschezlessujetssainsadultes.(Evaluationofthepharmacodynamicseffectsofaninnovativeprolongedreleasealkalinisingformulationintheurineparametersinhealthyadultsubjects.)AureliaBertholet-Thomas,Lyon(onbehalfofAdvicienne)
DAY2:Friday2ndDecember2016continued
13h00-14h30
Lunchandpostersession(tour)
14h30-17h30 Smallgroupmeetings/freetime17h30-19h00
SNPgeneralassemblyBAPNbusinessmeeting
Day3:Saturday3rdDecember2016
08h00-08h45Alexionbreakfastsymposium–seeseparateprogrammefordetails
Part5:CKDChairs TimUlinski(France);DavidMilford(UK)09h00-09h30 GrowthhormoneuseUK,Franceand
EuropeJérômeHarambat
09h30-10h00 Phosphatebindersandcalcium LesleyRees10h00-10h30 Bonedisease JustineBacchetta
10h30-11h00
Coffeebreakandpostersession
Part6:What’snew? Chairs MordiMuorah(UK),RémiSalomon(France)11h00-11h30 Geneticsofglomerulardisease MoinSaleem11h30-12h00 Geneticsofcomplementdisorders Anne-LaureSellier-Leclerc12h00-12h30 Geneticsoftubulardisease DetlefBockenhauer12h30-13h00 Geneticsofautosomaldominant
tubulointerstitialdiseaseBertrandKnebelmann
13h00-13h15 Closingremarks ChristinePietrementDavidHughes
SpeakersandChairs
ChristinePietrement ProfessorofPaediatrics,PaediatricNephrologist,CHUdeReims,SNPPresident
DavidHughes ConsultantPaediatricNephrologist,GlasgowandBAPNPresidentRémiSalomon ProfessorofPaediatrics,PaediatricNephrologist,HôpitalNeckerEnfants-
Malades,Paris,SNPVice-PresidentChristianJacquelinet MedicalDirector,AgencedelaBiomédecine,Saint-DenisandHeadof
FrenchESRDREINRegistryMartinChristian ConsultantPaediatricNephrologist,Nottingham,BAPNSecretaryMarie-AliceMacher PaediatricNephrologist,AgencedelaBiomédecineStephenMarks ConsultantPaediatricNephrologist,GreatOrmondStreetLondon,Chairof
PaediatricSub-GrouptoUKKidneyAdvisoryGroupClaireDossier PaediatricNephrologist,HôpitalRobertDebré,ParisNickWebb ProfessorofPaediatricNephrology,ManchesterRodneyGilbert ConsultantPaediatricNephrologist,SouthamptonVincentGuigonis ProfessorofPaediatrics,PaediatricNephrologist,CHUdeLimoges,SNP
TreasurerPierreCochat ProfessorofPaediatrics,LyonandIPNAPresidentJanDudley ConsultantPaediatricNephrologist,BristolHeatherLambert ConsultantPaediatricNephrologist,NewcastleRachelVieux ProfessorofPaediatrics,PaediatricNephrologist,CHUdeBesançonRachelLennon WelcomeIntermediateFellowandConsultantPaediatricNephrologist,
Manchester,BAPNResearchSecretaryOliviaBoyer AssociateProfessorofPaediatrics,PaediatricNephrologist,HôpitalNecker
Enfants-Malades,ParisDenisMorin ProfessorofPaediatrics,PaediatricNephrologist,CHUdeMontpellier,
ORKIDPresidentMichelleRossiter LayRepresentativetoBAPNExecutiveCommitteeandVolunteerwith
BritishKidneyPatientAssociationJérômeHarambat ProfessorofPaediatrics,PaediatricNephrologist,CHUdeBordeauxLesleyRees ProfessorofPaediatricNephrology,GreatOrmondStreetHospital,LondonJustineBacchetta AssociateProfessorofPaediatrics,PaediatricNephrologist,Hôpital
FemmeMèreEnfant,HospicescivilesdeLyon,BronTimUlinski ProfessorofPaediatrics,Hôpitald'EnfantsArmand-Trousseau,ParisDavidMilford ConsultantPaediatricNephrologist,BirminghamMoinSaleem ProfessorofPaediatricNephrology,BristolAnne-LaureSellier-Leclerc
PaediatricNephrologist,HôpitalFemmeMèreEnfant,HospicescivilesdeLyon,Bron
DetlefBockenhauer ProfessorofPaediatricNephrology,InstituteofChildHealth,London&ConsultantPaediatricNephrologist,GreatOrmondStreetHospital
BertrandKnebelmann ProfessorofNephrology,HôpitalNeckerEnfants-Malades,ParisMordiMuorah ConsultantPaediatricNephrologist,Birmingham
SocialEvents
ThursdayEvening
CocktailsandlightrefreshmentsatInstitutImagineimmediatelyfollowingfinalsession.TraineeswillcontinuetomeetforfurthersessionsharingtraininginFranceandtheUKwithseparatesocialeventafter.Thesessionconcludesaround9pmtoallowdelegatestoarrangerestaurantbookingsafterifwished.
FridayEvening
GaladinnerandRiverSeinecruise.Embarkationfrom7.30.Boatsailsat9pmwithreturnby11pm.Detailsinseparateinstructions.
Thismeetinghasbeenkindlysupportedbyeducationalgrantsfromthefollowingcompanies: