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Franco-British Paediatric Nephrology Meeting 1-3 December 2016 Institut Imagine Hôpital Universitaire Necker-Enfants Malades 24, Bd du Montarnasse, 75015. Paris Impossible d'acher l'image liée. Le fichier a peut-être été déplacé, renommé ou supprimé. Vérifiez que la liaison pointe vers le fichier et l'emplacement corrects.

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Franco-BritishPaediatricNephrologyMeeting

1-3December2016InstitutImagine

HôpitalUniversitaireNecker-EnfantsMalades24,BdduMontarnasse,75015.Paris

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DAY1:Thursday1stDecember2016

Part1:IntroductionandtransplantationChairs ChristianJacquelinet(France);DavidHughes(UK)

14h00-14h15 Welcome ChristinePietrementandRémiSalomon

14h15-14h30 OrganisationofpaediatricnephrologyservicesinFrance

ChristinePietrement

14h30-14h45 OrganisationofpaediatricnephrologyservicesinUK MartinChristian14h45-15h15 PaediatrictransplantexperienceinFrance Marie-AliceMacher15h15-15h45 PaediatrictransplantexperienceinUK StephenMarks

15h45-16h15 oralcommunications:

Pre-emptivekidneytransplantationisassociatedwithimprovedgraftsurvivalinchildren:datafromtheFrenchrenalreplacementtherapyregistry.MathildeReydit,BordeauxProphylaxieducytomégalovirusaprèstransplantationrénalechezl'enfant:versunallongementdeladuréedetraitement?(Cytomegalovirusprophylaxisafterkidneytransplantationinchildren:longerisbetter.)AlexisRybak,HôpitalRobertDebré,ParisInfection-relatedhospitalizationsafterkidneytransplantationinchildren:incidence,riskfactorsandcost.JulienHogan,HôpitalRobertDebré,ParisInterestofepitopeloadforevaluatingtheHLAcompatibilityinpediatricrenaltransplantation.MélissaOuldRabah,HôpitalNecker-EnfantsMalades,Paris

16h15-16h45

Coffeebreak/posters/exhibitors

Part2:SteroidsensitivenephroticsyndromeChairs NickWebb(UK);VincentGuigonis(France)

16h45-17h00 Managementofnewly-presentingnephroticsyndromeinFrance

ClaireDossier

17h00-17h15 Managementofnewly-presentingnephroticsyndromeinUK

NickWebb

17h15-17h30 ManagementofSDNSandRituximabexperienceinUK

RodneyGilbert

17h30-17h45 ManagementofSDNSandRituximabexperienceinFrance

VincentGuigonis

17h45-18h15 oralcommunications:

Rituximabforfrequentlyrelapsingnephroticsyndromeorsteroiddependentnephroticsyndrome:whatisthelowesteffectivedose?AndrewMaxted,NottinghamEffetsecondairedurituximabprescritchezdesenfantsayantunsyndromenéphrotique.Etuderétrospectivemulticentrique.[Adverseeffectsofrituximabusedinchildrenwithidiopathicnephroticsyndrome.Amulticentricretrospectivestudy.]FannyLaliève,LimogesRituximabandintravenousimmunoglobulininthetreatmentofsteroid-dependentnephroticsyndrome.JulienHogan,HôpitalRobertDebré,ParisSyndromenéphrotiquecongénitaletinfantilenon-génétique:nouvellesapprochesdiagnostiquesetthérapeutiques.(Non-geneticcongenitalandinfantilenephroticsyndrome:newdiagnosticandtherapeuticmanagement.)Jean-MariedeGuillebondeResnes,RobertDebréHospital,Paris

18h15-17h15 PaediatricnephrologytraininginFranceandtheUK.Sessionfortraineesonly

DAY2:Friday2ndDecember2016

08h00-08h45HorizonPharmabreakfastsymposium–seeseparateprogrammefordetails

Part3:EthicalissuesininfancyChairs PierreCochat(France);JanDudleyUK)

09h00-09h20 ManagementofESRDininfancyinUK HeatherLambert09h20-09h40 ManagementandethicalapproachesinFrance RachelVieux09h40-10h00 Generaldiscussion

10h00-11h00 oralcommunications:

Cakutome,ahigh-throughputtoolformoleculardiagnosisandidentificationofnovelcausativegenesforCAKUTpatientsLaurenceHeidet,HôpitalNecker-EnfantsMalades,ParisFrenchcohortoftransientantenatalBarttersyndromewithMAGED2mutations.AnneLegrand,HôpitalEuropéenGeorgesPompidou,ParisAretrospectivereviewofpaediatricpatientswithBartterandGitelmansyndrome.PatrickWalsh,NewcastleFistuleartérioveineuseparmicrochirurgiechezl’enfantdemoinsde20Kg:expériencemonocentrique.[Autologousarteriovenousfistulaeusingmicrosurgeryforhemodialysisinyoungchildrenweighing20kgorless:singlecenterexperience.]VasilikiKarava,HôpitalRobertDebré,ParisAsnapshotofacutekidneyinjuryintertiarypaediatriccentresintheUnitedKingdom.GeorgeVerghese,LiverpoolTimetoSTOPacutekidneyinjury.AmandaNewnham,LeedsAutomatedestimatedGFRreportinginchildrenusingaheight-independentformula.AndrewLunn,NottinghamEffectofnonsteroidalanti-inflammatorydrugsinchildrenwithBarttersyndrome.JulienHogan,HôpitalRobertDebré,Paris

11h00-11h30

Coffeebreakandpostersession(tour)

Part4:ResearchandpatientsupportChairs RachelLennon(UK);DenisMorin(France)

11h30-11h45 ResearchthemesinUK RachelLennon11h45-12h00 ResearchthemesinFrance OliviaBoyer12h00-12h15 PatientsupportinFrance DenisMorin12h15-12h30 PatientsupporttheUK MichelleRossiter12h30-13h00 Oralcommunications:

Inter-observervariabilityofthehistologicalclassificationoflupusglomerulonephritisinchildrenLouiseOni,LiverpoolMycophenolicacidareaunderthecurveisassociatedwiththerapeuticresponseinpediatriclupusnephritis.AstridGodron,BordeauxOutcomefollowingswitchbetweenbrandnameandgenerictacrolimusinpaediatricpopulation.SwethaVijayan,NottinghamEvaluationdeseffetspharmacodynamiquesd’uneformulationinnovanted’alcalinisantsàlibérationprolongéesurlesparamètresurinaireschezlessujetssainsadultes.(Evaluationofthepharmacodynamicseffectsofaninnovativeprolongedreleasealkalinisingformulationintheurineparametersinhealthyadultsubjects.)AureliaBertholet-Thomas,Lyon(onbehalfofAdvicienne)

DAY2:Friday2ndDecember2016continued

13h00-14h30

Lunchandpostersession(tour)

14h30-17h30 Smallgroupmeetings/freetime17h30-19h00

SNPgeneralassemblyBAPNbusinessmeeting

Day3:Saturday3rdDecember2016

08h00-08h45Alexionbreakfastsymposium–seeseparateprogrammefordetails

Part5:CKDChairs TimUlinski(France);DavidMilford(UK)09h00-09h30 GrowthhormoneuseUK,Franceand

EuropeJérômeHarambat

09h30-10h00 Phosphatebindersandcalcium LesleyRees10h00-10h30 Bonedisease JustineBacchetta

10h30-11h00

Coffeebreakandpostersession

Part6:What’snew? Chairs MordiMuorah(UK),RémiSalomon(France)11h00-11h30 Geneticsofglomerulardisease MoinSaleem11h30-12h00 Geneticsofcomplementdisorders Anne-LaureSellier-Leclerc12h00-12h30 Geneticsoftubulardisease DetlefBockenhauer12h30-13h00 Geneticsofautosomaldominant

tubulointerstitialdiseaseBertrandKnebelmann

13h00-13h15 Closingremarks ChristinePietrementDavidHughes

SpeakersandChairs

ChristinePietrement ProfessorofPaediatrics,PaediatricNephrologist,CHUdeReims,SNPPresident

DavidHughes ConsultantPaediatricNephrologist,GlasgowandBAPNPresidentRémiSalomon ProfessorofPaediatrics,PaediatricNephrologist,HôpitalNeckerEnfants-

Malades,Paris,SNPVice-PresidentChristianJacquelinet MedicalDirector,AgencedelaBiomédecine,Saint-DenisandHeadof

FrenchESRDREINRegistryMartinChristian ConsultantPaediatricNephrologist,Nottingham,BAPNSecretaryMarie-AliceMacher PaediatricNephrologist,AgencedelaBiomédecineStephenMarks ConsultantPaediatricNephrologist,GreatOrmondStreetLondon,Chairof

PaediatricSub-GrouptoUKKidneyAdvisoryGroupClaireDossier PaediatricNephrologist,HôpitalRobertDebré,ParisNickWebb ProfessorofPaediatricNephrology,ManchesterRodneyGilbert ConsultantPaediatricNephrologist,SouthamptonVincentGuigonis ProfessorofPaediatrics,PaediatricNephrologist,CHUdeLimoges,SNP

TreasurerPierreCochat ProfessorofPaediatrics,LyonandIPNAPresidentJanDudley ConsultantPaediatricNephrologist,BristolHeatherLambert ConsultantPaediatricNephrologist,NewcastleRachelVieux ProfessorofPaediatrics,PaediatricNephrologist,CHUdeBesançonRachelLennon WelcomeIntermediateFellowandConsultantPaediatricNephrologist,

Manchester,BAPNResearchSecretaryOliviaBoyer AssociateProfessorofPaediatrics,PaediatricNephrologist,HôpitalNecker

Enfants-Malades,ParisDenisMorin ProfessorofPaediatrics,PaediatricNephrologist,CHUdeMontpellier,

ORKIDPresidentMichelleRossiter LayRepresentativetoBAPNExecutiveCommitteeandVolunteerwith

BritishKidneyPatientAssociationJérômeHarambat ProfessorofPaediatrics,PaediatricNephrologist,CHUdeBordeauxLesleyRees ProfessorofPaediatricNephrology,GreatOrmondStreetHospital,LondonJustineBacchetta AssociateProfessorofPaediatrics,PaediatricNephrologist,Hôpital

FemmeMèreEnfant,HospicescivilesdeLyon,BronTimUlinski ProfessorofPaediatrics,Hôpitald'EnfantsArmand-Trousseau,ParisDavidMilford ConsultantPaediatricNephrologist,BirminghamMoinSaleem ProfessorofPaediatricNephrology,BristolAnne-LaureSellier-Leclerc

PaediatricNephrologist,HôpitalFemmeMèreEnfant,HospicescivilesdeLyon,Bron

DetlefBockenhauer ProfessorofPaediatricNephrology,InstituteofChildHealth,London&ConsultantPaediatricNephrologist,GreatOrmondStreetHospital

BertrandKnebelmann ProfessorofNephrology,HôpitalNeckerEnfants-Malades,ParisMordiMuorah ConsultantPaediatricNephrologist,Birmingham

SocialEvents

ThursdayEvening

CocktailsandlightrefreshmentsatInstitutImagineimmediatelyfollowingfinalsession.TraineeswillcontinuetomeetforfurthersessionsharingtraininginFranceandtheUKwithseparatesocialeventafter.Thesessionconcludesaround9pmtoallowdelegatestoarrangerestaurantbookingsafterifwished.

FridayEvening

GaladinnerandRiverSeinecruise.Embarkationfrom7.30.Boatsailsat9pmwithreturnby11pm.Detailsinseparateinstructions.

Thismeetinghasbeenkindlysupportedbyeducationalgrantsfromthefollowingcompanies: